Status:

COMPLETED

Clinical Study of Aldurazyme in Patients With Mucopolysaccharidosis (MPS) I

Lead Sponsor:

Genzyme, a Sanofi Company

Collaborating Sponsors:

BioMarin/Genzyme LLC

Conditions:

Mucopolysaccharidosis I

Hurlers Syndrome

Eligibility:

All Genders

5+ years

Phase:

PHASE3

Brief Summary

This study is being conducted to demonstrate the safety and clinical efficacy of Aldurazyme treatment in MPS I patients

Eligibility Criteria

Inclusion

  • The patient had a documented diagnosis of MPS I confirmed by measurable clinical signs and symptoms of MPS I and a fibroblast or leukocyte alpha-L-iduronidase enzyme activity level of less than 10% of the lower limit of the normal range of the measuring laboratory.
  • Female patients of childbearing potential had a negative pregnancy test (urine-beta-human chorionic gonadotropin (hCG)) at baseline (all female patients of childbearing potential and sexually mature male patients were advised to use a medically accepted method of contraception throughout the study).
  • The patient was capable of standing independently for 6 minutes and walking a minimum of 5 meters within 6 minutes.
  • The patient was capable of performing a reproducible FVC maneuver.
  • The patient had a baseline FVC value that was less than or equal to 80% of the patient's predicted normal FVC value based on polgar predicted values for standing height for children 5 through 7 years of age and the Hankinson predicted values for ages 8 and above.

Exclusion

  • The patient had undergone a tracheostomy.
  • The patient had previously undergone a bone marrow transplantation.
  • The patient was pregnant or lactating.
  • The patient has received an investigational drug within 30 days prior to study enrollment.
  • The patient had a medical condition, serious intercurrent illness, or other extenuating circumstance that could have significantly interfered with study compliance including all prescribing evaluations and follow-up activities.
  • The patient had a known hypersensitivity to rhIDU or to components of the active or placebo test solutions.

Key Trial Info

Start Date :

December 1 2000

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

September 1 2001

Estimated Enrollment :

45 Patients enrolled

Trial Details

Trial ID

NCT00912925

Start Date

December 1 2000

End Date

September 1 2001

Last Update

April 7 2015

Active Locations (4)

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Page 1 of 1 (4 locations)

1

New York, New York, United States

2

Chapel Hill, North Carolina, United States

3

Vancouver, British Columbia, Canada

4

Mainz, Germany