Actively Recruiting

Age: 2Years - 15Years
All Genders
ID06354790

A Prospective, Longitudinal Natural History Study of Children With LAMA2-related Dystrophies in France

Led by Institut de Myologie, France · Updated on 2024-12-12

40

Participants Needed

4

Research Sites

3 weeks

Total Duration

On this page

Sponsors

I

Institut de Myologie, France

Lead Sponsor

A

Association Française contre les Myopathies (AFM), Paris

Collaborating Sponsor

AI-Summary

What this Trial Is About

Researchers are studying children with LAMA2-related dystrophies (LAMA2-RD), a rare muscular condition, to better understand its natural course and characteristics. This observational study aims to create a well-defined group of patients in France for ongoing follow-up and to prepare for future clinical trials. The research focuses on multiple aspects of the disease including muscle function, breathing, cognitive abilities, quality of life, growth, and biomarkers.

CONDITIONS

Brief Title

Natural History Study of Children With LAMA2-related Dystrophies

Who Can Participate

Age: 2Years - 15Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Signed informed consent by a legal guardian and assent from the child if 6 years or older
  • Confirmed diagnosis of LAMA2-RD by genetic testing or muscle biopsy
  • No other confirmed neurological genetic diseases
  • Willingness to maintain current exercise and physical therapy during the study
  • Willingness to comply with study procedures and visits
  • Affiliation with or beneficiary of a French social security scheme
Not Eligible

You will not qualify if you...

  • Developmental quotient below 70 or behavioral disorder requiring anesthesia for MRI
  • Acute illness or hospitalization within 30 days before consent
  • Participation in other investigational drug trials for LAMA2-RD within 30 days prior to consent
  • Other significant medical conditions or frailty that may affect study results
  • Pregnant or breastfeeding females

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Your Study Journey

Screening

Duration - 2 to 4 weeks

Participants are screened for eligibility to participate in the trial.

1 visit (in-person)

Diagnostic Evaluation

Duration - Initial assessment at enrollment

Participants undergo evaluations including motor function tests, cognitive assessments, pulmonary and cardiac function tests, spinal X-rays, muscular MRI, and biomarker sample collections to assess the clinical characteristics of LAMA2-related dystrophies.

1 baseline visit (in-person)

Long-term Monitoring

Duration - Approximately 2 years

Participants are followed prospectively to monitor disease progression and changes in motor, cognitive, pulmonary, cardiac, and quality of life measures over time.

Regular visits during the study period (visit frequency determined by study protocol)

Trial Site Locations

Total: 4 locations

1

Centre de Référence GNMH, Pédiatrie Hôpital Raymond-Poincaré

Garches, France

Not Yet Recruiting

2

Service de MPR pédiatrique L'Escale - HCL

Lyon, France

Not Yet Recruiting

3

Département de neuropédiatrie Pôle Femme Mère Enfant CHU de Montpellier - Hôpital Gui de Chauliac

Montpellier, France

Not Yet Recruiting

4

Plateforme d'essais cliniques pédiatriques iMotion

Paris, France

Actively Recruiting

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Research Team

A

Andreea SEFERIAN, Dr

E

Erwan GASNIER, PhD

How is the study designed?

Study Type

OBSERVATIONAL

Masking

N/A

Allocation

N/A

Model

N/A

Primary Purpose

N/A

Number of Arms

1

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