Status:

COMPLETED

PKUDOS: Phenylketonuria (PKU) Demographic, Outcomes, and Safety Registry

Lead Sponsor:

BioMarin Pharmaceutical

Conditions:

Phenylketonuria

Hyperphenylalaninaemia

Eligibility:

All Genders

Brief Summary

The objective of this study is to evaluate the safety of long-term treatment with Kuvan.

Detailed Description

The PKUDOS program is a voluntary, multicenter, strictly observational program for patients with PKU who have either received Kuvan therapy, or currently receive Kuvan, or intend to begin receiving Ku...

Eligibility Criteria

Inclusion

  • PKUDOS Registry
  • Patient has confirmed diagnosis of PKU with hyperphenylalaninemia documented by a Phenylalanine level of greater than or equal to 360 umol/L (6 mg/dL)
  • Patient has previously received Kuvan
  • Patient is currently receiving Kuvan
  • Patient intends to receive Kuvan therapy within 90 days of enrollment into the registry
  • The Patient is being followed at a PKUDOS participating center
  • Willing and able to provide written authorization or, if under the age of 18 years, provide written assent (if required) and written patient authorization by a parent or legal guardian
  • Willing to provide personal health information

Exclusion

  • Patients are not eligible to participate in PKUDOS if they are participating in a BioMarin-sponsored clinical study of Kuvan
  • Patients not previously treated with Kuvan and patients that are unwilling to begin Kuvan therapy within 90 days of entry into the registry
  • PKU MOMS Subregistry
  • Inclusion Criteria:
  • Willing to enroll in (or are already enrolled in) PKUDOS
  • Agree to follow the standard of care for pregnant women with PKU in the United States (NIH, 200, NIH Consensus Statement)
  • Agree to be followed by a hospital or PKU clinic offering the standard of care for maternal PKU
  • Are within 10 weeks of their last menstrual period

Key Trial Info

Start Date :

September 1 2008

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

January 29 2021

Estimated Enrollment :

1887 Patients enrolled

Trial Details

Trial ID

NCT00778206

Start Date

September 1 2008

End Date

January 29 2021

Last Update

October 12 2022

Active Locations (45)

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Page 1 of 12 (45 locations)

1

Childrens Hospital of Los Angeles

Los Angeles, California, United States, 90027

2

LAC and USC Medical Center

Los Angeles, California, United States, 90033

3

UCLA

Los Angeles, California, United States, 90095

4

Children's Hospital of Orange County

Orange, California, United States, 92868