Status:

COMPLETED

Topical Sirolimus in Patients With Basal Cell Nevus Syndrome and in Healthy Participants

Lead Sponsor:

Yale University

Collaborating Sponsors:

National Cancer Institute (NCI)

Conditions:

Neoplastic Syndrome

Non-melanomatous Skin Cancer

Eligibility:

All Genders

18-120 years

Phase:

PHASE1

Brief Summary

RATIONALE: Studying samples of blood and tissue from patients with basal cell nevus syndrome and from healthy participants in the laboratory may help doctors learn more about changes that may occur in...

Detailed Description

OBJECTIVES: Primary * Compare messenger RNA and protein expression patterns in patients with basal cell nevus syndrome (BCNS) vs in cultured cells of healthy participants (control) before treatment ...

Eligibility Criteria

Inclusion

  • DISEASE CHARACTERISTICS:
  • Patient
  • Confirmed diagnosis of basal cell nevus syndrome (BCNS)
  • Known patched (PTCH) gene mutation
  • Must have full sequence of coding exons with intron/exon junctions in the PTCH gene OR prior genetic testing confirming PTCH mutation by the Yale University DNA Diagnostics Laboratory
  • Age- and sex-matched healthy participant (control)
  • Unaffected relative of patient OR normal healthy volunteer with no family history of BCNS or features of BCNS
  • No unrelated healthy participant meeting any of the following clinical criteria for BCNS:
  • Lamellar calcification of the falx cerebri
  • Prior odontogenic keratocyst or any jaw cyst for which a histopathologic diagnosis cannot be ascertained
  • Palmar or plantar pits typical of BCNS
  • More than 3 basal cell carcinomas (BCC) in a lifetime or 1 BCC under the age of 30
  • History of medulloblastoma
  • No unrelated healthy participant with 2 or more of the following features:
  • History of ovarian or cardiac fibroma
  • Mesenteric or pleural cysts
  • Polydactyly
  • Macrocephaly determined after adjustment for height
  • Craniofacial features of BCNS, including cleft palate, frontal bossing, hypertelorism, iris coloboma or other developmental defects of the eye, or coarse facies
  • Vertebral anomalies, including spina bifida occulta outside the lumbar region
  • Bifid or splayed ribs
  • Other radiographic findings, including bridging of the sella turcica, nonlamellar calcification of the falx cerebri, or flame-shaped lucencies in the phalanges = 1-3 BCCs over the age of 30
  • PATIENT CHARACTERISTICS:
  • WBC ≥ 4,000/mm³
  • Neutrophil count ≥ 2,000/mm³
  • Platelet count ≥ 150,000/mm³
  • Hemoglobin ≥ 11.5 g/dL
  • Bilirubin 0.3-1.0 mg/dL
  • AST 17-59 U/L
  • PTT 10-13 seconds OR INR 1.0-1.4
  • Creatinine clearance \> 50 mL/min
  • Cholesterol \< 350 mg/dL
  • Triglycerides \< 400 mg/dL
  • Not pregnant or nursing
  • Negative pregnancy test
  • Fertile participants must use effective contraception for ≥ 1 month before, during, and for ≥ 12 weeks after study treatment
  • No active infection
  • No alcohol or drug abuse
  • No psychiatric disorder or mental deficiency that would preclude study compliance
  • No uncontrolled hypertension (i.e., blood pressure \> 140/90 mm Hg on \> 2 measurements)
  • No chronic active infection requiring treatment
  • No untreated reactive purified protein derivative of tuberculin (PPD)
  • No HIV-1 infection
  • No infection requiring antibiotics within the past 30 days
  • No other skin disease affecting broad areas of the body, including the region to be treated and biopsied
  • No known hepatitis B or C infection (detectable RNA off antiviral therapy)
  • No immune deficiency disorder
  • No known hypersensitivity to sirolimus or macrolide antibiotics (e.g., erythromycin, azithromycin, or clarithromycin)
  • No cancer within the past 5 years except basal cell skin cancer
  • PRIOR CONCURRENT THERAPY:
  • At least 1 month since prior investigational drugs
  • No concurrent dietary supplements, including Hypericum perforatum (St. John's wort) or megadose vitamins
  • No other concurrent immunosuppressive medications, including corticosteroids
  • No concurrent medications known to interfere with sirolimus metabolism
  • No concurrent anticoagulants
  • No concurrent acetylsalicyclic acid or other drugs affecting platelet function or number
  • No routine (i.e., \> 2 doses/week) use of nonsteroidal anti-inflammatory drugs
  • No drugs or substances that would effect sirolimus blood concentrations, including any of the following:
  • Nicardipine
  • Verapamil
  • Clotrimazole
  • Fluconazole
  • Itraconazole
  • Troleandomycin
  • Cisapride
  • Metoclopramide
  • Clarithromycin
  • Erythromycin
  • Bromocriptine
  • Cimetidine
  • Danazol
  • HIV-protease inhibitors (e.g., ritonavir or indinavir)
  • Phenobarbital
  • Carbamazepine
  • Phenytoin
  • Rifabutin
  • Rifapentine
  • Grapefruit juice
  • Vaccinations (especially live vaccines)

Exclusion

    Key Trial Info

    Start Date :

    Trial Type :

    INTERVENTIONAL

    Allocation :

    ESTIMATED

    End Date :

    March 1 2008

    Estimated Enrollment :

    16 Patients enrolled

    Trial Details

    Trial ID

    NCT00433485

    End Date

    March 1 2008

    Last Update

    September 23 2016

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    Topical Sirolimus in Patients With Basal Cell Nevus Syndrome and in Healthy Participants | DecenTrialz