Status:

ACTIVE_NOT_RECRUITING

Clinical Trial Readiness Network FSHD France: Prospective 24 Months MRI Study

Lead Sponsor:

Centre Hospitalier Universitaire de Nice

Conditions:

Muscular Dystrophy

Facioscapulohumeral

Eligibility:

All Genders

18-75 years

Phase:

NA

Brief Summary

The overall aim of this study is to hasten drug development for facioscapulohumeral muscular dystrophy (FSHD). Recent breakthroughs in FSHD research have identified the primary disease mechanism as th...

Eligibility Criteria

Inclusion

  • Inclusion Criteria
  • Genetically confirmed FSHD1 or clinical diagnosis of FSHD with characteristic findings on exam and an affected parent or offspring 63
  • Age 18-75 years
  • Symptomatic limb weakness
  • Patient able to walk alone or with a walking aid.
  • Manual Muscle Testing (MMT) score ≥ 4 for one of the lower limb muscles
  • Patient affiliated to the social security system
  • Patient giving written consent after written and oral information.
  • If taking over the counter supplements willing to remain consistent with supplement regimen throughout the course of the study
  • Exclusion Criteria
  • Cardiac or respiratory dysfunction (deemed clinically unstable, or would interfere with safe testing in the opinion of the Investigator)
  • Orthopedic conditions that preclude safe testing of muscle function
  • Regular use of available muscle anabolic/catabolic agents such as corticosteroids, oral testosterone or derivatives, or oral beta agonists
  • Use of an experimental drug in an FSHD clinical trial within the past 30 days
  • Pregnancy.
  • Contraindication for muscle MRI
  • Any major comorbidity

Exclusion

    Key Trial Info

    Start Date :

    September 16 2019

    Trial Type :

    INTERVENTIONAL

    Allocation :

    ACTUAL

    End Date :

    September 3 2026

    Estimated Enrollment :

    100 Patients enrolled

    Trial Details

    Trial ID

    NCT04038138

    Start Date

    September 16 2019

    End Date

    September 3 2026

    Last Update

    December 3 2025

    Active Locations (3)

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    Page 1 of 1 (3 locations)

    1

    CHRU de Lille

    Lille, Hauts-de-France, France, 59000

    2

    CHU de Nice

    Nice, Provence-Alpes-Côte d'Azur Region, France, 06000

    3

    Myology institute Association

    Paris, Île-de-France Region, France, 75013