Status:

RECRUITING

Evaluation of Percutaneous Cryotherapy in the Treatment of Plexiform Neurofibromas and Unresectable Neurofibromas in Neurofibromatosis Type 1

Lead Sponsor:

Centre Leon Berard

Conditions:

Neurofibroma

Neurofibroma, Plexiform

Eligibility:

All Genders

18+ years

Phase:

NA

Brief Summary

Neurofibromatosis type 1 (NF1) is an autosomal dominant disease affecting chromosome 17. It is manifested by a neurogenic tumor proliferation that forms cutaneous, subcutaneous or deep neurofibromas. ...

Eligibility Criteria

Inclusion

  • Age ≥18 years;
  • Patient with neurofibromatosis type 1 according to NIH criteria ;
  • Patient with a benign neurofibromatous lesion that is painful and/or generates functional discomfort and is unresectable or with unacceptable scarring ;
  • Neutrophils \> 1 G/l in the 14 days prior to inclusion;
  • Adequate coagulation test with normals values (as judged by the investigator);
  • Signed and dated informed consent document indicating that the patient has been informed of all aspects of the trial prior to enrolment
  • Covered by a medical insurance;

Exclusion

  • Patient treated with concomitant chemotherapy and/or targeted therapies ;
  • Any contraindication to a percutaneous cryotherapy procedure, including the need for ice formation within 1 cm of the spinal cord, brain or other critical nerve structures, bowel or bladder (unless active or passive thermal protective maneuvers are performed);
  • Patient with malignant neurofibroma or MPNST ; CT scan without abnormality and if tumor presents a max SUV T/F\>1.5 ratio, targeted biopsy is required to confirm benign or malignant histology.
  • Patient with neurofibroma in areas at risk for neurological sequelae;
  • Patient with cold urticaria with history of angioedema;
  • Any cognitive impairment or condition that may limit the use of numerical scales and quality of life questionnaires;
  • Patient for whom follow-up does not seem feasible even in the short term;
  • Participation in another clinical trial that may interfere with the evaluation of the primary endpoint;
  • Patient under tutorshio, curatorship or deprived of liberty;
  • Pregnant or breast-feeding woman;
  • Any contraindication to the performance of an MRI
  • Patient with dysplastic neurofibroma

Key Trial Info

Start Date :

February 14 2022

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

February 7 2027

Estimated Enrollment :

30 Patients enrolled

Trial Details

Trial ID

NCT05199376

Start Date

February 14 2022

End Date

February 7 2027

Last Update

February 9 2024

Active Locations (1)

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1

Centre Leon Berard

Lyon, France, 69373