Actively Recruiting

Phase 2
Age: 0 - 65Years
All Genders
ID03579875

T Cell Receptor Alpha/Beta T Cell Depleted Hematopoietic Cell Transplantation in Patients With Inherited Bone Marrow Failure Disorders

Led by Masonic Cancer Center, University of Minnesota · Updated on 2026-01-30

48

Participants Needed

1

Research Sites

105 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Researchers are evaluating a phase II trial of T cell receptor alpha/beta depletion (α/β TCD) peripheral blood stem cell transplantation in patients with inherited bone marrow failure (BMF) disorders. The goal is to avoid routine immune suppression for graft-versus-host disease (GVHD), allowing earlier immune recovery and potentially reducing severe infection risks after transplantation. This trial is sponsored by the Masonic Cancer Center, University of Minnesota. Participants receive one of several treatment plans involving drugs such as total body irradiation (TBI), cyclophosphamide, fludarabine, methylprednisolone, rituximab, busulfan, alemtuzumab, melphalan, and a T cell receptor α/β depleted peripheral blood stem cell infusion on day 0. The conditioning regimens vary based on disease features, donor type, and patient tolerance, with some patients receiving TBI and others alternative drug combinations. G-CSF is administered after transplant to support neutrophil recovery. During the study, participants undergo monitoring for immune recovery and complications including acute and chronic GVHD, engraftment of neutrophils and platelets, infections, regimen-related toxicity, and overall survival up to one year after transplant. Evaluations include clinical assessments and laboratory tests at defined time points such as day 42, day 100, and one year post-transplant. The study aims to describe outcomes for approximately 3 to 5 patients treated annually under these protocols.

CONDITIONS

Brief Title

Alpha/Beta TCD HCT in Patients With Inherited BMF Disorders

Who Can Participate

Age: 0 - 65Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Diagnosis of Fanconi anemia with age under 65 years
  • Severe aplastic anemia, myelodysplastic features, high risk genotype, or immunodeficiency with recurrent infections
  • Karnofsky performance status ≥ 70% if 16 years or older, or Lansky play score ≥ 50% if younger than 16
  • Adequate pulmonary, cardiac, and liver function
  • Voluntary written consent (minor assent if appropriate)
  • Diagnosis of telomere biology disorder with age under 70 years
  • Same risk factors and performance status as for Fanconi anemia patients
  • Adequate organ function
  • Donor matching criteria including HLA-matched sibling or related donors, mismatched related donors, or matched unrelated donors
  • Donor weight at least 40 kilograms and age at least 12 years
  • Donor able to undergo mobilized peripheral blood apheresis and in good health
  • Donor organ function within specified laboratory limits
  • Donor negative for infections including HIV, hepatitis, and others
  • Negative pregnancy test for females of childbearing potential
  • Voluntary written consent for donors (parent/guardian and minor assent if under 18)
Not Eligible

You will not qualify if you...

  • Pregnant or breastfeeding females
  • Active uncontrolled infection within one week before starting treatment
  • Malignant solid tumor cancer within two years prior to study
  • Donors who are pregnant or positive for certain infections
  • Donors not meeting organ function or health requirements
  • Inability to provide voluntary written consent or minor assent if appropriate

AI-Screening

AI-Powered Screening

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Your Study Journey

Screening

Duration - 2 to 4 weeks

Participants are screened for eligibility to participate in the trial.

1 visit (in-person)

Treatment

Duration - Approximately 2 weeks

Participants receive conditioning drugs and undergo T cell receptor alpha/beta depleted peripheral blood stem cell transplantation.

Multiple visits from day -6 through day 0 for conditioning and transplantation

Follow-up

Duration - Up to 1 year after transplant

Participants are monitored for graft versus host disease, engraftment, infections, and overall survival after transplantation.

Regular visits for assessments up to 1 year post-transplant

Trial Site Locations

Total: 1 location

1

Masonic Cancer Center at University of Minnesota

Minneapolis, Minnesota, United States, 55455

Actively Recruiting

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Research Team

M

Margaret MacMillan, MD, Msc, FRCPC

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NON_RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

5

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