Actively Recruiting

Age: 6Years +
All Genders
ID06865482

Characteristics and Clinical Course of Disease in Participants With Cardiomyopathy Associated With Friedreich Ataxia (CLARITY-FA)

Led by Lexeo Therapeutics · Updated on 2026-06-08

65

Participants Needed

19

Research Sites

N/A

Total Duration

On this page

AI-Summary

What this Trial Is About

Researchers are studying the characteristics and progression of cardiomyopathy linked to Friedreich Ataxia (FA-CM), a genetic condition affecting the heart. This observational, global study aims to understand how cardiac disease presents and changes over time in participants diagnosed with FA-CM. The study includes both children and adults with genetically confirmed FA-CM and left ventricular hypertrophy and reduced ejection fraction. Participants are divided into two groups based on age: those 16 years and older, and those between 6 and under 16 years old. The study follows participants for at least 26 weeks to track disease progression. After this period, eligible participants may have a chance to join an interventional gene therapy study. The study involves no investigational treatments but focuses on monitoring disease features and changes. During the study, participants undergo assessments including cardiac imaging to evaluate heart structure and function, laboratory tests such as measuring high sensitivity troponin I, and questionnaires assessing illness perception and severity. Researchers will measure changes in left ventricular wall thickness, mass, ejection fraction, medication use, and evaluate major cardiovascular events and mortality over 12 months. The total participation duration and follow-up include detailed evaluations to better understand FA-CM progression.

CONDITIONS

Brief Title

Clinical Course Of Disease In Participants With FA-CM

Who Can Participate

Age: 6Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male or female aged 6 years or older at the time of consent
  • Diagnosis of Friedreich Ataxia confirmed by clinical signs and genetic testing with onset at age 25 years or younger
  • Confirmed left ventricular hypertrophy (LVH)
  • Left ventricular ejection fraction of 40% or higher
Not Eligible

You will not qualify if you...

  • Presence of other types of cardiomyopathy causing heart failure or significant heart abnormalities not due to FA-CM
  • Receiving intermittent or continuous intravenous inotrope infusion
  • History of ventricular assist device or prior heart transplantation
  • Contraindication to cardiac MRI; children under 12 who cannot complete MRI without sedation will have echocardiograms instead
  • Prior organ transplantation
  • Started cardiac resynchronization therapy within 6 months before screening
  • History of gene transfer or cell therapy
  • Poorly controlled diabetes with hemoglobin A1c of 8% or higher
  • Active blood or solid organ cancer

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

1
2
3
+1

Your Study Journey

Screening

Duration - 2 to 4 weeks

Participants are screened for eligibility to participate in the trial.

1 visit (in-person)

Long-term Monitoring

Duration - Up to 12 months

Participants are observed over time to characterize the nature and rate of cardiac disease progression associated with Friedreich Ataxia cardiomyopathy (FA-CM).

Multiple visits over 12 months to assess cardiac disease progression and health status

Trial Site Locations

Total: 19 locations

1

University of California San Diego

La Jolla, California, United States, 92037

Actively Recruiting

2

University of South Florida

Tampa, Florida, United States, 33612

Actively Recruiting

3

Indiana University - Riley Children's Health

Indianapolis, Indiana, United States, 46202

Actively Recruiting

4

Boston Children's Hospital

Boston, Massachusetts, United States, 02115

Actively Recruiting

5

Mayo Clinic

Rochester, Minnesota, United States, 55905

Actively Recruiting

6

Washington University School of Medicine in St. Louis

St Louis, Missouri, United States, 63110

Actively Recruiting

7

Cincinnati Children's Hospital

Cincinnati, Ohio, United States, 45229

Actively Recruiting

8

Oregon Health & Science University

Portland, Oregon, United States, 97239

Actively Recruiting

9

Hospital Universitário Walter Cantídio - Universidade Federal do Ceará

Fortaleza, Ceará, Brazil, 60430

Actively Recruiting

10

Instituto D'or de Pesquisa e Ensino - Hospital São Rafael

Salvador, Estado de Bahia, Brazil, 41253-190

Actively Recruiting

11

Hospital Das Clínicas Da Universidade Federal De Minas Gerais (UFMG)

Belo Horizonte, Minas Gerais, Brazil, 30130

Actively Recruiting

12

Campinas State University (UNICAMP)

Campinas, São Paulo, Brazil, 13083-887

Actively Recruiting

13

UPC Hospital das Clínicas da Faculdade de Medicina de Ribeirão Preto

Ribeirão Preto, São Paulo, Brazil, 14051

Actively Recruiting

14

Centre Hospitalier de Universite de Montreal (CHUM)

Montreal, Quebec, Canada, H2X 0C1

Actively Recruiting

15

Motol University Hospital and the Second Faculty of Medicine

Prague, Czechia, 15006

Actively Recruiting

16

Institut de Cardiologie Hopital Pitie Salpetriere

Paris, France, 75013

Actively Recruiting

17

University Hospital Tübingen

Tübingen, Baden-Wurttemberg, Germany, 72076

Actively Recruiting

18

Federico II University

Naples, Italy, 80131

Actively Recruiting

19

Hospital Univeritario Puerta de Hierro de Majadahonda

Majadahonda, Madrid, Spain, 28222

Actively Recruiting

Loading map...

Research Team

L

Lexeo Clinical Trials

How is the study designed?

Study Type

OBSERVATIONAL

Masking

N/A

Allocation

N/A

Model

N/A

Primary Purpose

N/A

Number of Arms

2

Similar Trials

A Bioequivalence Study of Two Formulations of HRS-1893 Table...

Cardiomyopathy

Actively Recruiting

1 location

A Phase 1/2, Open-Label, Multiple Ascending Dose Study to As...

Friedreich Ataxia

Actively Recruiting

3 locations

Clinical Evaluation of Arrhythmia Mapping With a Paddle-shap...

Scar-related Atrial Tachycardia

Actively Recruiting

6 locations

Frequently Asked Questions

Have more questions? Get in touch with our team for quick support

Not the Right Trial for You?

Explore thousands of other clinical trials that might be a better match.
Sign up to get personalized trial recommendations delivered to your inbox.

Already have an account? Log in here