Evaluating Accuracy of Home Lactate and Glucose Meters in Patients With Glycogen Storage Disease Types Ia, Ib, and XI

What this Trial Is About

This research aims to evaluate the accuracy of two home monitoring devicesthe Lactate Plus meter and the Accu-Chek Guide glucometerin patients with Glycogen Storage Disease Types Ia, Ib, and XI. The study focuses on comparing these devices readings with laboratory serum lactate and glucose levels to determine their reliability for this patient group. Participants will have a one-time planned hospital admission lasting about 8 hours, during which they will undergo hourly blood draws and finger-stick tests. These measurements will be used to compare the device readings against lab results throughout the 8-hour period. During the study visit, patients will have blood samples taken every hour alongside finger-stick glucose checks. Researchers will assess whether the Lactate Plus meter and Accu-Chek glucometer readings are within 20% of the laboratory values 95% of the time. This careful monitoring and comparison will help determine the accuracy of these home testing devices for managing Glycogen Storage Disease.

Accuracy of Home Lactate Meter and Accu-chek Glucometer in Patients With Glycogen Storage Disease