Status:

COMPLETED

Intra-Erythrocyte Dexamethasone Sodium Phosphate in Ataxia Teleangiectasia Patients

Lead Sponsor:

Quince Therapeutics S.p.A.

Conditions:

Nervous System Disorder

Genetic Syndrome

Eligibility:

All Genders

3+ years

Phase:

PHASE2

Brief Summary

The study has the aim to evaluate the improvement in CNS symptoms measured by International Co-operative Ataxia Rating Scale (ICARS) in patients with ataxia teleangectasia (AT), during a period of tre...

Detailed Description

This is a multi-centre, single arm, open label, 6 months, phase II study to evaluate the effect of ERY-DEX in improving Central Nervous System (CNS) symptoms in patients with Ataxia Teleangectasia (AT...

Eligibility Criteria

Inclusion

  • neurological signs of AT
  • patients in autonomous gait or helped by a support
  • proven molecular diagnosis of AT
  • Males and females aged \> 3 years
  • Body weight \>15 kg
  • Plasma levels of Lymphocytes CD4+/mm3 \> 500 (for patients aged 3-6 years) or \> 200 (older than 6 years)
  • written IC to participate.

Exclusion

  • Current or previous neoplastic disease
  • History of severe impairment of the immunological system
  • Chronic conditions representing a contraindication to the use of steroid drugs
  • Non compliance with the study request
  • Any previous steroid assumption within 30 days before starting ERY-DEX
  • Have any other significant disease that in the Investigator's opinion would exclude the patient from the trial
  • Females of childbearing potential who were pregnant, breast-feeding or were not using adequate contraceptive methods

Key Trial Info

Start Date :

February 1 2011

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

December 1 2011

Estimated Enrollment :

22 Patients enrolled

Trial Details

Trial ID

NCT01255358

Start Date

February 1 2011

End Date

December 1 2011

Last Update

October 10 2024

Active Locations (2)

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Page 1 of 1 (2 locations)

1

Spedali Civili

Brescia, Italy, 25123

2

University La Sapienza

Rome, Italy, 00185