Actively Recruiting

Phase 2
Age: 12Years +
All Genders
NCT06900595

Testing the Addition of an Anti-Cancer Drug, Cabozantinib to the Immunotherapy Drug Cemiplimab (REGN2810), in Adolescents and Adults With Advanced Adrenocortical Cancer

Led by National Cancer Institute (NCI) · Updated on 2026-05-13

48

Participants Needed

65

Research Sites

170 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

This phase II trial compares the effect of giving cabozantinib with or without cemiplimab in patients with adrenocortical cancer that has spread to nearby tissue or lymph nodes (locally advanced), and that cannot be removed by surgery (unresectable) or that has come back after a period of improvement (recurrent) or that has spread from where it first started (primary site) to other places in the body (metastatic). Cabozantinib is in a class of medications called tyrosine kinase inhibitors. It works by blocking the action of an abnormal protein that signals cancer cells to multiply, which may help keep cancer cells from growing. Immunotherapy with monoclonal antibodies, such as cemiplimab, may help the body's immune system attack the cancer, and may interfere with the ability of tumor cells to grow and spread. Giving cabozantinib with cemiplimab may kill more tumor cells in patients with locally advanced unresectable or recurrent/metastatic adrenocortical cancer.

CONDITIONS

Official Title

Testing the Addition of an Anti-Cancer Drug, Cabozantinib to the Immunotherapy Drug Cemiplimab (REGN2810), in Adolescents and Adults With Advanced Adrenocortical Cancer

Who Can Participate

Age: 12Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Patients must have confirmed adrenocortical carcinoma by histology or cytology
  • Disease must be locally advanced unresectable or recurrent/metastatic
  • Disease must be measurable by RECIST version 1.1 criteria
  • Up to 3 prior systemic therapy lines allowed; treatment-nafve patients are eligible
  • Mitotane treatment must be stopped 28 days before registration and levels below 2 mg/L if given within 6 months
  • No prior treatment with cabozantinib, cMET inhibitors, or anti-CTLA-4/PD-1/PD-L1 therapies
  • Previous radiation, chemotherapy, or targeted therapies allowed if stopped at least 14 days before registration and toxicities resolved to grade 1 or less (except alopecia or mild neuropathy)
  • Clinically adequate wound healing from prior therapies before enrollment
  • Age 12 years or older with body surface area 21.2 m
  • ECOG performance status 0-2 for adults; Lansky score 21 50 for ages 12 to <16; Karnofsky score 21 50 for ages 16 to <18
  • Neutrophil count 1,000/mcL without growth factor support within 2 weeks
  • Platelets 100,000/mcL
  • Hemoglobin 8 g/dL
  • Total bilirubin 1.5 x upper limit of normal (ULN), or  3 mg/dL if Gilbert's disease
  • AST/ALT 3 x ULN
  • Urine protein creatinine ratio 1 mg/mg
  • Creatinine clearance 30 mL/min
  • Assessment of adrenal steroid production within 3 months prior to registration
  • Negative pregnancy test for women of childbearing potential within 14 days
  • Cardiac function class II or better by NYHA within 28 days
  • No congenital long QT syndrome or myocarditis
  • No myocardial infarction or unstable angina within 6 months
  • No significant gastrointestinal conditions increasing bleeding or perforation risk
  • No pancreatitis or recent fractures within specified timeframes
  • No uncontrolled hypertension within 14 days
  • No major blood vessel tumor invasion or recent pulmonary hemorrhage
  • No history of pneumonitis
  • No brain metastases unless treated and stable for at least 4 weeks
  • No recent major or minor surgery with ongoing complications
  • Ability to swallow oral tablets
  • No allergic reaction to cabozantinib or similar compounds
  • Prior or concurrent malignancies allowed if not interfering with study
  • HIV patients on effective therapy with undetectable viral load
  • Controlled hepatitis B and C infections
  • No active autoimmune disease requiring immune suppressive treatment
  • No steroid use above 10 mg prednisone equivalents daily
  • No strong CYP3A4 inhibitors or inducers within 14 days
  • No herbal or traditional Chinese medicines
  • Restrictions on use of certain anticoagulants
  • For crossover: documented disease progression on cabozantinib monotherapy
Not Eligible

You will not qualify if you...

