Status:

UNKNOWN

Gene Therapy of Beta Thalassemia Using a Self-inactivating Lentiviral Vector

Lead Sponsor:

Shenzhen Geno-Immune Medical Institute

Conditions:

Beta-Thalassemia

Eligibility:

All Genders

4-70 years

Phase:

NA

Brief Summary

This is a Phase I/II clinical trial of gene transfer for treating Beta-thalassemia using a self-inactivating lentiviral vector to functionally correct the defective gene(s). The objectives are to eval...

Detailed Description

Thalassemia is considered the most common genetic disorder worldwide. Beta-thalassemia is caused by mutations in the beta-globin gene which encodes the beta-globin protein, leading to the ineffective ...

Eligibility Criteria

Inclusion

  • Diagnosis of Beta Thalathemia.
  • Age: ≥ 4 years.
  • Karnofsky: ≥ 80%.
  • Left ventricular ejection fraction (LVEF): \> 50%; no obvious heart disease and pulmonary hypertension.
  • Pulmonary function is normal; forced expiratory volumein one second (FEV1) and vital capacity greater than 60% and DLCO \> 50%.
  • Serum creatinine ≤ 2 × upper limit of normal range.
  • MRI showed no super-iron load in the heart and liver, and no severe cirrhosis.
  • Normal Coagulation.
  • Written, informed consent obtained prior to any study-specific procedures.

Exclusion

  • Diagnosis of active malignant disease (other than Bowen disease or cervical cancer); or has family history of cancer.
  • Myelopathy, tumor-related cytogenetic changes or other more severe blood diseases.
  • Has alcoholism experience within 6 months prior to enrollment.
  • History of epilepsy.
  • History of bone marrow transplantation.
  • Existence of an available HLA-identical related donor.
  • Pregnant or lactating females.
  • Subject infected with HCV (HCV antibody positive), HBV (HBsAg positive), HIV (HIV antibody positive), HTLV (HTLV antibody positive), Treponema pallidum antibody positive or TB culture positive.
  • Patients, in the opinion of investigators, may not be eligible or not able to comply with the study.

Key Trial Info

Start Date :

December 1 2017

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

December 31 2020

Estimated Enrollment :

20 Patients enrolled

Trial Details

Trial ID

NCT03351829

Start Date

December 1 2017

End Date

December 31 2020

Last Update

November 30 2017

Active Locations (1)

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Shenzhen Geno-immune Medical Institute

Shenzhen, Guangdong, China, 518000