Status:

COMPLETED

Study of Ranolazine in Myotonia Congenita, Paramyotonia Congenita and Myotonic Dystrophy Type 1

Lead Sponsor:

Ohio State University

Collaborating Sponsors:

Gilead Sciences

Conditions:

Myotonia Congenita

Paramyotonia Congenita

Eligibility:

All Genders

18-100 years

Phase:

PHASE1

Brief Summary

The purpose of this study is to gather preliminary data to determine if ranolazine is a safe and effective treatment for the symptoms of myotonia congenital, paramyotonia congenita, and myotonic dystr...

Detailed Description

Recent advances in the understanding of myotonia congenita have identified potential areas that could possibly respond to treatment in a drug study. The drug ranolazine (trade name Ranexa) is a FDA-ap...

Eligibility Criteria

Inclusion

  • Diagnosis of myotonia congenital, paramyotonia congenital or Myotonic Dystrophy Type 1 established by genetic testing in the subject or in a first-degree relative.
  • Clinically evident myotonia

Exclusion

  • Contraindications to ranolazine use:
  • for fungus infection: ketoconazole (Nizoral), itraconazole (Sporanox, Onmel)
  • for infection: clarithromycin (Biaxin)
  • for depression: nefazodone
  • for HIV: nelfinavir (Viracept), ritonavir (Norvir), lopinavir and ritonavir (Kaletra), indinavir (Crixivan), saquinavir (Invirase).
  • for tuberculosis (TB): rifampin (Rifadin), rifabutin (Mycobutin), rifapentine (Priftin)
  • for seizures: phenobarbital, phenytoin (Phenytek, Dilantin, Dilantin-125), carbamazepine (Tegretol)
  • the herbal supplement St. John's wort
  • you have scarring (cirrhosis) of your liver
  • Concurrent use of mexiletine, lacosamide, acetazolamide, phenytoin, quinine, procainamide, Saint John wort or tocainide. Patients who were previously treated with these medications may participate. They need to be off of the medication for at least a week prior to enrollment.
  • QTc \>470 ms for men and \>480 ms for women.
  • Women who are pregnant or breastfeeding
  • Direct family history of sudden cardiac death

Key Trial Info

Start Date :

August 1 2014

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

December 18 2017

Estimated Enrollment :

35 Patients enrolled

Trial Details

Trial ID

NCT02251457

Start Date

August 1 2014

End Date

December 18 2017

Last Update

March 5 2019

Active Locations (1)

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Page 1 of 1 (1 locations)

1

The Ohio State University Wexner Medical Center

Columbus, Ohio, United States, 43221

Study of Ranolazine in Myotonia Congenita, Paramyotonia Congenita and Myotonic Dystrophy Type 1 | DecenTrialz