Actively Recruiting

Phase 2
Age: 16Years +
All Genders
NCT06599697

The MIGHT Trial - An Exploratory Clinical Trial of IVIG in Anti-HMGCR Immune Mediated Necrotizing Myopathy

Led by University of Alabama at Birmingham · Updated on 2026-02-24

12

Participants Needed

5

Research Sites

87 weeks

Total Duration

On this page

Sponsors

U

University of Alabama at Birmingham

Lead Sponsor

N

National Institute of Arthritis and Musculoskeletal and Skin Diseases (NIAMS)

Collaborating Sponsor

AI-Summary

What this Trial Is About

This is a randomized, placebo-controlled, double blinded phase 2 exploratory clinical trial of intravenously administered pooled human immunoglobulin (IVIG) in anti-3-hydroxy-3-methylglutaryl-CoA reductase (HMGCR) immune mediated necrotizing myopathy (IMNM). Planned enrollment is 12 individuals with active anti-HMGCR IMNM meeting inclusion and exclusion criteria. Assuming 20% drop-out, the investigators anticipate 10 participants will complete all study assessments. Enrolled participants will be randomized 1:1 to either IVIG 2g/kg or placebo (0.9% sodium chloride at equivalent volume) at weeks 0, 4, and 8. The primary efficacy and co-primary safety and tolerability endpoints will be assessed at week 12. After the randomized phase of the trial, all participants will be offered to continue on to an open-label extension phase in which participants will receive IVIG at weeks 12, 16, and 20. Participants will then return at week 24 for a final non-infusion visit to reassess safety, tolerability, and efficacy outcome.

CONDITIONS

Official Title

The MIGHT Trial - An Exploratory Clinical Trial of IVIG in Anti-HMGCR Immune Mediated Necrotizing Myopathy

Who Can Participate

Age: 16Years +
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Age > 16 years
  • Positive for anti-HMGCR antibodies
  • Muscle strength (MMT-8) score less than 142
  • Serum creatine kinase (CK) level more than 5 times the upper limit of normal
  • Disease duration of anti-HMGCR IMNM less than 36 months at screening
  • No moderate or severe breathing or swallowing problems from anti-HMGCR IMNM at screening
  • No history of dermatomyositis rash
  • Must live in a state with a participating research site
Not Eligible

You will not qualify if you...

  • Taking oral glucocorticoid dose greater than 15 mg daily at screening
  • Changed oral glucocorticoid dose within 2 weeks before screening
  • Previous IVIG treatment for anti-HMGCR IMNM
  • Using more than one oral conventional synthetic DMARD at screening
  • Changed dose of DMARDs within 4 weeks before screening
  • Received rituximab within 6 months before screening
  • Received plasma exchange, cyclophosphamide, or biologic immunosuppressive medication within 3 months before screening
  • Using statin medication at screening
  • History of severe allergic reaction to IVIG
  • History of angina, heart attack, stroke, or transient ischemic attack within 12 months before screening
  • Pregnant, breastfeeding, or unwilling to use effective birth control if female of childbearing potential
  • Wells criteria score of 2 or more for deep vein thrombosis at screening
  • Wells criteria score of 4 or more for pulmonary embolism at screening
  • Weight over 120 kg
  • History of cancer (except non-melanoma skin cancer) within 5 years before screening
  • History of pulmonary embolism or deep vein thrombosis within 3 years before screening
  • History of blood thickening or clotting disorders
  • Currently using blood-thinning medications (except oral anti-platelet agents)
  • Kidney function (GFR) less than 60 mL/min at screening
  • Any medical condition that the investigator believes would make participation unsafe or interfere with study evaluation

AI-Screening

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Trial Site Locations

Total: 5 locations

1

University of Alabama at Birmingham

Birmingham, Alabama, United States, 35233

Actively Recruiting

2

Johns Hopkins University

Baltimore, Maryland, United States, 21218

Not Yet Recruiting

3

University of Pittsburgh

Pittsburgh, Pennsylvania, United States, 15260

Not Yet Recruiting

4

University of Texas Health Science Center at Houston

Houston, Texas, United States, 77030

Active, Not Recruiting

5

University of Washington

Seattle, Washington, United States, 98195

Active, Not Recruiting

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Research Team

J

James Andrews, MD

CONTACT

H

Hannah E Howell, MS

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

DOUBLE

Allocation

RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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