Status:

ACTIVE_NOT_RECRUITING

Non-contrast Lung Perfusion Mapping Applied for New Insights in Cystic Fibrosis

Lead Sponsor:

Children's Hospital Medical Center, Cincinnati

Conditions:

Cystic Fibrosis

Eligibility:

All Genders

6-21 years

Phase:

PHASE4

Brief Summary

Cystic fibrosis (CF) results in the thickening of mucus in the lungs and other organs due to dysfunction of a transmembrane conductance protein. This allows buildup of bacteria that results in inflamm...

Detailed Description

The Lung Perfusion in CF trial is a case-control observational study conducted at Cincinnati Children's Hospital. Patients will be assessed before and approximately 6 months after the clinical initia...

Eligibility Criteria

Inclusion

  • Inclusion CF Cohort
  • male or female between the ages of 6 through 21 years
  • diagnosis of CF by positive sweat test and genetic test
  • planning to start Trikafta based on clinical decision
  • baseline pulmonary function test (PFT) defined as FEV1% that is no less than 5% of the best PFT in the previous 6 months
  • Absence of exacerbation defined as
  • No acute antibiotic usage for 14 days prior to MRI visit
  • Able to perform an acceptable and reproducible spirometry
  • O2 saturation level at 90% or greater when laying flat
  • Inclusion Healthy Control Cohort
  • male or female between the ages of 6 through 21 years
  • no known diagnoses that impact lung function in the opinion of the investigators

Exclusion

  • Exclusion both cohorts
  • standard MRI exclusions (metal implants, claustrophobia)
  • pregnancy

Key Trial Info

Start Date :

November 15 2020

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

December 31 2026

Estimated Enrollment :

26 Patients enrolled

Trial Details

Trial ID

NCT04467957

Start Date

November 15 2020

End Date

December 31 2026

Last Update

January 7 2026

Active Locations (1)

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Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, United States, 45229