Status:

UNKNOWN

Natural History of GACI With or Without ARHR2 or PXE

Lead Sponsor:

Universität Münster

Collaborating Sponsors:

ICON plc

Conditions:

Generalized Arterial Calcification in Infancy

Autosomal Recessive Hypophosphatemic Rickets

Eligibility:

All Genders

Brief Summary

Generalized arterial calcification of infancy (GACI) is an ultra-rare disorder with an estimated birth prevalence of around 1 in 400,000.1 GACI is generally fatal before birth or within the first six ...

Detailed Description

Background: Generalized arterial calcification of infancy (GACI) is an ultra-rare disorder with an estimated birth prevalence of around 1 in 400,000.1 GACI is characterized by extensive arterial calc...

Eligibility Criteria

Inclusion

  • GACI genotype (mutation in ENPP1 and/or ABCC6) confirmed through mutational analysis of the patient and a GACI phenotype confirmed by imaging or biopsy; or
  • GACI phenotype confirmed with imaging, biopsy, or mutational analysis of the parents indicating a GACI genotype (mutation in ENPP1 and/or ABCC6) coinciding with symptoms of the patient.
  • Data will be collected for both living and deceased patients

Exclusion

  • Caregivers are not able to give written consent.

Key Trial Info

Start Date :

March 15 2018

Trial Type :

OBSERVATIONAL

Allocation :

ESTIMATED

End Date :

December 31 2019

Estimated Enrollment :

80 Patients enrolled

Trial Details

Trial ID

NCT03758534

Start Date

March 15 2018

End Date

December 31 2019

Last Update

November 29 2018

Active Locations (1)

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Page 1 of 1 (1 locations)

1

WWU Munster

Münster, Germany, 48149