Status:

COMPLETED

Open-Label Extension Study Evaluating Long Term Safety in Patients With Type 1 Gaucher Disease Receiving DRX008A (ERT)

Lead Sponsor:

Shire

Conditions:

Gaucher Disease

Eligibility:

All Genders

18+ years

Phase:

PHASE1

PHASE2

Brief Summary

Gaucher disease is a rare lysosomal storage disorder caused by the deficiency of the enzyme glucocerebrosidase (GCB). Due to the deficiency of functional GCB, glucocerebroside accumulates within macro...

Detailed Description

Type 1 Gaucher disease, the most common form, accounts for more than 90% of all cases and does not involve the central nervous system (CNS). Typical manifestations of type 1 Gaucher disease include he...

Eligibility Criteria

Inclusion

  • Patients who have completed through Week 41 visit in the TKT025 study.
  • Patients must have voluntarily signed an IRB/EC approved informed consent form after all relevant aspects of the study have been explained and discussed with the patient.
  • Patient must be sufficiently cooperative to participate in this clinical study as judged by the Investigator.
  • Female and male patients of child bearing potential must agree to use a medically acceptable method of contraception at all times during the study. Female patients must have a negative serum pregnancy test on enrollment.

Exclusion

  • Patient has received treatment with non-Gaucher disease related investigational drug or device within the past 30 days prior to study entry; such use during the study is not permitted.
  • Patient has a clinically relevant medical condition (e.g., HIV, hepatitis B or C) that would make implementation of the protocol difficult and/or confound an assessment of the effects of the experimental therapy and its adverse events.
  • Patient, patient's parent(s), or patient's legal guardian is unable to understand the nature, scope and possible consequences of the study.
  • Patient is unable to comply with the protocol, e.g. uncooperative attitude, medical condition, inability to return for safety evaluations, or is otherwise unlikely to complete the study, as determined by the Investigator.

Key Trial Info

Start Date :

September 13 2004

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

January 31 2008

Estimated Enrollment :

10 Patients enrolled

Trial Details

Trial ID

NCT00391625

Start Date

September 13 2004

End Date

January 31 2008

Last Update

June 22 2021

Active Locations (3)

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Page 1 of 1 (3 locations)

1

Shaare Zedek Medical Center

Jerusalem, Israel

2

Maria Sklodowska Curie Children's Hospital

Bucharest, Romania, 75544

3

Mother and Child Health Care Institute of Serbia

Belgrade, Serbia