Status:

ACTIVE_NOT_RECRUITING

First-in-Human Study of TSHA-101 Gene Therapy for Treatment of Infantile Onset GM2 Gangliosidosis

Lead Sponsor:

Dr. Anupam Sehgal

Collaborating Sponsors:

Taysha Gene Therapies, Inc.

GlycoNet

Conditions:

Infantile GM2 Gangliosidosis (Disorder)

Eligibility:

All Genders

Up to 15 years

Phase:

PHASE1

PHASE2

Brief Summary

GM2 gangliosidoses are a group of autosomal recessive neurodegenerative diseases characterized by a deficiency of the Hex A enzyme to catabolize GM2, thereby causing GM2 accumulation within cellular l...

Eligibility Criteria

Inclusion

  • Key
  • male or female with age less than or equal to 15 months
  • diagnosis of GM2 gangliosidosis with genetic and enzymatic documentation of infantile disease
  • Key

Exclusion

  • a second neurodevelopmental disorder independent of the HEXA or HEXB
  • inability to tolerate sedation or intrathecal administration
  • invasive ventilatory support
  • concomitant illness, allergies or known hypersensitivity to the required immunosuppression regimen

Key Trial Info

Start Date :

March 12 2021

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

March 12 2027

Estimated Enrollment :

3 Patients enrolled

Trial Details

Trial ID

NCT04798235

Start Date

March 12 2021

End Date

March 12 2027

Last Update

May 9 2023

Active Locations (1)

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Page 1 of 1 (1 locations)

1

Queen's University/Kingston Health Sciences Centre

Kingston, Ontario, Canada, K7L 2V7