Actively Recruiting

Phase 3
Age: 6Months +
All Genders
NCT05476939

Biological Medicine for Diffuse Intrinsic Pontine Glioma (DIPG) Eradication 2.0

Led by Gustave Roussy, Cancer Campus, Grand Paris · Updated on 2026-02-05

433

Participants Needed

50

Research Sites

465 weeks

Total Duration

On this page

Sponsors

G

Gustave Roussy, Cancer Campus, Grand Paris

Lead Sponsor

I

Innovative Therapies For Children with Cancer Consortium

Collaborating Sponsor

AI-Summary

What this Trial Is About

The BIOMEDE 2.0 study is the second stage of the BIOMEDE multi-arm, multistage rolling programme (adaptive platform protocol). It is a multicenter, randomized, open-label, controlled phase-3 trial evaluating efficacy of ONC201 in comparison with everolimus (primary objective based on internal comparison) and subsequently to historical controls. Two treatment groups will be compared. A switch between treatment groups is allowed after confirmation of the disease progression (real-time central review blinded to the treatment arm allocation). Study treatment will be continued until centrally confirmed disease progression (either radiologically or histologically), unacceptable toxicity or consent withdrawal. The final conclusion of the trial will be successful for ONC201, if ONC201 is found significantly superior to everolimus in terms of centrally-reviewed PFS (Progression-free survival) from randomization (internal comparison) either overall, considering ND-DMG and DIPG-patients together, or in the subgroup of ND-DMG patients alone. In other cases, Everolimus will remain the standard arm unless it appears associated with an excess of toxicity compared to ONC201 which could then be discussed as a new standard.

CONDITIONS

Official Title

Biological Medicine for Diffuse Intrinsic Pontine Glioma (DIPG) Eradication 2.0

Who Can Participate

Age: 6Months +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Diagnosis of DIPG by clinical and radiological criteria or histological/molecular confirmation including H3K28M mutation or EZHIP overexpression.
  • Eligible for biopsy or have biopsy material available for biomarker assessment.
  • Age greater than 6 months, with no upper age limit; children between 6 months and 3 years considered individually for biopsy feasibility.
  • Eligible for cerebral or craniospinal radiotherapy.
  • No prior chemotherapy or cerebral radiation therapy for the current cancer; surgery allowed for diagnosis or therapy.
  • Patients with metastatic or spinal tumors allowed; radiotherapy timing adjusted accordingly.
  • Affiliated with a social security system or equivalent.
  • Written informed consent from patient and/or legal representative and age-appropriate assent obtained as per guidelines.
  • Life expectancy greater than 12 weeks after treatment start.
  • Karnofsky or Lansky performance status above 50%, excluding neurological deficit as a factor.
  • Use of highly effective contraception for patients of reproductive potential during and for 6 months after treatment.
  • Negative pregnancy test within one week prior to randomization for sexually active females.
  • Adequate blood counts, liver and kidney function, and normal coagulation tests within local reference ranges.
  • Written informed consent for randomization obtained according to regulations.
Not Eligible

You will not qualify if you...

  • Uncontrolled spontaneous massive intratumor bleeding; controlled post-operative bleeding allowed.
  • Concurrent anti-cancer treatments not in protocol except corticosteroids and bevacizumab (with restrictions).
  • Diagnosis of any other cancer within the last 5 years.
  • Uncontrolled illness or active infection.
  • Co-morbid conditions impairing study participation as judged by investigator.
  • Inability to comply with medical follow-up.
  • Previous brainstem irradiation for another cancer.
  • Participation in another investigational clinical study during treatment.
  • Under legal guardianship or deprived of liberty or unable to consent.
  • Current organ toxicity above grade 2, especially cardiac or renal diseases.
  • Specific cardiac histories prohibiting ONC201 use, including prolonged QT interval or related risk factors.
  • Pregnant or breastfeeding women.
  • Known hypersensitivity to everolimus or ONC201 components; such patients assigned to alternate treatment arms.
  • Patients with congenital galactose intolerance, lactase deficiency, or glucose-galactose malabsorption assigned to ONC201 arm unless contraindicated.
  • Use of strong P450 or PgP inhibitors/inducers requires monitoring or alternative medications during everolimus treatment.

