Status:

COMPLETED

Study of Megakaryocytes From Patients With Abnormal Platelet Vesicles

Lead Sponsor:

National Human Genome Research Institute (NHGRI)

Conditions:

Blood Coagulation Disorders

Eligibility:

All Genders

2-80 years

Brief Summary

Congenital bleeding disorders characterized by abnormal platelet granules include Gray Platelet syndrome (GPS; defective alpha-granules), Hermansky-Pudlak syndrome (HPS; defective delta-granules), and...

Detailed Description

Congenital bleeding disorders characterized by abnormal platelet granules include Gray Platelet syndrome (GPS; defective alpha-granules), Hermansky-Pudlak syndrome (HPS; defective delta-granules), and...

Eligibility Criteria

Inclusion

  • INCLUSION CRITERIA:
  • This protocol will include children and adults with a clinical diagnosis of GPS, HPS, isolated delta-SPD, combined alpha delta-SPD, Griscelli disease, Chediak Higashi syndrome, Wiskott Aldrich syndrome or Thrombocytopenia absent radius syndrome. Patients whose platelets exhibit abnormal intracellular vesicle morphology will also be eligible.
  • EXCLUSION CRITERIA:
  • Patients younger than 2 years and older than 80 years will be excluded. Patients with severe thrombocytopenia (fewer than 20 times 10(12) platelets/L) will be excluded.

Exclusion

    Key Trial Info

    Start Date :

    June 29 2004

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ACTUAL

    End Date :

    June 13 2011

    Estimated Enrollment :

    3 Patients enrolled

    Trial Details

    Trial ID

    NCT00086476

    Start Date

    June 29 2004

    End Date

    June 13 2011

    Last Update

    July 2 2017

    Active Locations (1)

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    Page 1 of 1 (1 locations)

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    National Institutes of Health Clinical Center, 9000 Rockville Pike

    Bethesda, Maryland, United States, 20892