Actively Recruiting

Phase 3
Age: 0 - 30Years
All Genders
NCT06172296

Dinutuximab With Chemotherapy, Surgery and Stem Cell Transplantation for the Treatment of Children With Newly Diagnosed High Risk Neuroblastoma

Led by National Cancer Institute (NCI) · Updated on 2026-05-14

478

Participants Needed

177

Research Sites

297 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

This phase III trial tests how well the addition of dinutuximab to Induction chemotherapy along with standard of care surgical resection of the primary tumor, radiation, stem cell transplantation, and immunotherapy works for treating children with newly diagnosed high-risk neuroblastoma. Dinutuximab is a monoclonal antibody that binds to a molecule called GD2, which is found on the surface of neuroblastoma cells, but is not present on many healthy or normal cells in the body. When dinutuximab binds to the neuroblastoma cells, it helps signal the immune system to kill the tumor cells. This helps the cells of the immune system kill the cancer cells, this is a type of immunotherapy. When chemotherapy and immunotherapy are given together, during the same treatment cycle, it is called chemoimmunotherapy. This clinical trial randomly assigns patients to receive either standard chemotherapy and surgery or chemoimmunotherapy (chemotherapy plus dinutuximab) and surgery during Induction therapy. Chemotherapy drugs administered during Induction include, cyclophosphamide, topotecan, cisplatin, etoposide, vincristine, and doxorubicin. These drugs work in different ways to stop the growth of cancer cells, either by killing the cells, by stopping them from dividing or by stopping them from spreading. Upon completion of 5 cycles of Induction therapy, a disease evaluation is completed to determine how well the treatment worked. If the tumor responds to therapy, patients receive a tandem transplantation with stem cell rescue. If the tumor has little improvement or worsens, patients receive chemoimmunotherapy on Extended Induction. During Extended Induction, dinutuximab is given with irinotecan, temozolomide. Patients with a good response to therapy move on to Consolidation therapy, when very high doses of chemotherapy are given at two separate points to kill any remaining cancer cells. Following, transplant, radiation therapy is given to the site where the cancer originated (primary site) and to any other areas that are still active at the end of Induction. The final stage of therapy is Post-Consolidation. During Post-Consolidation, dinutuximab is given with isotretinoin, with the goal of maintaining the response achieved with the previous therapy. Adding dinutuximab to Induction chemotherapy along with standard of care surgical resection of the primary tumor, radiation, stem cell transplantation, and immunotherapy may be better at treating children with newly diagnosed high-risk neuroblastoma.

CONDITIONS

Official Title

Dinutuximab With Chemotherapy, Surgery and Stem Cell Transplantation for the Treatment of Children With Newly Diagnosed High Risk Neuroblastoma

Who Can Participate

Age: 0 - 30Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Patients must be enrolled on APEC14B1 and consent to Molecular Characterization Initiative testing before this study
  • Age 30 years or younger at initial diagnosis with high-risk neuroblastoma
  • Diagnosis of neuroblastoma or ganglioneuroblastoma (nodular) confirmed by tumor pathology or bone marrow tumor cells with elevated urinary catecholamines
  • Newly diagnosed high-risk neuroblastoma defined by INRG stage and MYCN amplification or age and stage criteria as specified
  • Body surface area of at least 0.25 m^2
  • No prior anti-cancer therapy except emergency treatment or one cycle of chemotherapy for low/intermediate risk disease
  • HIV-infected patients on effective antiretroviral therapy with undetectable viral load within 6 months
  • Kidney function with serum creatinine or GFR meeting specified age/sex thresholds
  • Total bilirubin less than or equal to 1.5 times the upper limit of normal for age
  • Alanine aminotransferase (ALT) less than or equal to 10 times the upper limit of normal
  • Heart function with shortening fraction of at least 27% or ejection fraction of at least 50%
  • Ability to tolerate peripheral blood stem cell collection without contraindications
  • Signed informed consent and compliance with all institutional, FDA, and NCI human study requirements
Not Eligible

You will not qualify if you...

