Actively Recruiting

Phase 1
Phase 2
Age: 18Years - 64Years
All Genders
NCT06300307

Study of ATX-01 in Participants With DM1

Led by ARTHEx Biotech S.L. · Updated on 2026-02-10

56

Participants Needed

12

Research Sites

141 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

The goal of this clinical trial is to test ATX-01 in participants with myotonic dystrophy type 1 (DM1). The main question it aims to answer is if ATX-01 is safe and well tolerated. The trial will compare the safety and tolerability of ATX-01 and a matching placebo. There will be a single-ascending dose part of the trial and a multiple-ascending dose part. In the single-ascending dose, participants will receive one dose of ATX-01 or placebo. In the multiple-ascending dose part, participants will receive three doses of ATX-01 or placebo. ATX-01 is a novel anti-miR (synthetic single stranded oligonucleotide) that inhibits a microRNA called miR-23b.

CONDITIONS

Official Title

Study of ATX-01 in Participants With DM1

Who Can Participate

Age: 18Years - 64Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Participants with a documented clinical diagnosis of DM1 (CTG expansion of >150 repeats in DMPK gene measured in peripheral blood mononuclear cells)
  • Able to walk or run 10 meters at screening without assistive devices except ankle-foot orthoses
  • Presence of grip myotonia lasting more than 3 seconds as confirmed by a central reader
Not Eligible

You will not qualify if you...

  • Participants with congenital DM1
  • Medical Research Council Muscle Scale score less than 4 on ankle dorsiflexion or significant tibialis anterior atrophy preventing muscle biopsy
  • Use of mexiletine or other agent for myotonia within 21 days or 5 half-lives, whichever is longer, prior to screening

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 12 locations

1

UCLA

Los Angeles, California, United States, 90095

Actively Recruiting

2

University of Florida

Gainesville, Florida, United States, 32610

Actively Recruiting

3

University of Iowa Health Care - Department of Neurology

Iowa City, Iowa, United States, 52242

Actively Recruiting

4

University of Kansas Medical Center, Department of Neurology

Fairway, Kansas, United States, 66205

Actively Recruiting

5

Virginia Commonwealth University

Richmond, Virginia, United States, 23298

Actively Recruiting

6

Centre Intégré Universitaire de Santé et Services Sociaux du Saguenay-Lac-St-Jean

Chicoutimi, Quebec, Canada, G7H 5H6

Actively Recruiting

7

Institute of Myology

Paris, France, 75651

Actively Recruiting

8

The NeMO Clinical Center in Milan, Neurorehabilitation Unit, University of Milan

Milan, Italy, 20162

Actively Recruiting

9

Fondazione Policlinico A. Gemelli- IRCCS

Rome, Italy, 00168

Actively Recruiting

10

Radboudumc

Nijmegen, Netherlands, 6525

Actively Recruiting

11

Hospital Universitario Donostia

Donostia / San Sebastian, Spain, 20014

Actively Recruiting

12

St. George's University Hospital

London, United Kingdom, SW17 0RE

Actively Recruiting

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Research Team

P

Project Manager

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

TRIPLE

Allocation

RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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