Status:

RECRUITING

Trial on the Biological and Clinical Effects of Acetyl-L-carnitine in ALS

Lead Sponsor:

Mario Negri Institute for Pharmacological Research

Collaborating Sponsors:

University of Sydney

FightMND

Conditions:

Amyotrophic Lateral Sclerosis

Eligibility:

All Genders

18+ years

Phase:

PHASE2

PHASE3

Brief Summary

Phase II/III multicenter, randomized, double-blind, placebo-controlled trial on acetyl-L-carnitine (ALCAR) in subjects living with amyotrophic lateral sclerosis (ALS). Primary study aim: The clinical ...

Eligibility Criteria

Inclusion

  • Age 18+;
  • ALS diagnosis according to the Gold Coast Criteria;
  • Disease duration \< 24 months from symptom onset, as indicated by limb weakness or bulbar symptoms, at the randomization/baseline visit\*;
  • Self-sufficiency \[Satisfactory bulbar and spinal function (score 3+ on the ALSFRS-R for swallowing, cutting food and handling utensils, and walking)\];
  • Satisfactory respiratory function (FVC ≥80% of predicted);
  • Documented progression of symptoms as measured by the ALSFRS-R scale. Disease progression rate (DFS) must be\>= 0.33. DFS =(48- ALSFRS-R at screening)/months from onset to screening.
  • Ability to understand and comply with the study requirements;
  • Ability to give written informed consent personally or, as an alternative, via a legally authorized representative;
  • Treatment with riluzole 50 mg twice/day for at least 4 weeks prior to randomization visit;
  • Intact cognitive function, again determined by the Principal Investigator.
  • The qualifying first symptoms of ALS are limited to manifestations of weakness in extremity, bulbar, or respiratory muscles. Cramps, fasciculations, or fatigue should not be taken in isolation as a first symptom of ALS.

Exclusion

  • Antecedent polio infection or other active infection;
  • Motor neuron disease (MND) other than ALS;
  • Involvement of other systems possibly determining a functional impairment (as measured by the endpoints) for the entire duration of the study;
  • Other severe clinical conditions (e.g., cardiovascular disorders, neoplasms) with an impact on survival or functional disability in the next 12 months;
  • Previous use of ALCAR for any reason;
  • Poor compliance with previous treatments;
  • Other experimental treatments in the three months prior to the screening visit (if a subject is receiving another experimental drug, a 3-month wash-out period before participating in the present clinical trial will be required);
  • Women who are lactating or able to become pregnant (e.g. who are not post-menopausal, surgically sterile, or using inadequate birth control) and men unable to practice contraception for the duration of the treatment and three months after its completion;
  • Inability to understand and comply with the study requirements;
  • Unwillingness or inability to take riluzole.

Key Trial Info

Start Date :

March 26 2025

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

September 1 2027

Estimated Enrollment :

246 Patients enrolled

Trial Details

Trial ID

NCT06126315

Start Date

March 26 2025

End Date

September 1 2027

Last Update

September 25 2025

Active Locations (19)

Enter a location and click search to find clinical trials sorted by distance.

Page 1 of 5 (19 locations)

1

Concord Hospital

Sydney, Australia, 2139

2

Azienda Socio Sanitaria Territoriale Papa Giovanni XXIII, Dipartimento di Neurologia

Bergamo, Italy, 24127

3

Fondazione Serena ONLUS Centro Clinico NEMO Brescia

Brescia, Italy, 25064

4

Istituto Auxologico Italiano, IRCCS Dipartimento di Neurologia

Milan, Italy, 20149