  • Patients aged 365 to 546 days with INRG stage M and MYCN non-amplified neuroblastoma
  • Patients 547 days or older with INRG stage L2 and MYCN non-amplified neuroblastoma
  • Known bone marrow failure syndromes
  • Use of chronic immunosuppressive medications except for allergic reactions or adrenal replacement (topical and inhaled corticosteroids allowed)
  • Primary immunodeficiency requiring ongoing immune globulin replacement
  • Pregnant females
  • Lactating females planning to breastfeed
  • Sexually active patients of reproductive potential not agreeing to effective contraception during study participation

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

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Trial Site Locations

Total: 177 locations

1

Children's Hospital of Alabama

Birmingham, Alabama, United States, 35233

Actively Recruiting

2

USA Health Strada Patient Care Center

Mobile, Alabama, United States, 36604

Actively Recruiting

3

Banner Children's at Desert

Mesa, Arizona, United States, 85202

Actively Recruiting

4

Phoenix Childrens Hospital

Phoenix, Arizona, United States, 85016

Actively Recruiting

5

Banner University Medical Center - Tucson

Tucson, Arizona, United States, 85719

Actively Recruiting

6

Arkansas Children's Hospital

Little Rock, Arkansas, United States, 72202-3591

Actively Recruiting

7

Kaiser Permanente Downey Medical Center

Downey, California, United States, 90242

Actively Recruiting

8

City of Hope Comprehensive Cancer Center

Duarte, California, United States, 91010

Actively Recruiting

9

Loma Linda University Medical Center

Loma Linda, California, United States, 92354

Actively Recruiting

10

Miller Children's and Women's Hospital Long Beach

Long Beach, California, United States, 90806

Actively Recruiting

11

Children's Hospital Los Angeles

Los Angeles, California, United States, 90027

Actively Recruiting

12

Cedars-Sinai Medical Center

Los Angeles, California, United States, 90048

Actively Recruiting

13

Mattel Children's Hospital UCLA

Los Angeles, California, United States, 90095

Actively Recruiting

14

Valley Children's Hospital

Madera, California, United States, 93636

Actively Recruiting

15

UCSF Benioff Children's Hospital Oakland

Oakland, California, United States, 94609

Actively Recruiting

16

Kaiser Permanente-Oakland

Oakland, California, United States, 94611

Actively Recruiting

17

Children's Hospital of Orange County

Orange, California, United States, 92868

Actively Recruiting

18

Lucile Packard Children's Hospital Stanford University

Palo Alto, California, United States, 94304

Actively Recruiting

19

Sutter Medical Center Sacramento

Sacramento, California, United States, 95816

Actively Recruiting

20

University of California Davis Comprehensive Cancer Center

Sacramento, California, United States, 95817

Actively Recruiting

21

Rady Children's Hospital - San Diego

San Diego, California, United States, 92123

Actively Recruiting

22

UCSF Medical Center-Mission Bay

San Francisco, California, United States, 94158

Actively Recruiting

23

Children's Hospital Colorado

Aurora, Colorado, United States, 80045

Actively Recruiting

24

Connecticut Children's Medical Center

Hartford, Connecticut, United States, 06106

Actively Recruiting

25

Yale University

New Haven, Connecticut, United States, 06520

Actively Recruiting

26

Alfred I duPont Hospital for Children

Wilmington, Delaware, United States, 19803

Actively Recruiting

27

Children's National Medical Center

Washington D.C., District of Columbia, United States, 20010

