Status:

COMPLETED

State Of The Art Functional Imaging In Sickle Cell Disease

Lead Sponsor:

St. Jude Children's Research Hospital

Conditions:

Sickle Cell Anemia

Eligibility:

All Genders

5-19 years

Brief Summary

Sickle cell anemia (SCA) is a serious blood disease with blood vessel changes leading to brain injury and stroke. Studies show about 11% of patients with SCA will develop obvious stroke before age 20 ...

Detailed Description

The Primary Objective of the study is to compare the research participant's GM \[Gray Matter\] CBF \[Cerebral Blood Flow\] by ASL \[Arterial Spin Labeling\] techniques before and after reaching a stab...

Eligibility Criteria

Inclusion

  • Inclusion Criteria for Pre-Hydroxyurea or Pre-Transfusion Therapy Study Participants:
  • The diagnosis of HbSS or HbS/ß0-thalassemia
  • Age: 8.0 -- \<19 years old
  • Inclusion Criteria for Study Participants for Observation:
  • The diagnosis of HbSS or HbS/ß0-thalassemia
  • Age: 8.0 -- \<19 years old
  • Inclusion Criteria for Study Participants for Family Related Controls:
  • No diagnosis of HbSS or HbS/ß0-thalassemia
  • Age: 8.0 -- \<19 years old
  • Exclusion Criteria for Pre-Hydroxyurea or Pre-Transfusion Therapy Study Participants:
  • Unable to tolerate the anatomical or fMRI \[functional magnetic resonance imaging\] without sedation or anesthesia
  • Currently receiving hydroxyurea therapy or transfusion therapy
  • Previous stem cell transplant or other myelosuppressive therapy
  • History of clinical stroke
  • Inability or unwillingness of research participant or legal guardian/representative to give written informed consent/assent.
  • Exclusion Criteria for Study Participants for Observation:
  • Unable to tolerate anatomical or fMRI components without sedation or anesthesia
  • Currently receiving hydroxyurea or transfusion therapy
  • Previous stem cell transplant or other myelosuppressive therapy
  • History of clinical stroke
  • Inability or unwillingness of research participant or legal guardian/representative to give written informed consent.
  • Exclusion Criteria for Study Participants for Family Related Controls:
  • Unable to tolerate anatomical or fMRI components without sedation or anesthesia
  • Currently receiving hydroxyurea or transfusion therapy
  • Previous stem cell transplant or other myelosuppressive therapy
  • History of clinical stroke
  • Inability or unwillingness of research participant or legal guardian/representative to give written informed consent.

Exclusion

    Key Trial Info

    Start Date :

    September 1 2010

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ACTUAL

    End Date :

    June 1 2016

    Estimated Enrollment :

    38 Patients enrolled

    Trial Details

    Trial ID

    NCT01137721

    Start Date

    September 1 2010

    End Date

    June 1 2016

    Last Update

    August 23 2018

    Active Locations (1)

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    St. Jude Children's Research Hospital

    Memphis, Tennessee, United States, 38105