Status:

COMPLETED

Efficacy & Safety Study of Bilateral IVT Injection of GS010 in LHON Subjects Due to the ND4 Mutation for up to 1 Year

Lead Sponsor:

GenSight Biologics

Conditions:

Leber Hereditary Optic Neuropathy

Eligibility:

All Genders

15+ years

Phase:

PHASE3

Brief Summary

The goal of this clinical trial is to assess the safety and efficacy of GS010, a gene therapy, in improving the retina functional \& structural outcomes in subjects with LHON due to the G11778A ND4 mi...

Detailed Description

GS-LHON-CLIN-05 is a Phase III, global, multi-center randomized, double-masked for the primary analysis, placebo-controlled, clinical study. As LHON is a neurodegenerative disease, the goal is to admi...

Eligibility Criteria

Inclusion

  • Main Selection Criteria:
  • Age 15 years or older on the date of signed informed consent.
  • Clinically manifested vision loss due to ND4 LHON, to any extent, in at least one eye.
  • Vision loss duration of ≤ 365 days (i.e. ≤ 1 year) in each affected eye at Inclusion Visit (Visit 2).
  • Main Non-Selection Criteria:
  • Contraindication to intravitreal injection in any eye.
  • Subjects refusing to discontinue idebenone.
  • Previous vitrectomy in either eye.
  • Narrow angle in any eye contra-indicating pupillary dilation.
  • Presence of known/documented mutations, other than the G11778A ND4 LHON-causing mutation, which are known to cause pathology of the optic nerve, retina or afferent visual system.
  • History of recurrent uveitis (idiopathic or immune-related) or active ocular inflammation.
  • Main
  • Vision loss duration of ≤ 365 days (i.e. ≤ 1 year) in each affected eye at Inclusion Visit (Visit 2).
  • Each eye of the subject must maintain at least Hand Motion (HM) visual acuity, as defined by the study's SOP for visual acuity testing.
  • Documented results of genotyping showing the presence of the G11778A mutation in the ND4 gene and the absence of the other primary LHON-associated mutations (ND1 or ND6) in the subject's mitochondrial DNA.
  • Main

Exclusion

  • Light Perception (LP) or No Light Perception (NLP) visual acuity in any eye, as defined by the study's standard operating procedure (SOP) for visual acuity testing.
  • Presence of active infectious conjunctivitis, keratitis, scleritis or endophthalmitis in either eye.
  • Presence of alcoholism, alcohol dependence, or alcohol or drug abuse (excluding nicotine).

Key Trial Info

Start Date :

March 12 2018

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

July 23 2024

Estimated Enrollment :

98 Patients enrolled

Trial Details

Trial ID

NCT03293524

Start Date

March 12 2018

End Date

July 23 2024

Last Update

August 26 2025

Active Locations (13)

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Page 1 of 4 (13 locations)

1

Doheny Eye Center UCLA Pasadena

Pasadena, California, United States, 91105

2

University of Colorado Health Eye Center

Aurora, Colorado, United States, 80045

3

Emory Healthcare - The Emory Clinic

Atlanta, Georgia, United States, 30322

4

Massachusetts Eye and Ear Infirmary

Boston, Massachusetts, United States, 02114