Actively Recruiting

28

Broward Health Medical Center

Fort Lauderdale, Florida, United States, 33316

Actively Recruiting

29

Golisano Children's Hospital of Southwest Florida

Fort Myers, Florida, United States, 33908

Actively Recruiting

30

UF Health Cancer Institute - Gainesville

Gainesville, Florida, United States, 32610

Actively Recruiting

31

Memorial Regional Hospital/Joe DiMaggio Children's Hospital

Hollywood, Florida, United States, 33021

Actively Recruiting

32

Nemours Children's Clinic-Jacksonville

Jacksonville, Florida, United States, 32207

Actively Recruiting

33

University of Miami Miller School of Medicine-Sylvester Cancer Center

Miami, Florida, United States, 33136

Actively Recruiting

34

Nicklaus Children's Hospital

Miami, Florida, United States, 33155

Actively Recruiting

35

AdventHealth Orlando

Orlando, Florida, United States, 32803

Actively Recruiting

36

Arnold Palmer Hospital for Children

Orlando, Florida, United States, 32806

Actively Recruiting

37

Nemours Children's Hospital

Orlando, Florida, United States, 32827

Actively Recruiting

38

Johns Hopkins All Children's Hospital

St. Petersburg, Florida, United States, 33701

Actively Recruiting

39

Saint Mary's Medical Center

West Palm Beach, Florida, United States, 33407

Actively Recruiting

40

Children's Healthcare of Atlanta - Arthur M Blank Hospital

Atlanta, Georgia, United States, 30329

Actively Recruiting

41

Memorial Health University Medical Center

Savannah, Georgia, United States, 31404

Actively Recruiting

42

Kapiolani Medical Center for Women and Children

Honolulu, Hawaii, United States, 96826

Actively Recruiting

43

Lurie Children's Hospital-Chicago

Chicago, Illinois, United States, 60611

Suspended

44

University of Illinois

Chicago, Illinois, United States, 60612

Actively Recruiting

45

University of Chicago Comprehensive Cancer Center

Chicago, Illinois, United States, 60637

Actively Recruiting

46

Advocate Children's Hospital-Oak Lawn

Oak Lawn, Illinois, United States, 60453

Actively Recruiting

47

Advocate Children's Hospital-Park Ridge

Park Ridge, Illinois, United States, 60068

Actively Recruiting

48

Saint Jude Midwest Affiliate

Peoria, Illinois, United States, 61637

Actively Recruiting

49

Southern Illinois University School of Medicine

Springfield, Illinois, United States, 62702

Actively Recruiting

50

Riley Hospital for Children

Indianapolis, Indiana, United States, 46202

Actively Recruiting

51

Blank Children's Hospital

Des Moines, Iowa, United States, 50309

Actively Recruiting

52

University of Iowa/Holden Comprehensive Cancer Center

Iowa City, Iowa, United States, 52242

Actively Recruiting

53

Wesley Medical Center

Wichita, Kansas, United States, 67214

Actively Recruiting

54

University of Kentucky/Markey Cancer Center

Lexington, Kentucky, United States, 40536

Actively Recruiting

55

Norton Children's Hospital

Louisville, Kentucky, United States, 40202

Actively Recruiting

56

Children's Hospital New Orleans

New Orleans, Louisiana, United States, 70118

Actively Recruiting

57

Eastern Maine Medical Center

Bangor, Maine, United States, 04401

Actively Recruiting

58

Maine Children's Cancer Program

Scarborough, Maine, United States, 04074

Actively Recruiting

59

University of Maryland/Greenebaum Cancer Center

Baltimore, Maryland, United States, 21201

Actively Recruiting

60

Sinai Hospital of Baltimore

Baltimore, Maryland, United States, 21215

Actively Recruiting

61

Johns Hopkins University/Sidney Kimmel Cancer Center

