Status:

RECRUITING

(HARBOR) Study to Evaluate Efficacy and Safety of BLU-263 Versus Placebo in Patients With Indolent Systemic Mastocytosis

Lead Sponsor:

Blueprint Medicines Corporation

Conditions:

Indolent Systemic Mastocytosis

Smoldering Systemic Mastocytosis

Eligibility:

All Genders

18+ years

Phase:

PHASE2

PHASE3

Brief Summary

This is a randomized, double-blind, placebo-controlled, Phase 2/3 study comparing the efficacy and safety of elenestinib (BLU-263) + symptom directed therapy (SDT) with placebo + SDT in participants w...

Eligibility Criteria

Inclusion

  • Key
  • All Participants:
  • Participant must have an Eastern Cooperative Oncology Group Performance Status (ECOG PS) of 0 to 2.
  • Part 1 and PK groups:
  • Participant has confirmed diagnosis of ISM, confirmed by Central Pathology Review
  • Participant must have failed to achieve adequate symptom control for 1 or more Baseline symptoms, as determined by the Investigator, with at least 2 of the following symptom-directed therapies administered: H1 blockers, H2 blockers, proton-pump inhibitors, leukotriene inhibitors, cromolyn sodium, corticosteroids, or omalizumab.
  • Participants must have SDT for ISM symptom management stabilized for at least 14 days prior to starting screening procedures.
  • For participants receiving corticosteroids, the dose must be ≤ 20 mg/day prednisone or equivalent, and the dose must be stable for ≥ 14 days.
  • Part K:
  • Participant has confirmed diagnosis of ISM, confirmed by Central Pathology Review
  • Part S:
  • Participant has confirmed diagnosis of SSM, confirmed by Central Pathology Review of BM biopsy and central review of B- and C-findings by WHO diagnostic criteria.
  • Part 2:
  • Participant has confirmed diagnosis of ISM, confirmed by Central Pathology Review
  • Key

Exclusion

  • Participant has been diagnosed with any of the following WHO systemic mastocytosis (SM) sub-classifications: cutaneous mastocytosis only, SM with an associated hematologic neoplasm of non-MC lineage (SM-AHN), aggressive SM, mast cell leukemia, or mast cell sarcoma.
  • Participant has been diagnosed with another myeloproliferative disorder.
  • Participant has organ damage attributable to SM.
  • Participant has clinically significant, uncontrolled, cardiovascular disease
  • Participant has a QT interval corrected using Fridericia's formula (QTcF) \> \> 470 milliseconds (msec) (for females) or \> 450 msec (for males).
  • Participant has a history of a primary malignancy that has been diagnosed or required therapy within 3 years. The following prior malignancies are not exclusionary: completely resected basal cell and squamous cell skin cancer, curatively treated localized prostate cancer, and completely resected carcinoma in situ of any site.
  • Time since any cytoreductive therapy including masitinib and midostaurin should be at least 5 half-lives or 14 days (whichever is longer), and for cladribine, interferon alpha, pegylated interferon, or antibody therapy \< 28 days or 5 half-lives of the drug (whichever is longer), before beginning the screening period.
  • Participant has received radiotherapy or psoralen and ultraviolet A (PUVA) therapy \< 14 days before beginning the screening period.
  • Other protocol-defined criteria apply.

Key Trial Info

Start Date :

November 30 2021

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

September 30 2032

Estimated Enrollment :

534 Patients enrolled

Trial Details

Trial ID

NCT04910685

Start Date

November 30 2021

End Date

September 30 2032

Last Update

November 3 2025

Active Locations (54)

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Page 1 of 14 (54 locations)

1

University of Alabama at Birmingham

Birmingham, Alabama, United States, 35294

2

Stanford Cancer Institute

Palo Alto, California, United States, 94305

3

Brigham and Women's Hospital

Boston, Massachusetts, United States, 02115

4

Michigan Medicine University of Michigan

Ann Arbor, Michigan, United States, 48109