Actively Recruiting

Age: 18Years +
All Genders
NCT05319132

Evaluate DF-003 in ex Vivo Assays Using Peripheral Blood Mononuclear Cell From Subjects With ROSAH Syndrome

Led by Hospices Civils de Lyon · Updated on 2025-08-08

4

Participants Needed

5

Research Sites

295 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Alpha-1 kinase (ALPK1) has been reported as a potential causative gene for ROSAH Syndrome. Genetic variants including T237M have been found in ROSAH Syndrome patients. Our in-house study has found that T237M mutation leads to hyperactivity of ALPK1, which may be the cause of the inflammatory syndromes found in ROSAH Syndrome patients. We hypothesize that T237M mutation ALPK1 cause ROSAH Syndrome and an ALPK1 inhibitor can be a potential therapy for treating this disease. To test our hypothesis, we designed an experiment in which ex vivo peripheral blood mononuclear cells (PBMCs) from ROSAH Syndrome patients will be exposed to a potent ALPK1 inhibitor (DF-003) or placebo. We expect to see downregulation of activated inflammatory genes, chemokine/cytokines and acute phase proteins in the ROSAH Syndrome patient samples that are exposed DF-003.

CONDITIONS

Official Title

Evaluate DF-003 in ex Vivo Assays Using Peripheral Blood Mononuclear Cell From Subjects With ROSAH Syndrome

Who Can Participate

Age: 18Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male or female aged over 18
  • Patient with ROSAH syndrome with the confirm T237M mutation
Not Eligible

You will not qualify if you...

  • Person under legal protection or protective measures
  • Person unable to express consent
  • Person in emergency situation (vital or not)
  • Person infected by Human Immunodeficiency Virus and/or Hepatitis B Virus and/or Hepatitis C Virus

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 5 locations

1

Hôpital Nord Croix Rousse

Lyon, Auvergne-Rhône-Alpes, France, 69004

Actively Recruiting

2

service de Genetique - Institut de Biologie Santé PBH-IBS

Angers, France, 49000

Not Yet Recruiting

3

Hôpital de la Pitié Salpétrière

Paris, France, 75013

Actively Recruiting

4

Service D'ophtalmologie

Reims, France, 51000

Not Yet Recruiting

5

Service de médecine interne et immunologie clinique

Rennes, France, 35000

Not Yet Recruiting

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Research Team

Y

YVAN JAMILLOUX, MD

CONTACT

N

Nora MARTEL

CONTACT

How is the study designed?

Study Type

OBSERVATIONAL

Masking

N/A

Allocation

N/A

Model

N/A

Primary Purpose

N/A

Number of Arms

0

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Evaluate DF-003 in ex Vivo Assays Using Peripheral Blood Mononuclear Cell From Subjects With ROSAH Syndrome | DecenTrialz