Actively Recruiting

Phase 2
Age: 8Years +
MALE
NCT06092034

A Gene Therapy Study of RP-A501 in Male Patients With Danon Disease

Led by Rocket Pharmaceuticals Inc. · Updated on 2026-05-04

14

Participants Needed

6

Research Sites

447 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

This is a single arm Phase 2 trial to evaluate the efficacy and safety of RP-A501, a recombinant adeno-associated virus serotype 9 (AAV9) containing the human lysosome-associated membrane protein 2 isoform B (LAMP2B) transgene, in male patients with Danon Disease.

CONDITIONS

Official Title

A Gene Therapy Study of RP-A501 in Male Patients With Danon Disease

Who Can Participate

Age: 8Years +
MALE

Eligibility Criteria

Eligible

You may qualify if you...

  • Male patients
  • Age 8 years or older
  • Documented pathogenic or likely pathogenic variant of the LAMP2 gene
  • Evidence of left ventricular hypertrophy with abnormal thickening of the left ventricular wall
  • Left ventricular ejection fraction (LVEF) of 50% or higher
  • New York Heart Association (NYHA) Class II to III
  • High sensitivity Troponin I (hsTnI) level at least 20% above the upper limit of normal
  • Ability to comply with study procedures including investigational therapy and follow-up evaluations
Not Eligible

You will not qualify if you...

  • Anti-AAV9 neutralizing antibody titer greater than 1:40
  • Severe heart failure or need for advanced therapies
  • History of intracardiac thrombosis or arterial thromboembolic events including stroke, transient ischemic attack (TIA), acute coronary syndrome, myocardial infarction, or unstable angina
  • Prior cardiac or other organ transplantation such as lung or liver

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 6 locations

1

University of California, San Diego

La Jolla, California, United States, 92037

Actively Recruiting

2

Boston Children's Hospital

Boston, Massachusetts, United States, 02115

Actively Recruiting

3

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

4

German Heart Center Munich

Munich, Germany

Actively Recruiting

5

Meyer Childrens Hospital

Florence, Italy

Actively Recruiting

6

Great Ormund Street Hospital & UCL Institute of Cardiovascular Science

London, United Kingdom

Actively Recruiting

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Research Team

C

Clinical Information

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

SINGLE_GROUP

Primary Purpose

TREATMENT

Number of Arms

1

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A Gene Therapy Study of RP-A501 in Male Patients With Danon Disease | DecenTrialz