Baltimore, Maryland, United States, 21287

Actively Recruiting

62

Walter Reed National Military Medical Center

Bethesda, Maryland, United States, 20889-5600

Actively Recruiting

63

Massachusetts General Hospital Cancer Center

Boston, Massachusetts, United States, 02114

Actively Recruiting

64

Dana-Farber Cancer Institute

Boston, Massachusetts, United States, 02215

Actively Recruiting

65

C S Mott Children's Hospital

Ann Arbor, Michigan, United States, 48109

Actively Recruiting

66

Children's Hospital of Michigan

Detroit, Michigan, United States, 48201

Actively Recruiting

67

Corewell Health Grand Rapids Hospitals - Helen DeVos Children's Hospital

Grand Rapids, Michigan, United States, 49503

Actively Recruiting

68

Bronson Methodist Hospital

Kalamazoo, Michigan, United States, 49007

Actively Recruiting

69

Corewell Health Children's

Royal Oak, Michigan, United States, 48073

Actively Recruiting

70

Children's Hospitals and Clinics of Minnesota - Minneapolis

Minneapolis, Minnesota, United States, 55404

Actively Recruiting

71

University of Minnesota/Masonic Cancer Center

Minneapolis, Minnesota, United States, 55455

Actively Recruiting

72

Mayo Clinic in Rochester

Rochester, Minnesota, United States, 55905

Actively Recruiting

73

University of Mississippi Medical Center

Jackson, Mississippi, United States, 39216

Actively Recruiting

74

University of Missouri Children's Hospital

Columbia, Missouri, United States, 65212

Actively Recruiting

75

Children's Mercy Hospitals and Clinics

Kansas City, Missouri, United States, 64108

Actively Recruiting

76

Washington University School of Medicine

St Louis, Missouri, United States, 63110

Actively Recruiting

77

Mercy Hospital Saint Louis

St Louis, Missouri, United States, 63141

Actively Recruiting

78

Children's Hospital and Medical Center of Omaha

Omaha, Nebraska, United States, 68114

Actively Recruiting

79

University of Nebraska Medical Center

Omaha, Nebraska, United States, 68198

Actively Recruiting

80

Alliance for Childhood Diseases/Cure 4 the Kids Foundation

Las Vegas, Nevada, United States, 89135

Actively Recruiting

81

Dartmouth Hitchcock Medical Center/Dartmouth Cancer Center

Lebanon, New Hampshire, United States, 03756

Actively Recruiting

82

Hackensack University Medical Center

Hackensack, New Jersey, United States, 07601

Actively Recruiting

83

Morristown Medical Center

Morristown, New Jersey, United States, 07960

Actively Recruiting

84

Saint Peter's University Hospital

New Brunswick, New Jersey, United States, 08901

Actively Recruiting

85

Rutgers Cancer Institute of New Jersey-Robert Wood Johnson University Hospital

New Brunswick, New Jersey, United States, 08903

Actively Recruiting

86

Saint Joseph's Regional Medical Center

Paterson, New Jersey, United States, 07503

Actively Recruiting

87

University of New Mexico Cancer Center

Albuquerque, New Mexico, United States, 87106

Suspended

88

Albany Medical Center

Albany, New York, United States, 12208

Actively Recruiting

89

Roswell Park Cancer Institute

Buffalo, New York, United States, 14263

Actively Recruiting

90

NYU Langone Hospital - Long Island

Mineola, New York, United States, 11501

Actively Recruiting

91

The Steven and Alexandra Cohen Children's Medical Center of New York

New Hyde Park, New York, United States, 11040

Actively Recruiting

92

Laura and Isaac Perlmutter Cancer Center at NYU Langone

New York, New York, United States, 10016

Actively Recruiting

93

NYP/Columbia University Medical Center/Herbert Irving Comprehensive Cancer Center

