Status:

COMPLETED

Trehalose in Subjects With Neuronal Ceroid Lipofuscinoses

Lead Sponsor:

IRCCS Fondazione Stella Maris

Conditions:

Neuronal Ceroid-Lipofuscinoses

Eligibility:

All Genders

7-45 years

Brief Summary

Neuronal Ceroid Lipofuscinoses (NCL) or Batten's disease are the most common juvenile neurodegenerative disease, characterized by early blindness, movement disorders, cognitive and behavioral impairme...

Detailed Description

This study aims to collect clinical and laboratory data of patients with NCL taking Trehalose.

Eligibility Criteria

Inclusion

  • NCL genetic diagnosis (mutation in genes CLN3 or CLN6)
  • Signed informed consent

Exclusion

  • Other concomitant neurodegenerative diseases.
  • Therapeutic and eating changes in the last four months prior to the study
  • Unstable clinical conditions (myoclonus worsening, instability in sleep, parenteral nutrition)
  • Refusal to sign the informed consent

Key Trial Info

Start Date :

August 1 2020

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

October 1 2021

Estimated Enrollment :

8 Patients enrolled

Trial Details

Trial ID

NCT04808297

Start Date

August 1 2020

End Date

October 1 2021

Last Update

April 11 2022

Active Locations (1)

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IRCCS Fondazione Stella Maris

Pisa, PI, Italy, 56128