  • Pregnant or nursing individuals
  • Patients with history of myocarditis or congenital long QT syndrome
  • History of myocardial infarction or unstable angina within the past 6 months
  • Clinically significant gastrointestinal abnormalities that increase bleeding or perforation risk
  • History of gastrointestinal perforation within 6 months
  • Known tumor invading gastrointestinal tract increasing risk of bleeding or perforation
  • Current radiologic or clinical evidence of pancreatitis
  • History of clinically significant non-healing wounds or ulcers within 28 days
  • Uncontrolled hypertension within 14 days before registration
  • Known endobronchial lesions or pulmonary hemorrhage within 3 months
  • History of pneumonitis
  • Tumor invading or encasing major blood vessels
  • History of fracture within 28 days
  • Known brain metastases or cranial epidural disease unless treated and stable
  • Major surgery within 2 weeks or minor surgery within 10 days before registration with ongoing complications
  • Allergic reaction to cabozantinib or similar compounds
  • Active autoimmune disease requiring immune suppressive treatment
  • Steroid use above 10 mg prednisone equivalents daily
  • Use of strong CYP3A4 inhibitors or inducers within 14 days
  • Use of herbal supplements or traditional Chinese medicines
  • Active treatment with certain anticoagulants like coumarin agents within 5 days
  • Patients discontinued or meeting discontinuation criteria for cabozantinib due to toxicity not eligible for crossover