New York, New York, United States, 10032

Actively Recruiting

94

University of Rochester

Rochester, New York, United States, 14642

Actively Recruiting

95

State University of New York Upstate Medical University

Syracuse, New York, United States, 13210

Actively Recruiting

96

Montefiore Medical Center - Moses Campus

The Bronx, New York, United States, 10467

Actively Recruiting

97

New York Medical College

Valhalla, New York, United States, 10595

Actively Recruiting

98

Mission Hospital

Asheville, North Carolina, United States, 28801

Suspended

99

UNC Lineberger Comprehensive Cancer Center

Chapel Hill, North Carolina, United States, 27599

Actively Recruiting

100

Carolinas Medical Center/Levine Cancer Institute

Charlotte, North Carolina, United States, 28203

Actively Recruiting

101

Novant Health Presbyterian Medical Center

Charlotte, North Carolina, United States, 28204

Actively Recruiting

102

Duke University Medical Center

Durham, North Carolina, United States, 27710

Actively Recruiting

103

East Carolina University

Greenville, North Carolina, United States, 27834

Actively Recruiting

104

Wake Forest University Health Sciences

Winston-Salem, North Carolina, United States, 27157

Actively Recruiting

105

Sanford Broadway Medical Center

Fargo, North Dakota, United States, 58122

Actively Recruiting

106

Children's Hospital Medical Center of Akron

Akron, Ohio, United States, 44308

Actively Recruiting

107

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, United States, 45229

Suspended

108

Rainbow Babies and Childrens Hospital

Cleveland, Ohio, United States, 44106

Actively Recruiting

109

Cleveland Clinic Foundation

Cleveland, Ohio, United States, 44195

Actively Recruiting

110

Nationwide Children's Hospital

Columbus, Ohio, United States, 43205

Actively Recruiting

111

Dayton Children's Hospital

Dayton, Ohio, United States, 45404

Actively Recruiting

112

ProMedica Toledo Hospital/Russell J Ebeid Children's Hospital

Toledo, Ohio, United States, 43606

Actively Recruiting

113

University of Oklahoma Health Sciences Center

Oklahoma City, Oklahoma, United States, 73104

Actively Recruiting

114

Natalie Warren Bryant Cancer Center at Saint Francis

Tulsa, Oklahoma, United States, 74136

Actively Recruiting

115

Legacy Emanuel Children's Hospital

Portland, Oregon, United States, 97227

Actively Recruiting

116

Oregon Health and Science University

Portland, Oregon, United States, 97239

Actively Recruiting

117

Lehigh Valley Hospital-Cedar Crest

Allentown, Pennsylvania, United States, 18103

Actively Recruiting

118

Geisinger Medical Center

Danville, Pennsylvania, United States, 17822

Actively Recruiting

119

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

120

Saint Christopher's Hospital for Children

Philadelphia, Pennsylvania, United States, 19134

Actively Recruiting

121

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, United States, 15224

Actively Recruiting

122

Rhode Island Hospital

Providence, Rhode Island, United States, 02903

Actively Recruiting

123

Medical University of South Carolina

Charleston, South Carolina, United States, 29425

Actively Recruiting

124

Prisma Health Richland Hospital

Columbia, South Carolina, United States, 29203

Actively Recruiting

125

BI-LO Charities Children's Cancer Center

Greenville, South Carolina, United States, 29605

Actively Recruiting

126

Sanford USD Medical Center - Sioux Falls

Sioux Falls, South Dakota, United States, 57117-5134

Actively Recruiting

127

East Tennessee Childrens Hospital

Knoxville, Tennessee, United States, 37916

Actively Recruiting

128

Saint Jude Children's Research Hospital

Memphis, Tennessee, United States, 38105

Actively Recruiting

129

The Children's Hospital at TriStar Centennial

Nashville, Tennessee, United States, 37203

Actively Recruiting

130

Vanderbilt University/Ingram Cancer Center

Nashville, Tennessee, United States, 37232

Actively Recruiting

131

Dell Children's Medical Center of Central Texas

Austin, Texas, United States, 78723

Actively Recruiting

132

Driscoll Children's Hospital

Corpus Christi, Texas, United States, 78411

Actively Recruiting

133

Medical City Dallas Hospital

Dallas, Texas, United States, 75230

Actively Recruiting

134

UT Southwestern/Simmons Cancer Center-Dallas

Dallas, Texas, United States, 75390

Actively Recruiting

135

El Paso Children's Hospital

El Paso, Texas, United States, 79905

Actively Recruiting

136

Cook Children's Medical Center

Fort Worth, Texas, United States, 76104

Actively Recruiting

137

