Actively Recruiting

Phase 1
Phase 2
Age: 16Years - 70Years
All Genders
NCT06131983

Study of ARO-DUX4 in Adult and Adolescent Patients With Facioscapulohumeral Muscular Dystrophy Type 1

Led by Arrowhead Pharmaceuticals · Updated on 2026-02-06

60

Participants Needed

17

Research Sites

144 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

The purpose of this study is to evaluate the safety, tolerability, pharmacokinetics (PK) and pharmacodynamics (PD) of ARO-DUX4 in participants with facioscapulohumeral muscular dystrophy Type 1 (FSHD1). In Part 1 of the study, participants will receive one dose of ARO-DUX4 or placebo. In Part 2 of the study, participants will receive 4 doses of ARO-DUX4 or placebo. Participants who complete Part 1 will have the option to re-screen and re-randomize into Part 2. All participants will undergo pre- and post-dose MRI-guided muscle biopsies (a total of 2 biopsies). Participants who complete Part 1 and enroll in Part 2 will be required to undergo an additional screening biopsy. Participants completing Part 1 or Part 2 may have the option to continue to receive drug in an open-label extension study or may be eligible to participate in later-stage clinical studies.

CONDITIONS

Official Title

Study of ARO-DUX4 in Adult and Adolescent Patients With Facioscapulohumeral Muscular Dystrophy Type 1

Who Can Participate

Age: 16Years - 70Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Genetically confirmed facioscapulohumeral muscular dystrophy Type 1 (FSHD1)
  • Clinical severity score between 3 and 8 on a scale of 0 to 10
  • Eligible lower extremity muscle for biopsy confirmed by MRI
  • Normal 12-lead electrocardiogram (ECG) at screening
  • Use of highly effective contraception during the study and for at least 12 weeks after last dose for participants of childbearing potential and their partners
  • Males must not donate sperm during the study and for at least 12 weeks after last dose
Not Eligible

You will not qualify if you...

  • Positive test for HIV infection at screening
  • Positive test for hepatitis B (HBV) or hepatitis C (HCV) at screening
  • Uncontrolled hypertension
  • Severe cardiovascular disease
  • History of thrombotic events
  • Platelet count below normal limits at screening
  • History or presence of hypercoagulable state, nephrotic range proteinuria, antiphospholipid antibody syndrome, myeloproliferative disease
  • Inability to walk
  • Use of hormone-based contraceptives
  • Any contraindication to muscle biopsy or MRI
  • Additional criteria may apply per protocol

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 17 locations

1

Research Site 2

Liverpool, New South Wales, Australia, 2170

Actively Recruiting

2

Research Site 3

Auchenflower, Queensland, Australia, 4066

Actively Recruiting

3

Research Site 1

Birtinya, Queensland, Australia, 4575

Actively Recruiting

4

Research Site 4

Melbourne, Victoria, Australia, 3004

Actively Recruiting

5

Research Site 2

Calgary, Alberta, Canada, T2N4Z6

Not Yet Recruiting

6

Research Site 3

Edmonton, Alberta, Canada, T6G2G4

Actively Recruiting

7

Research Site 1

Montreal, Quebec, Canada, H3A2B4

Actively Recruiting

8

Research Site 2

München, Germany, 80336

Actively Recruiting

9

Research Site 1

Ulm, Germany, 89081

Actively Recruiting

10

Research Site 1

Milan, Italy, 20162

Actively Recruiting

11

Research Site 2

Roma, Italy, 00168

Actively Recruiting

12

Research Site 1

Leiden, Netherlands, 2333

Actively Recruiting

13

Research Site 1

Auckland, New Zealand, 1010

Actively Recruiting

14

Research Site 3

Barcelona, Spain, 08035

Actively Recruiting

15

Research Site 2

Madrid, Spain, 28034

Actively Recruiting

16

Research Site 1

Valencia, Spain, 46026

Actively Recruiting

17

Research Site

Bangkok, Thailand, 10700

Withdrawn

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Research Team

M

Medical Monitor

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

QUADRUPLE

Allocation

RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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