Actively Recruiting

Phase 4
Age: 1Year - 5Years
All Genders
NCT07142343

A Study to Test the Safety of Pozelimab in Pediatric Participants 1 to 5 Years of Age With a Rare Disease Called CHAPLE (Complement Hyperactivation, Angiopathic Thrombosis, Protein-losing Enteropathy) Disease

Led by Regeneron Pharmaceuticals · Updated on 2026-04-13

5

Participants Needed

1

Research Sites

203 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

This study is researching a drug called pozelimab (called "study drug"). The main aim of this study is to monitor the safety and tolerability of the study drug. The study is focused on young children 1 to 5 years of age, who have CHAPLE disease. CHAPLE is a very rare hereditary disease that can cause potentially life-threatening symptoms related to the stomach and intestines (gastrointestinal symptoms), and symptoms related to the heart and blood vessels (cardiovascular symptoms). The study is also looking at several other research questions, including: * What side effects may happen from taking the study drug * How much study drug is in the blood at different times * Whether the study drug blocks Complement 5 (C5) in the body * Whether the study drug changes the level of a substance called CH50 measured in the blood * Whether the study drug changes the levels of albumin and other proteins * Whether the body makes antibodies against study drug, which could make the study drug less effective or could lead to side effects

CONDITIONS

Official Title

A Study to Test the Safety of Pozelimab in Pediatric Participants 1 to 5 Years of Age With a Rare Disease Called CHAPLE (Complement Hyperactivation, Angiopathic Thrombosis, Protein-losing Enteropathy) Disease

Who Can Participate

Age: 1Year - 5Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Clinical diagnosis of CD55-deficient CHAPLE disease as described in the protocol
  • Parent(s)/legal guardian(s) willing and able to follow clinic visits and study procedures
  • Parent(s)/legal guardian(s) willing to give written informed consent
  • Participant has active CHAPLE disease as described in the protocol
Not Eligible

You will not qualify if you...

  • History of meningococcal infection
  • No documented meningococcal quadrivalent (serotype ACWY) vaccination before screening and unwillingness to vaccinate during the study
  • No documented vaccination for Haemophilus influenzae and Streptococcus pneumoniae if applicable based on local guidelines
  • Prior treatment with a complement inhibitor as described in the protocol
  • Presence of another disease causing hypoproteinemia or secondary intestinal lymphangiectasia as described in the protocol
  • Other protocol-defined exclusion criteria apply

AI-Screening

AI-Powered Screening

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Trial Site Locations

Total: 1 location

1

Marmara University Hospital

Istanbul, Turkey (Türkiye), 10 34899

Actively Recruiting

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Research Team

C

Clinical Trials Administrator

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

NA

Model

SINGLE_GROUP

Primary Purpose

TREATMENT

Number of Arms

1

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A Study to Test the Safety of Pozelimab in Pediatric Participants 1 to 5 Years of Age With a Rare Disease Called CHAPLE (Complement Hyperactivation, Angiopathic Thrombosis, Protein-losing Enteropathy) Disease | DecenTrialz