Actively Recruiting

Phase 1
Phase 2
Age: 2Years - 24Years
All Genders
NCT04923126

SJ901: Evaluation of Mirdametinib in Children, Adolescents, and Young Adults With Low-Grade Glioma

Led by St. Jude Children's Research Hospital · Updated on 2026-02-04

132

Participants Needed

1

Research Sites

518 weeks

Total Duration

On this page

Sponsors

S

St. Jude Children's Research Hospital

Lead Sponsor

S

SpringWorks Therapeutics, Inc.

Collaborating Sponsor

AI-Summary

What this Trial Is About

This is an open-label, multi-center, Phase 1/2 study of the brain-penetrant MEK inhibitor, mirdametinib (PD-0325901), in patients with pediatric low-grade glioma (pLGG).

CONDITIONS

Official Title

SJ901: Evaluation of Mirdametinib in Children, Adolescents, and Young Adults With Low-Grade Glioma

Who Can Participate

Age: 2Years - 24Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Participant must have histologically confirmed or suspected low-grade glioma including neuronal and mixed neuronal-glial tumors
  • Participant must have adequate tumor tissue for central pathology review
  • Age must be 2 years or older and less than 25 years at enrollment
  • Participant's body surface area (BSA) must meet protocol requirements for dose level in Phase 1; no upper BSA limits in Phase 2
  • Participant and/or guardian must understand and be willing to sign informed consent
  • Participant must have measurable or evaluable disease
  • Participants receiving corticosteroids must be on stable or decreasing dose for at least 1 week prior to enrollment
  • Performance score (Lansky <16 years or Karnofsky ≥16 years) must be 50 or higher with minimum life expectancy of 6 weeks
  • Adequate bone marrow, organ, renal, and cardiac function as defined in the protocol
  • Blood pressure must be controlled within specified limits for age and gender
  • Participants of childbearing potential must agree to use contraception
  • Participants must have confirmation of eligible tumor types per central pathology review
  • Tumor must show evidence of MAPK pathway activation or participant must have known relevant germline mutation
  • For Phase 1: tumor must be progressive or recurrent without prior MEK inhibitor exposure
  • Prior chemotherapy and radiation must meet protocol timelines for last treatment
  • No prior MEK inhibitor exposure for Phase 1 and Phase 2 Cohorts 1 and 2
  • Cohort 1: Newly diagnosed or previously untreated except surgery; tumor must warrant treatment
  • Cohort 2: Progressive or recurrent tumor without prior MEK inhibitor exposure
  • Cohort 3A: Prior MEK inhibitor treatment ≥6 cycles without progression on therapy, progression off therapy
  • Cohort 3B: Prior non-mirdametinib MEK inhibitor treatment with progression on therapy
  • Participants must recover from prior treatment toxicities according to protocol timelines
Not Eligible

You will not qualify if you...

  • Tumor classified as high-grade (WHO III or IV), subependymal giant cell astrocytoma, ependymoma, histone H3 or BRAF V600 mutant, NTRK1/2/3, ALK, ROS1 fusion-positive, or IDH 1/2 mutant
  • Currently receiving other anticancer or investigational agents (except ^11C-methionine) or recovering from related toxicity
  • Known retinal diseases including central serous retinopathy, retinal vein occlusion, retinal detachment, or uncontrolled glaucoma
  • Clinically significant medical disorders that could affect treatment tolerance or study participation
  • Sexually active patients of reproductive potential not agreeing to effective contraception
  • Unable to comply with protocol guidelines

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 1 location

1

St. Jude Children's Research Hospital

Memphis, Tennessee, United States, 38105

Actively Recruiting

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Research Team

T

Tabatha E. Doyle, RN

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NON_RANDOMIZED

Model

SEQUENTIAL

Primary Purpose

TREATMENT

Number of Arms

5

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