Actively Recruiting

Phase 2
Age: 18Years +
All Genders
NCT07171905

CAT-VHL Exploring the Role of Carbonic Anhydrase IX as Diagnostic and Theranostic Target in Von-Hippel Lindau Disease

Led by IRCCS Ospedale San Raffaele · Updated on 2026-03-09

38

Participants Needed

1

Research Sites

44 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

The study is a phase 2, non-comparative and non-randomized, single arm, national clinical trial testing the hypothesis that CAIX-PET has diagnostic and theranostic potential in VHL disease and in VHL-/- tumors. Participants will receive a single dose of the diagnostic radiopharmaceutical \[89Zr\]Zr-DFO-Girentuximab and subsequently will be subjected to imaging with an hybrid PET/CT scanner. Sensitivity and diagnostic accuracy of experimental imaging will be assessed against standard of truth derived from standard of care procedures such as MRI or pathology following surgery. A theranostic approach will be simulated by replacing the physical decay of the diagnostic isotope \[89Zr\]Zr with the physical decay of therapeutic isotopes and evaluating tissue dosimetry.

CONDITIONS

Official Title

CAT-VHL Exploring the Role of Carbonic Anhydrase IX as Diagnostic and Theranostic Target in Von-Hippel Lindau Disease

Who Can Participate

Age: 18Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Voluntarily given informed consent
  • Age 18 years or older
  • Performance Status ECOG/WHO score 0-2
  • For females of reproductive potential, negative pregnancy test and use of highly effective contraception for 30 days following radiopharmaceutical administration
  • For males of reproductive potential, use of highly effective contraception for 30 days following radiopharmaceutical administration
  • Diagnosis of VHL disease requiring surveillance confirmed by genetic testing
  • Alternatively, clinical or pathological diagnosis of hemangioblastoma, pheochromocytoma, pancreatic neuroendocrine tumor, or clear cell renal cell carcinoma requiring surgery
Not Eligible

You will not qualify if you...

  • Performance Status ECOG/WHO score greater than 2
  • Women who are pregnant, breastfeeding, or planning pregnancy during the study
  • Men planning fatherhood during the study
  • Exposure to any murine or chimeric antibodies within 5 years prior to planned radiopharmaceutical administration
  • Exposure to any experimental diagnostic or therapeutic drug within 30 days prior to planned radiopharmaceutical administration
  • Surgery, biopsy, ablative procedure, radiotherapy, or other local treatment for any primary tumor within 4 weeks prior to planned radiopharmaceutical administration
  • Exposure to systemic agents within 4 weeks prior to planned radiopharmaceutical administration or ongoing adverse effects greater than grade 1 from such therapy
  • Current exposure to systemic agents or scheduled therapy in the 6 months following planned radiopharmaceutical administration
  • Serious non-malignant diseases that may interfere with study objectives or safety, as judged by the investigator
  • Known hypersensitivity to [89Zr]Zr-DFO-Girentuximab or DFO (Desferrioxamine)
  • Severe chronic kidney disease with glomerular filtration rate less than or equal to 30 mL/min/1.73m2
  • Other vulnerable categories besides rare disease, such as being in detention

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 1 location

1

IRCCS Ospedale San Raffaele

Milan, Italia, Italy, 20132

Actively Recruiting

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Research Team

A

Alessandro Larcher

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

SINGLE_GROUP

Primary Purpose

DIAGNOSTIC

Number of Arms

1

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CAT-VHL Exploring the Role of Carbonic Anhydrase IX as Diagnostic and Theranostic Target in Von-Hippel Lindau Disease | DecenTrialz