Status:

TERMINATED

Analysis of Oculo-motor Deficiencies Associated With FMR1 Gene Expression (Genetic Abnormality Predisposing to a Neurodegenerative Disease)

Lead Sponsor:

Nantes University Hospital

Conditions:

Pre-mutation on FMR1 Gene

Eligibility:

MALE

18-50 years

Phase:

NA

Brief Summary

The specific aim of this study is to compare ocular movements abnormalities between males with pre-mutation on FRM1 gene (symptomatic or asymptomatic on the motor plan and/or on the cognitive plan), m...

Detailed Description

Patient will be followed at the Nantes hospital during half a day for : * examination of ocular movements * performing Neuro-psychological test (MATTIS) * performing tests with scales of motricity (U...

Eligibility Criteria

Inclusion

  • FOR PATIENTS WITH PREMUTATION ON FMR1 GENE (30 patients expected):
  • Inclusion criteria:
  • Male
  • \> or equal to 50 years old
  • Ally second or third degree with a child affected of "fragile X"
  • Not living far from Nantes so that visits to the Nantes hospital can be easy
  • Pre-mutation on FMR1 gene
  • Signed informed consent
  • Exclusion criteria:
  • Female
  • \<50 years old
  • visual acuteness \< 1/10
  • MATTIS dementia scale \<100 (normal:144)
  • Occurrence, shown by MRI (Magnetic Resonance Imaging), of a pathology either ischemic vascular or hemorrhagic or tumoral
  • FOR PATIENTS WITHOUT PRE-MUTATION ON FMR1 GENE (10 patients expected):
  • Inclusion criteria:
  • Male
  • \> or equal to 50 years old
  • Ally second or third degree with a child affected of "fragile X"
  • Not living far from Nantes so that visits to the Nantes hospital can be easy - Signed informed consent
  • Exclusion criteria:
  • Female
  • \<50 years old
  • visual acuteness \< 1/10
  • MATTIS dementia scale \<100 (normal:144)
  • Pre-mutation on FMR1 gene
  • Occurrence, shown by MRI, of a pathology either ischemic vascular or hemorrhagic or tumoral
  • FOR PATIENTS WITH MULTI-SYSTEMATIZED ATROPHY (10 patients expected):
  • Inclusion criteria:
  • Male
  • \> or equal to 50 years old
  • Not living far from Nantes so that visits to the Nantes hospital can be easy
  • "probable" diagnosis of multi-systematized atrophy
  • Signed informed consent
  • Exclusion Criteria:
  • Female
  • \<50 years old
  • visual acuteness \< 1/10
  • MATTIS dementia scale \<100 (normal:144)
  • Occurrence, shown by MRI, of a pathology either ischemic vascular or hemorrhagic or tumoral

Exclusion

    Key Trial Info

    Start Date :

    June 1 2008

    Trial Type :

    INTERVENTIONAL

    Allocation :

    ACTUAL

    End Date :

    September 1 2009

    Estimated Enrollment :

    27 Patients enrolled

    Trial Details

    Trial ID

    NCT00763191

    Start Date

    June 1 2008

    End Date

    September 1 2009

    Last Update

    December 10 2012

    Active Locations (1)

    Enter a location and click search to find clinical trials sorted by distance.

    Page 1 of 1 (1 locations)

    1

    Laennec hospital, university hospital of Nantes

    Nantes, France, 44093