Actively Recruiting

Phase 3
Age: 6Years - 17Years
All Genders
NCT06321601

Study to Evaluate Avacopan in Combination With a Rituximab or Cyclophosphamide-containing Regimen, in Children From 6 Years to < 18 Years of Age With AAV.

Led by Amgen · Updated on 2026-05-14

20

Participants Needed

32

Research Sites

205 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

The main objective of this study is to explore the efficacy of avacopan in participants affected by AAV.

CONDITIONS

Official Title

Study to Evaluate Avacopan in Combination With a Rituximab or Cyclophosphamide-containing Regimen, in Children From 6 Years to < 18 Years of Age With AAV.

Who Can Participate

Age: 6Years - 17Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male and female children and adolescents from 6 to < 18 years of age
  • Clinical diagnosis of granulomatosis with polyangiitis (GPA) or microscopic polyangiitis (MPA) per Chapel-Hill Consensus definitions
  • Newly diagnosed or relapsed AAV with positive anti-PR3 or anti-MPO antibodies
  • At least 1 major item or 3 nonmajor items on the Pediatric Vasculitis Activities Score (PVAS), or the 2 renal items of proteinuria and hematuria
  • Estimated glomerular filtration rate (eGFR) > 15 mL/min/1.73 m2 using modified Schwartz equation
  • Bodyweight of at least 15 kg at day 1
Not Eligible

You will not qualify if you...

  • Any other known multisystem autoimmune disease including eosinophilic granulomatosis with polyangiitis, systemic lupus erythematosus, IgA vasculitis, rheumatoid vasculitis, Sjogren's syndrome, anti-glomerular basement membrane disease, or cryoglobulinemic vasculitis
  • Alveolar hemorrhage requiring invasive pulmonary ventilation support expected beyond screening
  • Medical conditions requiring ongoing immunosuppressive treatments, including corticosteroids, that may interfere with study assessments or conclusions

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 32 locations

1

Emory University

Atlanta, Georgia, United States, 30322

Actively Recruiting

2

Riley Hospital for Children

Indianapolis, Indiana, United States, 46202

Actively Recruiting

3

University of Minnesota Masonic Childrens Hospital Discovery Clinic

Minneapolis, Minnesota, United States, 55454

Actively Recruiting

4

Cohen Children Medical Center

Lake Success, New York, United States, 11042

Actively Recruiting

5

University of North Carolina

Chapel Hill, North Carolina, United States, 27599

Actively Recruiting

6

Wake Forest University Health Sciences

Charlotte, North Carolina, United States, 28203

Actively Recruiting

7

Akron Childrens Hospital

Akron, Ohio, United States, 44308

Actively Recruiting

8

Cleveland Clinic Foundation

Cleveland, Ohio, United States, 44195

Actively Recruiting

9

University of Pittsburgh Medical Center Childrens Hospital of Pittsburgh

Pittsburgh, Pennsylvania, United States, 15224

Actively Recruiting

10

Texas Childrens Hospital

Houston, Texas, United States, 77030

Actively Recruiting

11

Universitair Ziekenhuis Gent

Ghent, Belgium, 9000

Actively Recruiting

12

Universitair Ziekenhuis Leuven - Gasthuisberg

Leuven, Belgium, 3000

Actively Recruiting

13

Alberta Childrens Hospital

Calgary, Alberta, Canada, T3B 6A8

Actively Recruiting

14

Stollery Childrens Hospital

Edmonton, Alberta, Canada, T6G 1C9

Actively Recruiting

15

British Columbia Childrens Hospital

Vancouver, British Columbia, Canada, V6H 3N1

Actively Recruiting

16

CHU Sainte Justine

Montreal, Quebec, Canada, H3T 1C5

Actively Recruiting

17

Vseobecna fakultni nemocnice v Praze

Prague, Czechia, 128 08

Actively Recruiting

18

Fakultni nemocnice v Motole

Prague, Czechia, 150 06

Actively Recruiting

19

Centre Hospitalier Universitaire de Bordeaux - Hopital Pellegrin

Bordeaux, France, 33076

Actively Recruiting

20

Hospices Civils de Lyon Hopital Femme Mere Enfant

Bron, France, 69677

Actively Recruiting

21

Hopital Necker Enfants Malades

Paris, France, 75015

Actively Recruiting

22

Hopital Necker

Paris, France, 75015

Actively Recruiting

23

Semmelweis Egyetem

Budapest, Hungary, 1094

Actively Recruiting

24

Szegedi Tudomanyegyetem Szent-Gyorgyi Albert Klinikai Kozpont Altalanos Orvostudomanyi Kar

Szeged, Hungary, 6720

Terminated

25

Uniwersyteckie Centrum Kliniczne

Gdansk, Poland, 80-952

Actively Recruiting

26

Uniwersytecki Szpital Dzieciecy w Krakowie

Krakow, Poland, 30-663

Actively Recruiting

27

Dzieciecy Szpital Kliniczny im. Jozefa Polikarpa Brudzinskiego w Warszawie

Warsaw, Poland, 02-091

Actively Recruiting

28

Narodny ustav detskych chorob

Bratislava, Slovakia, 833 40

Actively Recruiting

29

Hospital Universitari Vall d Hebron

Barcelona, Catalonia, Spain, 08035

Actively Recruiting

30

Hospital Sant Joan de Deu

Esplugues de Llobregat, Catalonia, Spain, 08950

Actively Recruiting

31

Hospital Universitario 12 de Octubre

Madrid, Spain, 28041

Actively Recruiting

32

Hacettepe Universitesi Tip Fakultesi Hastanesi

Ankara, Turkey (Türkiye), 06100

Actively Recruiting

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Research Team

A

Amgen Call Center

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NON_RANDOMIZED

Model

SINGLE_GROUP

Primary Purpose

TREATMENT

Number of Arms

1

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