Status:

RECRUITING

A Study of EPX-100 (Clemizole Hydrochloride) in Participants With Dravet Syndrome

Lead Sponsor:

Epygenix

Collaborating Sponsors:

Harmony Biosciences Management, Inc.

Conditions:

Dravet Syndrome

Eligibility:

All Genders

2+ years

Phase:

PHASE3

Brief Summary

This is a multicenter, Phase 3, randomized, double-blind, placebo-controlled study designed to evaluate the efficacy and safety of clemizole hydrochloride (EPX-100) as adjunctive therapy in children a...

Detailed Description

This is a global, multicenter, randomized, double-blind, placebo-controlled study to evaluate the safety and efficacy of clemizole hydrochloride as adjunctive therapy in children and adult participant...

Eligibility Criteria

Inclusion

  • Key
  • Male and female participants 2 years and older at time of consent.
  • Participant or parent/legally authorized representative (LAR) willing and able to provide written informed consent, assent (if applicable) prior to initiation of any study related procedures.
  • Clinical diagnosis of DS. Participants must have seizures which are not completely controlled by AEDs with the following criteria:
  • Onset of seizures prior to 18 months of age,
  • Normal development at onset,
  • History of at least one type of countable motor seizure (CMS),
  • Brain MRI without cortical malformation (not including mild atrophy associated with the natural progression of DS),
  • Genetic mutation of the SCN1A gene must be documented.
  • Key

Exclusion

  • Known sensitivity, allergy, or previous exposure to clemizole HCl.
  • Exposure to any investigational drug or device \<90 days prior to screening or plans to participate in another drug or device trial at any time during the study.
  • Seizures secondary to illicit drug (this includes concomitant use of tetrahydrocannabinol \[THC\] and nonprescription cannabidiol preparations) or alcohol use, infection, neoplasm, demyelinating disease, degenerative neurological disease, or central nervous system disease deemed progressive, metabolic illness, or progressive degenerative disease.
  • Concurrent use of lorcaserin. Note: Prior use of lorcaserin is permitted if at least 30 days have passed since the last dose.
  • Concurrent use of fenfluramine.
  • Epilepsy surgery planned during the study or epilepsy surgery within 6 months prior to Screening.

Key Trial Info

Start Date :

September 15 2020

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

May 1 2029

Estimated Enrollment :

150 Patients enrolled

Trial Details

Trial ID

NCT04462770

Start Date

September 15 2020

End Date

May 1 2029

Last Update

August 28 2025

Active Locations (46)

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Page 1 of 12 (46 locations)

1

Children's Hospital of Los Angeles

Los Angeles, California, United States, 90027

2

University of California Irvine

Orange, California, United States, 92868

3

UCSF Medical Center

San Francisco, California, United States, 94158

4

Yale University School of Medicine

New Haven, Connecticut, United States, 06510

A Study of EPX-100 (Clemizole Hydrochloride) in Participants With Dravet Syndrome | DecenTrialz