Actively Recruiting

Phase 2
Age: 2Years - 100Years
All Genders
NCT06997588

EPIK-P4: A Phase II Single-arm Study to Assess the Efficacy, Safety and Pharmacokinetics of Alpelisib (BYL719) in Pediatric and Adult Patients With PIK3CA-related Overgrowth Spectrum (PROS)

Led by Novartis Pharmaceuticals · Updated on 2026-04-30

104

Participants Needed

30

Research Sites

259 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

This study is designed to demonstrate the efficacy and assess safety and tolerability of oral daily alpelisib in participants with PIK3CA-related overgrowth spectrum (PROS).

CONDITIONS

Official Title

EPIK-P4: A Phase II Single-arm Study to Assess the Efficacy, Safety and Pharmacokinetics of Alpelisib (BYL719) in Pediatric and Adult Patients With PIK3CA-related Overgrowth Spectrum (PROS)

Who Can Participate

Age: 2Years - 100Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male or female participants aged 652 years at the time of informed consent or assent
  • Diagnosis of PROS with symptomatic and progressive overgrowth, including syndromic disease or isolated features except isolated macrodactyly, macrocephaly or epidermal nevus
  • Documented somatic mutation in the PIK3CA gene confirmed by DNA-based test and available archival tissue or fresh biopsy if needed
  • Karnofsky performance status 6550 for participants older than 16 years or Lansky performance status 6550 for those 16 years or younger
  • PGI-S score of mild, moderate, severe, or very severe at screening
  • Adequate bone marrow and organ function
  • At least one measurable PROS-related lesion (longest diameter 652 cm) confirmed by BIRC and causing complaints, symptoms, or functional limitations affecting daily life
Not Eligible

You will not qualify if you...

  • Participants with only isolated macrodactyly, epidermal nevus/nevi, and macroencephaly without other PROS-related lesions
  • Previous treatment with alpelisib or other PI3K inhibitors except short treatment attempts less than 2 weeks stopped at least 4 weeks before study
  • Major surgery within 3 months prior to consent or assent
  • Radiation treatment for PROS within 12 months prior to consent or assent
  • Significant PROS-related thrombotic event (Grade 2 or higher) within 30 days before consent or assent
  • Sclerotherapy or embolization for vascular complications within 6 weeks before consent or assent
  • Clinically significant bleeding from a PROS lesion (Grade 2 or higher) within 30 days before treatment start
  • Worsening PROS-related lab abnormalities or symptoms indicating uncontrolled condition during screening

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 30 locations

1

Washington University

St Louis, Missouri, United States, 63110

Actively Recruiting

2

Cinn Children Hosp Medical Center

Cincinnati, Ohio, United States, 45206

Actively Recruiting

3

Novartis Investigative Site

Sydney, New South Wales, Australia, 2010

Actively Recruiting

4

Novartis Investigative Site

Sydney, New South Wales, Australia, 2031

Actively Recruiting

5

Novartis Investigative Site

North Adelaide, South Australia, Australia, 5066

Actively Recruiting

6

Novartis Investigative Site

Salzburg, Austria, 5020

Actively Recruiting

7

Novartis Investigative Site

Vienna, Austria, A 1090

Actively Recruiting

8

Novartis Investigative Site

Ghent, Belgium, 9000

Actively Recruiting

9

Novartis Investigative Site

Angers, France, 49933

Actively Recruiting

10

Novartis Investigative Site

Bron, France, 69677

Actively Recruiting

11

Novartis Investigative Site

Dijon, France, 21000

Actively Recruiting

12

Novartis Investigative Site

Montpellier, France, 34295

Actively Recruiting

13

Novartis Investigative Site

Paris, France, 75015

Actively Recruiting

14

Novartis Investigative Site

Toulouse, France, 31400

Actively Recruiting

15

Novartis Investigative Site

Tours, France, 37044

Actively Recruiting

16

Novartis Investigative Site

Freiburg im Breisgau, Baden-Wurttemberg, Germany, 79106

Actively Recruiting

17

Novartis Investigative Site

Düsseldorf, North Rhine-Westphalia, Germany, 40225

Actively Recruiting

18

Novartis Investigative Site

Leipzig, Saxony, Germany, 04103

Actively Recruiting

19

Novartis Investigative Site

Halle, Saxony-Anhalt, Germany, 06120

Actively Recruiting

20

Novartis Investigative Site

Berlin, Germany, 13353

Actively Recruiting

21

Novartis Investigative Site

Stuttgart, Germany, 70374

Actively Recruiting

22

Novartis Investigative Site

Roma, RM, Italy, 00168

Actively Recruiting

23

Novartis Investigative Site

Torino, TO, Italy, 10126

Actively Recruiting

24

Novartis Investigative Site

Trieste, TS, Italy, 34137

Actively Recruiting

25

Novartis Investigative Site

Esplugues, Barcelona, Spain, 08950

Actively Recruiting

26

Novartis Investigative Site

A Coruña, Spain, 15006

Actively Recruiting

27

Novartis Investigative Site

Barcelona, Spain, 08035

Actively Recruiting

28

Novartis Investigative Site

Madrid, Spain, 28046

Actively Recruiting

29

Novartis Investigative Site

Lausanne, Switzerland, 1011

Actively Recruiting

30

Novartis Investigative Site

Liverpool, United Kingdom, L12 2AP

Actively Recruiting

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Research Team

N

Novartis Pharmaceuticals

CONTACT

N

Novartis Pharmaceuticals

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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