Actively Recruiting

Phase 1
Phase 2
Age: 18Years +
All Genders
ID07187401

A Randomized, Double-Blind, Placebo-Controlled, First-In-Human Study of ALN-CFB, an Investigational siRNA Drug Targeting Complement Factor B, in Adults With Paroxysmal Nocturnal Hemoglobinuria and Persistent Anemia on C5 Inhibitor Therapy

Led by Regeneron Pharmaceuticals · Updated on 2026-03-17

24

Participants Needed

7

Research Sites

84 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Researchers are evaluating an experimental drug called ALN-CFB in adults with Paroxysmal Nocturnal Hemoglobinuria (PNH) who continue to have anemia despite treatment with a complement component C5 inhibitor. This Phase 1 and 2 study aims to assess the safety and tolerability of ALN-CFB compared to a placebo, while also examining how the drug affects levels of Complement Factor B (CFB) protein in the blood and its concentration over time. Participants will be randomly assigned to receive either ALN-CFB or a placebo following a single-ascending dose escalation design. The study includes a double-blind period where neither participants nor researchers know who receives the drug or placebo. The protocol will be updated to describe Part B after analysis of Part A data. During the study, participants will be monitored for treatment-emergent adverse events and their severity over one year. Researchers will measure ALN-CFB and its metabolites in plasma and urine, along with changes in CFB concentration from baseline. The study involves regular visits for assessments and safety monitoring, lasting up to 365 days.

CONDITIONS

Brief Title

A First-in-Human Safety and Efficacy Study of ALN-CFB, a Small Interfering RNA (siRNA) Targeting Complement Factor B, in Adult Participants With Paroxysmal Nocturnal Hemoglobinuria With Persistent Anemia on a C5 Inhibitor

Who Can Participate

Age: 18Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Diagnosed with Paroxysmal Nocturnal Hemoglobinuria confirmed by a history of high flow cytometry
  • Treated with a stable dose of C5 inhibitor (eculizumab, approved biosimilar, ravulizumab, or crovalimab) for at least 24 weeks before screening
  • Hemoglobin level of 10.5 g/dL or lower at screening visit 1 with evidence of anemia prior to this visit
  • Peripheral blood reticulocyte count of at least 100 x 10^9/L at screening visit 1
Not Eligible

You will not qualify if you...

  • History of bone marrow transplantation or organ transplant
  • History of meningococcal infection or recurrent infections by other encapsulated bacteria
  • Any active infection or recent infection requiring systemic antibiotics, antivirals, or antifungals within 2 weeks of screening or during screening
  • Laboratory evidence of bone marrow failure
  • Recent unstable medical conditions not related to PNH or its complications

AI-Screening

AI-Powered Screening

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Your Study Journey

Screening

Duration - 2 to 4 weeks

Participants are screened for eligibility to participate in the trial.

1 visit (in-person)

Run-in Period

Duration - At least 24 weeks prior to screening

Participants continue stable C5 inhibitor treatment to establish baseline before receiving the investigational drug or placebo.

Visit schedule as per routine care; not part of trial visits

Treatment

Duration - Up to 365 days

Participants receive either the investigational siRNA drug ALN-CFB or placebo as defined in the protocol to evaluate safety and efficacy.

Multiple visits during treatment as scheduled by the trial protocol

Follow-up

Duration - Up to 365 days post-treatment

Participants are monitored for treatment-emergent adverse events and changes in blood and urine concentrations of the drug and metabolites after dosing.

Visits for safety and laboratory assessments as scheduled

Trial Site Locations

Total: 7 locations

1

Toronto General Hospital

Toronto, Ontario, Canada, M5G 2C4

Actively Recruiting

2

St. Vincent Hospital - The Catholic University of Korea

Suwon, Gyeonggi-do, South Korea, 16247

Actively Recruiting

3

Seoul National University Hospital

Seoul, South Korea, 03080

Actively Recruiting

4

The Catholic University of Korea, Seoul St. Mary's Hospital

Seoul, South Korea, 06591

Actively Recruiting

5

Severance Hospital

Seoul, South Korea, 3722

Actively Recruiting

6

Samsung Medical Center

Seoul, South Korea, 6351

Actively Recruiting

7

St. James's University Hospital

Leeds, West Yorkshire, United Kingdom, LS97TF

Actively Recruiting

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Research Team

C

Clinical Trials Administrator

How is the study designed?

Study Type

INTERVENTIONAL

Masking

QUADRUPLE

Allocation

RANDOMIZED

Model

SEQUENTIAL

Primary Purpose

TREATMENT

Number of Arms

2

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