Status:

TERMINATED

A Natural History Study of Aspartylglucosaminuria

Lead Sponsor:

Neurogene Inc.

Conditions:

Aspartylglucosaminuria

Aspartylglucosamidase (AGA) Deficiency

Eligibility:

All Genders

Brief Summary

Aspartylglucosaminuria (AGU) is a rare neurodegenerative lysosomal storage disease (LSD) characterized by developmental delay, psychomotor regression, worsening intellectual disability, gait disturban...

Detailed Description

Lysosomal storage disorders (LSDs) are a group of inherited metabolic diseases caused by a genetic mutation resulting in deficiency or absence of a critical enzyme, leading to the accumulation of toxi...

Eligibility Criteria

Inclusion

  • Participants must have a diagnosis of AGU based on clinical presentation and genetic testing (known or suspected pathogenic mutation in AGA gene).

Exclusion

  • Patients unable to travel to UT Southwestern Medical Center and Children's Health Dallas will not be enrolled in the prospective natural history study collecting standardized clinical data; however, with participant consent, medical records will be obtained, reviewed, and recorded in the natural history database over time.

Key Trial Info

Start Date :

April 18 2019

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

March 17 2022

Estimated Enrollment :

8 Patients enrolled

Trial Details

Trial ID

NCT03853876

Start Date

April 18 2019

End Date

March 17 2022

Last Update

April 12 2022

Active Locations (1)

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Page 1 of 1 (1 locations)

1

University of Texas Southwestern

Dallas, Texas, United States, 75390