Baylor College of Medicine/Dan L Duncan Comprehensive Cancer Center

Houston, Texas, United States, 77030

Actively Recruiting

138

M D Anderson Cancer Center

Houston, Texas, United States, 77030

Actively Recruiting

139

Covenant Children's Hospital

Lubbock, Texas, United States, 79410

Actively Recruiting

140

UMC Cancer Center / UMC Health System

Lubbock, Texas, United States, 79415

Actively Recruiting

141

Children's Hospital of San Antonio

San Antonio, Texas, United States, 78207

Actively Recruiting

142

Methodist Children's Hospital of South Texas

San Antonio, Texas, United States, 78229

Actively Recruiting

143

University of Texas Health Science Center at San Antonio

San Antonio, Texas, United States, 78229

Actively Recruiting

144

Primary Children's Hospital

Salt Lake City, Utah, United States, 84113

Actively Recruiting

145

University of Vermont and State Agricultural College

Burlington, Vermont, United States, 05405

Actively Recruiting

146

University of Virginia Cancer Center

Charlottesville, Virginia, United States, 22908

Actively Recruiting

147

Naval Medical Center - Portsmouth

Portsmouth, Virginia, United States, 23708-2197

Actively Recruiting

148

Seattle Children's Hospital

Seattle, Washington, United States, 98105

Actively Recruiting

149

Providence Sacred Heart Medical Center and Children's Hospital

Spokane, Washington, United States, 99204

Actively Recruiting

150

Mary Bridge Children's Hospital and Health Center

Tacoma, Washington, United States, 98405

Actively Recruiting

151

Edwards Comprehensive Cancer Center

Huntington, West Virginia, United States, 25701

Actively Recruiting

152

West Virginia University Healthcare

Morgantown, West Virginia, United States, 26506

Actively Recruiting

153

Saint Vincent Hospital Cancer Center Green Bay

Green Bay, Wisconsin, United States, 54301

Suspended

154

University of Wisconsin Carbone Cancer Center - University Hospital

Madison, Wisconsin, United States, 53792

Actively Recruiting

155

Marshfield Medical Center-Marshfield

Marshfield, Wisconsin, United States, 54449

Actively Recruiting

156

Children's Hospital of Wisconsin

Milwaukee, Wisconsin, United States, 53226

Actively Recruiting

157

Sydney Children's Hospital

Randwick, New South Wales, Australia, 2031

Actively Recruiting

158

The Children's Hospital at Westmead

Westmead, New South Wales, Australia, 2145

Actively Recruiting

159

Queensland Children's Hospital

South Brisbane, Queensland, Australia, 4101

Actively Recruiting

160

Royal Children's Hospital

Parkville, Victoria, Australia, 3052

Actively Recruiting

161

Perth Children's Hospital

Perth, Western Australia, Australia, 6009

Actively Recruiting

162

Alberta Children's Hospital

Calgary, Alberta, Canada, T3B 6A8

Actively Recruiting

163

University of Alberta Hospital

Edmonton, Alberta, Canada, T6G 2B7

Actively Recruiting

164

British Columbia Children's Hospital

Vancouver, British Columbia, Canada, V6H 3V4

Actively Recruiting

165

CancerCare Manitoba

Winnipeg, Manitoba, Canada, R3E 0V9

Actively Recruiting

166

Janeway Child Health Centre

St. John's, Newfoundland and Labrador, Canada, A1B 3V6

Actively Recruiting

167

IWK Health Centre

Halifax, Nova Scotia, Canada, B3K 6R8

Actively Recruiting

168

McMaster Children's Hospital at Hamilton Health Sciences

Hamilton, Ontario, Canada, L8N 3Z5

Actively Recruiting

169

Children's Hospital

London, Ontario, Canada, N6A 5W9

Actively Recruiting

170

Children's Hospital of Eastern Ontario

Ottawa, Ontario, Canada, K1H 8L1

Actively Recruiting

171

Hospital for Sick Children

Toronto, Ontario, Canada, M5G 1X8

Actively Recruiting

172

The Montreal Children's Hospital of the MUHC

Montreal, Quebec, Canada, H3H 1P3

Actively Recruiting

173

Centre Hospitalier Universitaire Sainte-Justine

Montreal, Quebec, Canada, H3T 1C5

Actively Recruiting

174

Centre Hospitalier Universitaire de Sherbrooke-Fleurimont

Sherbrooke, Quebec, Canada, J1H 5N4

Actively Recruiting

175

Jim Pattison Children's Hospital

Saskatoon, Saskatchewan, Canada, S7N 0W8

Actively Recruiting

176

CHU de Quebec-Centre Hospitalier de l'Universite Laval (CHUL)

Québec, Canada, G1V 4G2

Actively Recruiting

177

Starship Children's Hospital

Grafton, Auckland, New Zealand, 1145

Actively Recruiting

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How is the study designed?

Study Type

INTERVENTIONAL

Masking

NONE

Allocation

RANDOMIZED

Model

PARALLEL

Primary Purpose

TREATMENT

Number of Arms

2

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