Actively Recruiting

Age: 18Years +
All Genders
NCT03716908

Genotype-phenotype Correlation Study of Presymptomatic and Symptomatic DFNA9 Patients

Led by Jessa Hospital · Updated on 2021-10-28

70

Participants Needed

1

Research Sites

443 weeks

Total Duration

On this page

Sponsors

J

Jessa Hospital

Lead Sponsor

U

University Hospital, Antwerp

Collaborating Sponsor

AI-Summary

What this Trial Is About

DFNA9 (Deafness Autosomal Dominant 9) is an autosomal dominant hereditary hearing loss which is associated with vestibular deterioration. The most recent genotype-phenotype correlation studies have been conducted more than 15 years ago. Meanwhile, emerging and valuable vestibular tests have been added to the vestibular test battery. These tests were not available at the time of the correlation studies. The aim of this study is to carry out a prospective cross-sectional study on symptomatic and presymptomatic affected carriers of the Pro51Ser (P51S) Coagulation Factor C Homology (COCH) mutation in order to correlate vestibular data using the complete vestibular test battery with the known data on hearing and vestibular function in relation to age.

CONDITIONS

Official Title

Genotype-phenotype Correlation Study of Presymptomatic and Symptomatic DFNA9 Patients

Who Can Participate

Age: 18Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • 18 years of age or older
  • Must be a family member of the family pedigree's proband(s) carrying a Pro51Ser (P51S) COCH mutation
Not Eligible

You will not qualify if you...

  • Younger than 18 years
  • Not a family member of the pedigree's proband(s) carrying a P51S mutation
  • Unable to undergo medical or mental investigations
  • Not willing to participate in the study
  • Have other middle or inner ear diseases
  • Have had middle ear or inner ear surgery
  • Have other vestibular diseases besides DFNA9
  • Have had vestibular surgery or non-invasive vestibular treatments such as gentamicin intratympanal injections

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 1 location

1

University of Antwerp

Antwerp, Belgium, 2650

Actively Recruiting

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Research Team

S

sebastien PF JanssensdeVarebeke, MD

CONTACT

V

Vincent Van Rompaey, PhD, MD

CONTACT

How is the study designed?

Study Type

OBSERVATIONAL

Masking

N/A

Allocation

N/A

Model

N/A

Primary Purpose

N/A

Number of Arms

2

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Genotype-phenotype Correlation Study of Presymptomatic and Symptomatic DFNA9 Patients | DecenTrialz