Status:

COMPLETED

Single-Dose Gene Replacement Therapy Clinical Trial for Participants With Spinal Muscular Atrophy Type 1

Lead Sponsor:

Novartis Gene Therapies

Conditions:

SMA

Eligibility:

All Genders

Up to 6 years

Phase:

PHASE3

Brief Summary

Phase 3, open-label, single-arm, single-dose, trial of onasemnogene abeparvovec-xioi (gene replacement therapy) in patients with spinal muscular atrophy (SMA) Type 1 who meet enrollment criteria and a...

Detailed Description

Phase 3, open-label, single-arm, single-dose, trial of onasemnogene abeparvovec-xioi (gene replacement therapy) in patients with spinal muscular atrophy (SMA) Type 1 who meet enrollment criteria and a...

Eligibility Criteria

Inclusion

  • Patients with SMA Type 1 as determined by diagnosis of SMA based on gene mutation analysis with biallelic SMN1 mutations (deletion or point mutations) and one or two copies of SMN2 \[inclusive of the known SMN2 gene modifier mutation (c.859G\>C)\]
  • Patients must be \< 6 months (\< 180 days) of age at the time of onasemnogene abeparvovec-xioi infusion
  • Patients must have a swallowing evaluation test performed prior to administration of gene replacement therapy

Exclusion

  • Previous, planned or expected scoliosis repair surgery/procedure prior to 18 months of age
  • Use of invasive ventilatory support (tracheotomy with positive pressure) or pulse oximetry \< 95% saturation at screening
  • Use or requirement of non-invasive ventilatory support for 12 or more hours daily in the two weeks prior to dosing
  • Patient with signs of aspiration based on a swallowing test or whose weight-for-age falls below the 3rd percentile based on World Health Organization (WHO) Child Growth Standards and unwilling to use an alternative method to oral feeding
  • Participation in recent SMA treatment clinical trial (with the exception of observational cohort studies or non-interventional studies) or receipt of an investigational or commercial compound, product or therapy administered with the intent to treat SMA (eg, nusinersen, valproic acid,) at any time prior to screening for this trial.

Key Trial Info

Start Date :

August 16 2018

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

September 11 2020

Estimated Enrollment :

33 Patients enrolled

Trial Details

Trial ID

NCT03461289

Start Date

August 16 2018

End Date

September 11 2020

Last Update

August 16 2022

Active Locations (10)

Enter a location and click search to find clinical trials sorted by distance.

Page 1 of 3 (10 locations)

1

University Hospital Ghent Neuromuscular reference center

Ghent, Belgium

2

Neuropédiatrie - Centre de Référence des Maladies Neuromusculaires

Liège, Belgium

3

Hôpital Armand Trousseau

Paris, France

4

Istituto Gianninia Gaslini

Genova, Italy