Actively Recruiting

Phase 2
Age: 12Years - 16Years
All Genders
NCT05953584

A Phase 2 Open-label Study to Evaluate the Activity of Etavopivat on Transcranial Doppler Velocities in Pediatric Patients With Sickle Cell Disease Who Are at Increased Risk for Primary Stroke

Led by Forma Therapeutics, Inc. · Updated on 2025-09-18

27

Participants Needed

9

Research Sites

221 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

The study will test a new medicine, etavopivat, for sickle cell disease and see if it is safe and help-ful for participants with sickle cell disease who are at an increased risk of stroke. Participants will be divided into two cohorts depending on their transcranial doppler (TCD) ultrasound results and whether or not they receive hydroxyurea (medication that they may already be taking). In one cohort, participants with conditional transcranial doppler (TCD) or participants with abnormal TCD who are not able to receive hydroxyurea will be included. The study doctor will determine if the TCD result is conditional or abnormal. In another cohort, participants with conditional TCD or participants with abnormal TCD who are receiving a stable dose of hydroxyurea will be included. The study doctor will determine if the TCD result is conditional or abnormal. The participant will start a 52-week (1 year) treatment period. The participant will take 400 milligrams (mg) of etavopivat once a day for the 52 weeks. The dose of 400 mg will be taken as 2 tablets by mouth, each containing 200 mg of etavopivat. Etavopivat may be taken with or without food. Each dose should be taken with a glass of water. As part of the study, the participants will be asked to visit the clinic frequently. The participant will have the opportunity to participate in a 48-week optional extension treatment period. The optional extension treatment period will allow continued as-sessment of safety of etavopivat in paediatric patients. At the end of the study, if deemed appro-priate the participant, the caregiver, and the study doctor, the participant may be offered the op-portunity to participate in a separate study to continue receiving etavopivat. If/when this separate study becomes available, the participant may only transfer to the new study after completion of the 52-week primary treatment period and at any time during the 48-week optional extension treatment period.

CONDITIONS

Official Title

A Phase 2 Open-label Study to Evaluate the Activity of Etavopivat on Transcranial Doppler Velocities in Pediatric Patients With Sickle Cell Disease Who Are at Increased Risk for Primary Stroke

Who Can Participate

Age: 12Years - 16Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Patient's parent, legal guardian, or legal representative has given informed consent, and patient has provided age-appropriate assent
  • Age between 12 and 16 years at screening
  • Confirmed diagnosis of sickle cell disease of any genotype
  • Blood flow velocity (TAMMV) of 170 cm/s or higher in internal carotid or middle cerebral artery confirmed twice, with no history of stroke, transient ischemic attack, or severe CNS vasculopathy
  • Hemoglobin level between 6 and 9 grams per deciliter at screening
  • If taking hydroxyurea, dose must be stable (no more than 20% change) for at least 90 days before study start with no expected dose changes except weight-based adjustments
  • Female patients of childbearing potential must use acceptable contraception and agree not to donate ova during the study and for 90 days after last dose; males must agree to use contraception and not donate sperm during the same period
Not Eligible

You will not qualify if you...

  • Female who is pregnant or breastfeeding
  • History of seizure disorder
  • Prior overt stroke or significant neurological deficits suggesting stroke
  • Severe CNS vasculopathy (Grade 4 or higher) based on local MRA read
  • Significant low blood counts: neutrophils less than 1.5 x 10^3/µL, platelets less than 150,000/µL, or reticulocytes less than 80,000/µL
  • Severe kidney dysfunction or on chronic dialysis
  • Liver dysfunction with ALT more than 4 times upper limit of normal or direct bilirubin more than 3 times upper limit
  • Active significant infections requiring systemic treatment or history of infections causing neurological impairment
  • Known HIV infection
  • Known hepatitis B infection (positive surface antigen and core antibody)

AI-Screening

AI-Powered Screening

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Trial Site Locations

Total: 9 locations

1

All India Institute of Medical Sciences (AIIMS), Raipur

Raipur, Chhattisgarh, India, 492099

Actively Recruiting

2

All India Institute of Medical Sciences-Delhi

Delhi, India, 110029

Actively Recruiting

3

Nirmal Hospital Pvt. Ltd.

Gujarat, India, 395002

Actively Recruiting

4

Suretech Hospital and Research Centre Ltd.

Maharashtra, India, 440012

Actively Recruiting

5

Indira Gandhi Government Medical College & Hospital

Nagpur, India, 440018

Not Yet Recruiting

6

University of Ibadan, University College Hospital

Ibadan, Nigeria, 200285

Actively Recruiting

7

Lagos University Teaching Hospital, Lagos

Lagos, Nigeria, 102215

Actively Recruiting

8

Aminu Kano Teaching Hospital (AKTH)

Tarauni, Nigeria, 700101

Actively Recruiting

9

Sultan Qaboos University Hospital

Muscat, Sultanet of Oman/Muscat/Al Khoud, Oman, 123

Actively Recruiting

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Research Team

N

Novo Nordisk

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NON_RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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