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

1
2
3
+1

Trial Site Locations

Total: 65 locations

1

UC San Diego Moores Cancer Center

La Jolla, California, United States, 92093

Actively Recruiting

2

UCHealth University of Colorado Hospital

Aurora, Colorado, United States, 80045

Actively Recruiting

3

Lurie Children's Hospital-Chicago

Chicago, Illinois, United States, 60611

Suspended

4

Northwestern University

Chicago, Illinois, United States, 60611

Actively Recruiting

5

Carle at The Riverfront

Danville, Illinois, United States, 61832

Actively Recruiting

6

Northwestern Medicine Cancer Center Kishwaukee

DeKalb, Illinois, United States, 60115

Actively Recruiting

7

Carle Physician Group-Effingham

Effingham, Illinois, United States, 62401

Actively Recruiting

8

Northwestern Medicine Cancer Center Delnor

Geneva, Illinois, United States, 60134

Actively Recruiting

9

Northwestern Medicine Glenview Outpatient Center

Glenview, Illinois, United States, 60026

Actively Recruiting

10

Northwestern Medicine Grayslake Outpatient Center

Grayslake, Illinois, United States, 60030

Actively Recruiting

11

Northwestern Medicine Lake Forest Hospital

Lake Forest, Illinois, United States, 60045

Actively Recruiting

12

Carle Physician Group-Mattoon/Charleston

Mattoon, Illinois, United States, 61938

Actively Recruiting

13

Carle BroMenn Medical Center

Normal, Illinois, United States, 61761

Actively Recruiting

14

Carle Cancer Institute Normal

Normal, Illinois, United States, 61761

Actively Recruiting

15

Northwestern Medicine Oak Brook

Oak Brook, Illinois, United States, 60523

Actively Recruiting

16

Northwestern Medicine Orland Park

Orland Park, Illinois, United States, 60462

Actively Recruiting

17

Memorial Hospital East

Shiloh, Illinois, United States, 62269

Actively Recruiting

18

Carle Cancer Center

Urbana, Illinois, United States, 61801

Actively Recruiting

19

Northwestern Medicine Cancer Center Warrenville

Warrenville, Illinois, United States, 60555

Actively Recruiting

20

UI Health Care Mission Cancer and Blood - Ankeny Clinic

Ankeny, Iowa, United States, 50023

Actively Recruiting

21

Saint Anthony Regional Hospital

Carroll, Iowa, United States, 51401

Actively Recruiting

22

UI Health Care Mission Cancer and Blood - West Des Moines Clinic

Clive, Iowa, United States, 50325

Actively Recruiting

23

Iowa Methodist Medical Center

Des Moines, Iowa, United States, 50309

Actively Recruiting

24

UI Health Care Mission Cancer and Blood - Des Moines Clinic

Des Moines, Iowa, United States, 50309

Actively Recruiting

25

Broadlawns Medical Center

Des Moines, Iowa, United States, 50314

Actively Recruiting

26

Mercy Medical Center - Des Moines

Des Moines, Iowa, United States, 50314

Actively Recruiting

27

UI Health Care Mission Cancer and Blood - Laurel Clinic

Des Moines, Iowa, United States, 50314

Actively Recruiting

28

UI Healthcare Mission Cancer and Blood - Fort Dodge

Fort Dodge, Iowa, United States, 50501

Actively Recruiting

29

UI Health Care Mission Cancer and Blood - Waukee Clinic

Waukee, Iowa, United States, 50263

Actively Recruiting

30

Dana-Farber Cancer Institute

Boston, Massachusetts, United States, 02215

Actively Recruiting

31

University of Michigan Rogel Cancer Center

Ann Arbor, Michigan, United States, 48109

Actively Recruiting

32

Siteman Cancer Center at Saint Peters Hospital

City of Saint Peters, Missouri, United States, 63376

Actively Recruiting

33

Siteman Cancer Center at West County Hospital

Creve Coeur, Missouri, United States, 63141

Actively Recruiting

34

CoxHealth South Hospital

Springfield, Missouri, United States, 65807

Actively Recruiting

35

Washington University School of Medicine

St Louis, Missouri, United States, 63110

Actively Recruiting

36

Siteman Cancer Center-South County

St Louis, Missouri, United States, 63129

Actively Recruiting

37

Siteman Cancer Center at Christian Hospital

St Louis, Missouri, United States, 63136

Actively Recruiting

38

Nebraska Medicine-Bellevue

Bellevue, Nebraska, United States, 68123

Actively Recruiting

39

Nebraska Medicine-Village Pointe

Omaha, Nebraska, United States, 68118

Actively Recruiting

40

University of Nebraska Medical Center

Omaha, Nebraska, United States, 68198

Actively Recruiting

41

Memorial Sloan Kettering Basking Ridge

Basking Ridge, New Jersey, United States, 07920

Actively Recruiting

42

Memorial Sloan Kettering Monmouth

Middletown, New Jersey, United States, 07748

Actively Recruiting

43

Memorial Sloan Kettering Bergen

Montvale, New Jersey, United States, 07645

Actively Recruiting

44

Memorial Sloan Kettering Commack

Commack, New York, United States, 11725

Actively Recruiting

45

Memorial Sloan Kettering Westchester

Harrison, New York, United States, 10604

Actively Recruiting

46

Memorial Sloan Kettering Cancer Center

New York, New York, United States, 10065

Actively Recruiting

47

Memorial Sloan Kettering Nassau

Uniondale, New York, United States, 11553

Actively Recruiting

48

Duke Cancer Center Cary

Cary, North Carolina, United States, 27518

Actively Recruiting

49

Duke University Medical Center

Durham, North Carolina, United States, 27710

Actively Recruiting

50

Duke Cancer Center Raleigh

Raleigh, North Carolina, United States, 27609

Actively Recruiting

51

Ohio State University Comprehensive Cancer Center

Columbus, Ohio, United States, 43210

Actively Recruiting

52

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, United States, 15224

Actively Recruiting

53

Prisma Health Cancer Institute - Spartanburg

Boiling Springs, South Carolina, United States, 29316

Actively Recruiting

54

Prisma Health Richland Hospital

Columbia, South Carolina, United States, 29203

Actively Recruiting

55

Prisma Health Cancer Institute - Easley

Easley, South Carolina, United States, 29640

Actively Recruiting

56

BI-LO Charities Children's Cancer Center

Greenville, South Carolina, United States, 29605

Actively Recruiting

57

Prisma Health Cancer Institute - Butternut

Greenville, South Carolina, United States, 29605

Actively Recruiting

58

Prisma Health Cancer Institute - Faris

Greenville, South Carolina, United States, 29605

Actively Recruiting

59

Prisma Health Cancer Institute - Eastside

Greenville, South Carolina, United States, 29615

Actively Recruiting

60

Prisma Health Cancer Institute - Greer

Greer, South Carolina, United States, 29650

Actively Recruiting

61

Prisma Health Cancer Institute - Seneca

Seneca, South Carolina, United States, 29672

Actively Recruiting

62

Saint Jude Children's Research Hospital

Memphis, Tennessee, United States, 38105

Actively Recruiting

63

University of Texas Health Science Center at San Antonio

San Antonio, Texas, United States, 78229

Actively Recruiting

64

VCU Massey Cancer Center at Stony Point

Richmond, Virginia, United States, 23235

Actively Recruiting

65

VCU Massey Comprehensive Cancer Center

Richmond, Virginia, United States, 23298

Actively Recruiting

Loading map...

How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

RANDOMIZED

Model

CROSSOVER

Primary Purpose

TREATMENT

Number of Arms

2

Not the Right Trial for You?

Explore thousands of other clinical trials that might be a better match.
Sign up to get personalized trial recommendations delivered to your inbox.

Already have an account? Log in here