Actively Recruiting

Phase 2
Age: 1Year - 18Years
All Genders
NCT06017869

Evaluate the Safety and Therapeutic Effects of a Single Intravenous Infusion (IV) of Autologous CD34+ Cells Enriched With Allogenic Placenta-derived Mitochondria in Patients With a Diagnosis of Pearson Syndrome (PS)

Led by Minovia Therapeutics Ltd. · Updated on 2025-06-22

6

Participants Needed

1

Research Sites

226 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Primary Mitochondrial diseases are a clinically and genetically heterogeneous group of disorders caused by mutations in genes encoded by nuclear Deoxyribonucleic Acid (DNA) or by mutations and/or deletions in the mitochondrial DNA (mtDNA). While some mitochondrial disorders only affect a single organ (e.g., the eye in Leber hereditary optic neuropathy \[LHON\]), many involve multiple organs. Mitochondrial disorders may present at any age and a frequent feature is the increasing number of organs involved in the course of the disease. Minovia Therapeutics Ltd. ("Minovia") is a biotech company developing novel therapeutics based on its mitochondrial augmentation technology (MAT). MNV-201 is a cell therapy produced by MAT that consists of the participant's autologous CD34+ hematopoietic stem and progenitor cells (HSPCs) enriched with allogeneic placental-derived mitochondria, manufactured in Minovia's GMP facility.

CONDITIONS

Official Title

Evaluate the Safety and Therapeutic Effects of a Single Intravenous Infusion (IV) of Autologous CD34+ Cells Enriched With Allogenic Placenta-derived Mitochondria in Patients With a Diagnosis of Pearson Syndrome (PS)

Who Can Participate

Age: 1Year - 18Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male or female participants aged from 1 to 18 years old
  • Diagnosis of Pearson Syndrome (current or history) confirmed by molecular identification of mtDNA deletion
  • Failure to thrive with height SDS smaller than -1
  • At least 12 months history of body weight, height, and calculated GFR before treatment
  • Body weight at least 10 kg
  • Living parent(s) or legal guardian(s) able to understand and provide voluntary written informed consent
  • Parent(s) or guardian(s) able to comply with study visits and caregiver assessments
  • Written informed consent provided prior to participation
  • Medically able to undergo study interventions as determined by Investigator
Not Eligible

You will not qualify if you...

  • History of infection with HIV-1, HIV-2, or HTLV I/II
  • Any active infection
  • Diagnosis of Myelodysplastic Syndrome confirmed by FISH and/or karyotype
  • Unable to undergo apheresis
  • Known hypersensitivity to murine proteins or iron-dextran
  • Severe chronic infection
  • Diseases or conditions risking participant safety or interfering with study results
  • History of malignancy
  • Prior treatment with gene therapy, allogeneic bone marrow or cord blood transplantation
  • Change in growth hormone regimen less than 2 years prior to treatment
  • Participation in another clinical trial or receipt of experimental medications within 1 month before study start
  • Pregnant or intending pregnancy within 12 months
  • Investigator's judgment of unsuitability for study participation

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 1 location

1

Sheba Medical Center

Ramat Gan, Israel, Israel, 5266202

Actively Recruiting

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Research Team

L

Lea Bensoussan, Msc

CONTACT

N

Natalie Yivgi Ohana, PhD

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

SINGLE_GROUP

Primary Purpose

TREATMENT

Number of Arms

1

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