Actively Recruiting

Phase 1
Phase 2
Age: 6Months +
All Genders
ID05757141

A Phase 1b/2 Open-label Study to Evaluate Safety, Tolerability, Pharmacokinetics, and Exploratory Efficacy of Fosigotifator in Adults and Children With Vanishing White Matter Disease

Led by Calico Life Sciences LLC · Updated on 2026-06-02

50

Participants Needed

5

Research Sites

104 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Researchers are evaluating Fosigotifator, an investigational oral drug, for treating Vanishing White Matter disease in adults, children, and infants. This is an open-label study lasting 201 weeks, including multiple groups based on age. The study aims to assess safety, tolerability, pharmacokinetics, and exploratory efficacy for participants with this disease. Participants are divided into cohorts by age: adults 18 years and older, children aged 12 to less than 18 years, children 6 to less than 12 years, and children 6 months to less than 6 years. All participants receive Fosigotifator orally. The study includes regular visits and ongoing assessments over nearly four years. During the study, participants will have medical exams, blood tests, questionnaires, and evaluations for side effects. Researchers will monitor vital signs, ECGs, lab tests, and brain MRI changes. Drug levels in the blood and cognitive safety measures are also tracked. The study involves close monitoring from baseline to about week 197 to understand the drug's effects and participant safety.

CONDITIONS

Brief Title

An Open-Label Exploratory Study of Fosigotifator in Participants With Vanishing White Matter Disease

Who Can Participate

Age: 6Months +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Males and females aged 6 months or older at screening
  • Diagnosed with Vanishing White Matter disease by a physician experienced with this condition
  • Molecular diagnosis and MRI findings consistent with Vanishing White Matter disease
  • Have a caregiver able to complete caregiver assessments
  • Signed informed consent by participant or legally authorized representative
  • Meet one of the following: history of at least one neurological symptom related to the disease, inability to walk 10 or more steps with or without light support, or cognitive score below 50 on specific tests
  • Pediatric participants in youngest cohort must meet additional specific motor or genetic risk criteria
  • Sexually active males and females must agree to use contraceptive methods and avoid sperm or egg donation during and for 30 days after the study
Not Eligible

You will not qualify if you...

  • Pediatric participants aged 6 months to less than 6 years who use any form of respiratory support at screening
  • Changes in medication for Vanishing White Matter disease symptoms within 4 weeks before screening
  • Seizure disorder not well controlled within 6 months prior to screening
  • Inability to complete study visits and procedures as judged by investigator
  • Adult females who are pregnant, breastfeeding, or providing breast milk
  • Treatment with other investigational therapies within 30 days or 5 half-lives before baseline
  • Clinically significant laboratory or imaging abnormalities at screening

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Your Study Journey

Screening

Duration - 2 to 4 weeks

Participants are screened for eligibility to participate in the trial.

1 visit (in-person)

Treatment

Duration - Up to approximately 96 weeks

Participants receive Fosigotifator orally as the study treatment.

Visits scheduled regularly during treatment up to Week 96

Follow-up

Duration - Up to approximately Week 197 from baseline

Participants continue to be monitored for safety and efficacy after treatment ends.

Visits scheduled periodically up to Week 197

Trial Site Locations

Total: 5 locations

1

Massachusetts General Hospital /ID# 270960

Boston, Massachusetts, United States, 02114

Actively Recruiting

2

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

3

University of Utah /ID# 255624

Salt Lake City, Utah, United States, 84112-5339

Actively Recruiting

4

McGill University Health Centre - Glen Site

Montreal, Quebec, Canada, H3H2L9

Actively Recruiting

5

Amsterdam UMC, locatie VUmc /ID# 270955

Amsterdam, North Holland, Netherlands, 1081 HV

Actively Recruiting

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Research Team

C

Call Center - English

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NON_RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

5

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