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 50 locations

1

Aarhus Universitetshospital Skejby

Aarhus, Denmark, 8200

Actively Recruiting

2

Rigshospitalet

Copenhagen, Denmark, 2100

Actively Recruiting

3

H.C. Andersen Children's Hospital, Odense Universitetshospital

Odense, Denmark, 5000

Actively Recruiting

4

Gustave Roussy

Villejuif, Val de Marne, France, 94805

Actively Recruiting

5

CHU d'Amiens-Picardie Site Sud

Amiens, France, 80054

Actively Recruiting

6

Institut de Cancérologie de l'Ouest (ICO) - Site Paul Papin

Angers, France, 49055

Actively Recruiting

7

CHU d'Angers - Bâtiment Robert Debré

Angers, France, 49933

Actively Recruiting

8

CHU Besançon - Hôpital Jean Minjoz

Besançon, France, 25030

Actively Recruiting

9

CHU de Bordeaux - Groupe hospitalier Saint André - Hôpital Saint André

Bordeaux, France, 33000

Actively Recruiting

10

CHU de Bordeaux - Groupe hospitalier Pellegrin - Hôpital des enfants

Bordeaux, France, 33076

Actively Recruiting

11

CHRU de Brest - Hôpital Morvan

Brest, France, 29609

Actively Recruiting

12

CHU de Caen - Hôpital Côte de Nacre

Caen, France, 14033

Actively Recruiting

13

CHU Estaing

Clermont-Ferrand, France, 63003

Actively Recruiting

14

Centre Jean Perrin

Clermont-Ferrand, France, 63011

Actively Recruiting

15

CHU François Mitterrand

Dijon, France, 21079

Actively Recruiting

16

CHU Grenoble Alpes - Hôpital Albert Michallon

Grenoble, France, 38700

Not Yet Recruiting

17

CHU Grenoble Alpes - Hôpital Couple-Enfant

Grenoble, France, 38700

Actively Recruiting

18

Centre Oscar Lambret

Lille, France, 59020

Actively Recruiting

19

Hôpital Roger Salengro

Lille, France, 59037

Not Yet Recruiting

20

Hôpital de la mère et de l'enfant

Limoges, France, 87042

Actively Recruiting

21

Centre Léon Bérard

Lyon, France, 69373

Actively Recruiting

22

Hôpital Pierre Wertheimer

Lyon, France, 69500

Actively Recruiting

23

Hôpital de La Timone

Marseille, France, 13005

Actively Recruiting

24

Hôpital Arnaud de Villeneuve

Montpellier, France, 34090

Actively Recruiting

25

CHRU Nancy - Hôpital central

Nancy, France, 54035

Actively Recruiting

26

CHRU Nancy Brabois - Hôpital d'enfants

Nancy, France, 54500

Actively Recruiting

27

CHU de Nice - Hôpital Pasteur 2

Nice, France, 06000

Actively Recruiting

28

CHU de Nice - Hôpital L'Archet 2

Nice, France, 06202

Actively Recruiting

29

Hôpital Saint Louis

Paris, France, 75010

Actively Recruiting

30

Hôpitaux Universitaires La Pitié Salpêtrière-Charles Foix

Paris, France, 75013

Actively Recruiting

31

Institut Curie

Paris, France, 75248

Actively Recruiting

32

CHU Poitiers

Poitiers, France, 86021

Actively Recruiting

33

CHU de Reims - American Memorial Hospital 2

Reims, France, 51092

Actively Recruiting

34

Centre Eugène Marquis

Rennes, France, 35042

Actively Recruiting

35

CHU Rennes - Hôpital Sud

Rennes, France, 35203

Actively Recruiting

36

CHU Rouen Normandie - Hôpital Charles-Nicolle

Rouen, France, 76000

Actively Recruiting

37

CHU de Saint-Denis de La Réunion

Saint-Denis, France, 97400

Actively Recruiting

38

CHU de Saint-Etienne - Hôpital Nord

Saint-Etienne, France, 42270

Actively Recruiting

39

CHU de Saint-Pierre de La Réunion Sud

Saint-Pierre, France, 97488

Not Yet Recruiting

40

Centre Régional Lutte Contre le Cancer Paul STRAUSS

Strasbourg, France, 67065

Actively Recruiting

41

Hôpital de Hautepierre

Strasbourg, France, 67200

Actively Recruiting

42

Hôpital Foch

Suresnes, France, 92150

Not Yet Recruiting

43

Hôpital des enfants

Toulouse, France, 31059

Actively Recruiting

44

Institut Universitaire du Cancer de Toulouse-Oncopole (IUCT-O) - Institut Claudius Regaud

Toulouse, France, 31059

Actively Recruiting

45

CHRU Tours - Hôpital Clocheville

Tours, France, 37000

Actively Recruiting

46

CHRU Tours - Hôpital Bretonneau

Tours, France, 37044

Actively Recruiting

47

Hospital Vall D´Hebron

Barcelona, Spain, 8035

Actively Recruiting

48

Hospital Universitario Niño Jesus

Madrid, Spain, 28009

Actively Recruiting

49

Hospital Universitario y Politécnico de La Fe

Valencia, Spain, 46026

Actively Recruiting

50

Karolinska University Hospital

Stockholm, Sweden, 17176

Actively Recruiting

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Research Team

J

Jacques GRILL, MD, PhD

CONTACT

A

Anne-Sophie BLANC, PharmD

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

RANDOMIZED

Model

CROSSOVER

Primary Purpose

TREATMENT

Number of Arms

2

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Biological Medicine for Diffuse Intrinsic Pontine Glioma (DIPG) Eradication 2.0 | DecenTrialz