Actively Recruiting

All Genders
Healthy Volunteers
NCT01193075

Natural History Evaluation of Charcot Marie Tooth Disease (CMT) Types CMT1B, CMT2A, CMT4A, CMT4C, and Others

Led by Michael Shy · Updated on 2025-10-07

5000

Participants Needed

22

Research Sites

869 weeks

Total Duration

On this page

Sponsors

M

Michael Shy

Lead Sponsor

F

Fondazione I.R.C.C.S. Istituto Neurologico Carlo Besta

Collaborating Sponsor

AI-Summary

What this Trial Is About

This is an observational longitudinal study to determine the natural history and genotype-phenotype correlations of disease causing mutations in Charcot Marie Tooth disease (CMT) type 1B (CMT1B), 2A (CMT2A), 4A (CMT4A), and 4C (CMT4C). The investigators will also be determine the capability of the newly developed CMT Pediatric Scale (CMT Peds scale) and the Minimal Dataset to measure impairment and perform longitudinal measurements in patients with multiple forms of CMT over a five year window

CONDITIONS

Official Title

Natural History Evaluation of Charcot Marie Tooth Disease (CMT) Types CMT1B, CMT2A, CMT4A, CMT4C, and Others

Who Can Participate

All Genders
Healthy Volunteers

Eligibility Criteria

Eligible

You may qualify if you...

  • Patients must attend an in-person visit at a participating center for the initial evaluation.
  • Patient has a documented pathogenic or likely pathogenic CMT-causing genetic variant.
  • Alternatively, patient has a first- or second-degree family member with a documented pathogenic or likely pathogenic CMT variant and a clear link plus a matching clinical picture.
  • Patients with variants of uncertain significance may be included if classified as pathogenic per guidelines, found in affected family members but not in unaffected ones, or agreed upon by investigators as likely pathogenic.
  • Patients with clinical signs suggestive of CMT but unknown type or variant will be categorized by nerve conduction and inheritance patterns.
  • Patients or their legal representatives must understand and sign an IRB-approved consent form; teens 13-17 and cognitively able adults must sign an assent form as required.
  • Control participants must not have peripheral neuropathy and must sign consent; teens 13-17 must sign assent as required.
Not Eligible

You will not qualify if you...

  • Patients with variants of uncertain significance that cannot be classified according to inclusion criteria methods.
  • Patients who do not wish to participate or have not signed informed consent.
  • Patients deemed inappropriate for the study by the site principal investigator.

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

1
2
3
+1

Trial Site Locations

Total: 22 locations

1

Cedars-Sinai Medical Center

Los Angeles, California, United States, 90048

Actively Recruiting

2

Stanford University

Palo Alto, California, United States, 94305

Actively Recruiting

3

University of Colorado Hospital

Aurora, Colorado, United States, 80045

Actively Recruiting

4

University of Connecticut/Connecticut Children's Medical Center

Hartford, Connecticut, United States, 06106

Actively Recruiting

5

Children's National Hospital

Washington D.C., District of Columbia, United States, 20010

Actively Recruiting

6

University of Miami

Miami, Florida, United States, 33136

Actively Recruiting

7

Nemours Children's Health

Orlando, Florida, United States, 32827

Actively Recruiting

8

Nemours Children's Hospital

Orlando, Florida, United States, 32827

Actively Recruiting

9

University of Iowa

Iowa City, Iowa, United States, 52242

Actively Recruiting

10

Johns Hopkins University

Baltimore, Maryland, United States, 21205

Actively Recruiting

11

Harvard/Massachusetts General Hospital

Boston, Massachusetts, United States, 02114

Actively Recruiting

12

University of Michigan

Ann Arbor, Michigan, United States, 48109

Not Yet Recruiting

13

University of Minnesota

Minneapolis, Minnesota, United States, 55455

Actively Recruiting

14

University of Rochester

Rochester, New York, United States, 14642

Actively Recruiting

15

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

16

University of Pennsylvania

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

17

St. Jude Children's Research Hospital

Memphis, Tennessee, United States, 38105-3678

Actively Recruiting

18

Seattle Children's Hospital

Seattle, Washington, United States, 98105

Not Yet Recruiting

19

University of Westmead

Sydney, New South Wales, Australia, 2145

Actively Recruiting

20

The Hospital for Sick Children

Toronto, Ontario, Canada, M5G 1E8

Actively Recruiting

21

C. Besta Neurological Institute

Milan, Milan, Italy

Actively Recruiting

22

National Hospital of Neurology and Neurosurgery

London, England, United Kingdom, WC1N 3BG

Actively Recruiting

Loading map...

Research Team

N

Nicole M Kressin, MSN, RN

CONTACT

T

Tiffany Grider, MS, CGC

CONTACT

How is the study designed?

Study Type

OBSERVATIONAL

Masking

N/A

Allocation

N/A

Model

N/A

Primary Purpose

N/A

Number of Arms

5

Not the Right Trial for You?

Explore thousands of other clinical trials that might be a better match.
Sign up to get personalized trial recommendations delivered to your inbox.

Already have an account? Log in here