Actively Recruiting

Phase 1
Age: 18Years - 50Years
FEMALE
NCT04532047

PEARL (PrEnAtal Enzyme Replacement Therapy for Lysosomal Storage Disorders)

Led by University of California, San Francisco · Updated on 2026-03-17

10

Participants Needed

1

Research Sites

578 weeks

Total Duration

On this page

Sponsors

U

University of California, San Francisco

Lead Sponsor

D

Duke University

Collaborating Sponsor

AI-Summary

What this Trial Is About

For detailed information, please view our study website: https://pearltrial.ucsf.edu/ The investigators aims to determine the the maternal and fetal safety and feasibility of in utero fetal enzyme replacement therapy in fetuses with Lysosomal Storage Diseases.

CONDITIONS

Official Title

PEARL (PrEnAtal Enzyme Replacement Therapy for Lysosomal Storage Disorders)

Who Can Participate

Age: 18Years - 50Years
FEMALE

Eligibility Criteria

Eligible

You may qualify if you...

  • Pregnant women aged 18 to 50 years carrying a live fetus between 18 0/7 and 34 6/7 weeks gestation
  • Fetus diagnosed prenatally with one of eight specified Lysosomal Storage Diseases by genetic or enzymatic testing
  • Ability to provide written informed consent and comply with study requirements
Not Eligible

You will not qualify if you...

  • Fetuses with severe structural anomalies unrelated to the Lysosomal Storage Disease
  • Fetuses with additional significant pathogenic genetic variants increasing morbidity or mortality risk
  • Pregnant women with significant comorbidities preventing fetal intervention, including: inability to complete procedure due to body habitus or placental location, significant cardiopulmonary disease, mirror syndrome, end organ failure, altered mental status, placental abruption, active preterm labor, or preterm premature rupture of membranes
  • Use of therapeutic anticoagulation within 24 hours before or after the intervention

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 1 location

1

University of California

San Francisco, California, United States, 94158

Actively Recruiting

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Research Team

T

Tippi MacKenzie, MD

CONTACT

E

Emma Canepa, MS, CCRP

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

SINGLE_GROUP

Primary Purpose

TREATMENT

Number of Arms

1

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PEARL (PrEnAtal Enzyme Replacement Therapy for Lysosomal Storage Disorders) | DecenTrialz