Status:

TERMINATED

Study to Evaluate the Effect on Nitrogen Retention of Two Different Posology Schemes of PKU GOLIKE PLUS 3-16 and Free AAs in Patients With Phenylketonuria

Lead Sponsor:

APR Applied Pharma Research s.a.

Conditions:

Phenylketonurias

Eligibility:

All Genders

3-20 years

Phase:

NA

Brief Summary

This is an open-label, randomized, 4-way crossover, monocentric, controlled study in patients (3 ≤ years of age ≤ 20 )) with phenylketonuria (PKU). The primary comparison will be between the test pro...

Detailed Description

This is an open-label, randomized, 4-way crossover, monocentric, controlled study in patients (3 ≤ years of age ≤ 20 ) with phenylketonuria (PKU). The primary comparison will be between the test prod...

Eligibility Criteria

Inclusion

  • Signed, informed consent obtained prior to being enrolled into the study and prior to starting any data collection. Consent of a legally authorized guardian is required for legally minor patients as defined by local regulation. If the patient is legally a minor, signed written consent shall be obtained from parent(s)/legal guardian and assent obtained from the patient, if applicable.
  • Male or female, aged 3-20 (limits included).
  • Patients with diagnosis of PKU at newborn screening.
  • Patients starting low Phe diet before 1 month of age.
  • Ability and willingness to comply with all study procedures and availability for the duration of the study.

Exclusion

  • Known or suspected hypersensitivity to any excipients/components of the investigational products.
  • Treatment with therapy for PKU other than amino-acids supplementation.
  • Patients aged \>12 years old with 4 repeated average values of blood Phe \>600 µM in the previous 6 months.
  • Patients aged \<12 years old with 4 repeated average values of blood Phe \>360 µM in the previous 6 months.
  • Any moderate to severe medical condition, which in the opinion of the Investigator would interfere with the study procedures or study outcome (reasoning to be provided), such as history of clinically significant diseases or malfunctions including, but not limited to, gastrointestinal, renal, hepatic, pulmonary, cardiovascular or endocrine disease, hemophilia, hyperlipidemia, impaired glucose tolerance or diabetes (type 1 or 2), or anemia.
  • History of poor co-operation, non-compliance with medical treatments and diet, or poor adherence to investigational procedures.
  • Any current participation in another clinical trial involving investigational or marketed products in the 3 months prior to the inclusion in this study.
  • Pregnancy or lactation.

Key Trial Info

Start Date :

May 6 2022

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

February 7 2023

Estimated Enrollment :

5 Patients enrolled

Trial Details

Trial ID

NCT05229549

Start Date

May 6 2022

End Date

February 7 2023

Last Update

July 7 2023

Active Locations (1)

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Page 1 of 1 (1 locations)

1

San Paolo Hospital

Milan, Italy