Status:

ACTIVE_NOT_RECRUITING

CNS10-NPC-GDNF Delivered to the Motor Cortex for ALS

Lead Sponsor:

Cedars-Sinai Medical Center

Collaborating Sponsors:

California Institute for Regenerative Medicine (CIRM)

Conditions:

Amyotrophic Lateral Sclerosis

Eligibility:

All Genders

18+ years

Phase:

PHASE1

Brief Summary

The investigator is examining the safety of transplanting cells, that have been engineered to produce a growth factor, into the motor cortex (brain) of patients with Amyotrophic Lateral Sclerosis (ALS...

Detailed Description

This study will be the first to use a genetically modified progenitor cell line delivered to the motor cortex to treat a neurodegenerative disease. This is a Phase 1/2a, single-center, safety study of...

Eligibility Criteria

Inclusion

  • Inclusion:
  • Confirmed diagnosis of ALS (Possible, Lab-supported Probable, Probable or Definite El Escorial Criteria)
  • Duration of ALS symptoms ≤ 36 months
  • Progressive weakness in upper extremities, with EMG supported evidence of denervation in both upper extremities
  • Forced Vital Capacity ≥50% of predicted normal in supine
  • Age: 18 years or older
  • Able to provide Informed Consent
  • Be geographically accessible to the study site and able to travel to study site for required visits
  • Have caregiver to assist in the transportation and care required by participation in the study
  • Not taking riluzole and/or edaravone or on a stable dose for ≥ 30 day
  • For women of child bearing capacity, negative pregnancy test prior to surgery and willingness to use birth control for the duration of the trial.
  • Medically able to undergo craniotomy as determined by the site PI and/or investigators
  • Medically able to tolerate the immunosuppression regimen as determined by the site PI
  • Exclusion:
  • Using invasive ventilatory assistance
  • Diagnosis of another active or unstable medical illness that may interfere with study participation at discretion of PI
  • Presence of any of the following conditions:
  • Current drug or alcohol abuse
  • Any known immunodeficiency syndrome
  • Unstable medical condition
  • Unstable psychiatric illness including psychosis and untreated major depression within 90 days of screening
  • Persons of child bearing capacity not willing to practice birth control
  • Receiving any investigational device/biologic/drug in the past 30 days or any previous exposure to stem cell therapy
  • Any condition in the upper extremities that precludes serial strength or coordination testing
  • Any condition that the investigators feel may pose complications for the surgery
  • Any condition or ALS disease phenotype that the site PI feels may interfere with participation in the study or in the interpretation of study endpoints
  • Allergy to Beta-Lactam antibiotics
  • Donor Specific Antibodies (DSA) ≥ 2500MFI or CPRA ≥ 20%
  • Contraindications to MRI

Exclusion

    Key Trial Info

    Start Date :

    May 8 2022

    Trial Type :

    INTERVENTIONAL

    Allocation :

    ESTIMATED

    End Date :

    October 1 2026

    Estimated Enrollment :

    16 Patients enrolled

    Trial Details

    Trial ID

    NCT05306457

    Start Date

    May 8 2022

    End Date

    October 1 2026

    Last Update

    August 19 2025

    Active Locations (1)

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    Page 1 of 1 (1 locations)

    1

    Cedars-Sinai Medical Center

    Los Angeles, California, United States, 90048

    CNS10-NPC-GDNF Delivered to the Motor Cortex for ALS | DecenTrialz