Actively Recruiting

Phase 3
Age: 18Years - 75Years
All Genders
NCT06563895

Acoramidis Transthyretin Amyloidosis Prevention Trial in the Young (ACT-EARLY) Study in Asymptomatic Carriers of a Pathogenic TTR Variant

Led by Eidos Therapeutics, a BridgeBio company · Updated on 2026-05-12

587

Participants Needed

101

Research Sites

394 weeks

Total Duration

On this page

AI-Summary

What this Trial Is About

Transthyretin amyloidosis (ATTR) is a disease where the normally occurring transthyretin (TTR) protein falls apart and forms amyloid, a sticky plaque-like substance that accumulates in different organs in the body and can cause damage to the organ. There are two ways that the TTR protein can fall apart. One way occurs as a person ages, where the normal TTR protein can fall apart and form amyloid that may no longer be sufficiently cleared by the body. This type of ATTR is known as wild-type ATTR (ATTRwt). The other way occurs when a person inherits a defective TTR gene that causes the TTR protein to spontaneously fall apart. This form of the disease is known as variant ATTR (ATTRv) and can be detected in adults by a genetic test of their TTR gene before they age. Amyloid build-up in the heart causes the heart wall to become thick and stiff and can result in heart failure and even death. Accumulation of TTR amyloid in the heart is known as transthyretin amyloid cardiomyopathy or ATTR-CM. Amyloid can also deposit in the nerve tissues leading to nerve problems. Accumulation of TTR in the nerves is known as transthyretin amyloid polyneuropathy or ATTR-PN. Acoramidis is an experimental drug designed to bind tightly to TTR in the blood and stabilize its structure, so it does not form the harmful amyloid plaques that can cause damage to organs. This study is intended to determine if treatment with acoramidis in participants with ATTRv who have not yet developed any symptoms of disease can prevent or delay the development of ATTR-CM or ATTR-PN disease. If adults with an inherited defective TTR gene are treated early before any of the symptoms of disease have developed, it may be possible to delay the onset or prevent the disease entirely.

CONDITIONS

Official Title

Acoramidis Transthyretin Amyloidosis Prevention Trial in the Young (ACT-EARLY) Study in Asymptomatic Carriers of a Pathogenic TTR Variant

Who Can Participate

Age: 18Years - 75Years
All Genders

Eligibility Criteria

Eligible

You may qualify if you...

  • Male or female aged 18 to 75 years inclusive
  • Established genotype confirming pathogenic or likely pathogenic TTR gene variant
  • Age within 10 years younger or older than predicted age of disease onset based on family history or published data
Not Eligible

You will not qualify if you...

  • Evidence of transthyretin amyloid cardiomyopathy or polyneuropathy
  • Current or recent (within 1 to 12 months) treatment with other TTR modifying therapies
  • Contraindication to or inability to undergo cardiac magnetic resonance testing
  • Major organ dysfunction including kidney, liver, heart disease, or neuropathy
  • Other significant diseases or conditions such as cancer within 5 years, untreated thyroid disorders, type 1 diabetes, active hepatitis B or C, or HIV
  • Major surgery within the past 3 months or planned within the next 12 months
  • Known hypersensitivity to acoramidis

AI-Screening

AI-Powered Screening

Complete this quick 3-step screening to check your eligibility

1
2
3
+1

Trial Site Locations

Total: 101 locations

1

University of California, San Diego (UCSD) - Medical Center

La Jolla, California, United States, 92037

Actively Recruiting

2

University of California, Los Angeles (UCLA) - David Geffen School of Medicine

Los Angeles, California, United States, 90095

Actively Recruiting

3

University of California, San Francisco (UCSF)

San Francisco, California, United States, 94143

Actively Recruiting

4

Stanford University

Stanford, California, United States, 94305

Actively Recruiting

5

University of Colorado Anschutz

Aurora, Colorado, United States, 80045

Actively Recruiting

6

Yale University School of Medicine - Section of Cardiology

New Haven, Connecticut, United States, 06519

Actively Recruiting

7

MedStar Washington Hospital Center - MedStar Heart and Vascular Institute

Washington D.C., District of Columbia, United States, 20010

Actively Recruiting

8

Mayo Clinic - Jacksonville

Jacksonville, Florida, United States, 32224

Actively Recruiting

9

Cleveland Clinic Florida

Weston, Florida, United States, 33331

Actively Recruiting

10

Emory University School of Medicine

Atlanta, Georgia, United States, 30322

Actively Recruiting

11

John H. Stroger, Jr. Hospital of Cook County

Chicago, Illinois, United States, 60612

Actively Recruiting

12

University of Chicago - Medical Center

Chicago, Illinois, United States, 60637

Actively Recruiting

13

University of Maryland Medical Center

Baltimore, Maryland, United States, 21201

Actively Recruiting

14

Johns Hopkins University

Baltimore, Maryland, United States, 21287

Actively Recruiting

15

Massachusetts General Hospital

Boston, Massachusetts, United States, 02114

Actively Recruiting

16

Brigham and Women's Hospital

Boston, Massachusetts, United States, 02115

Actively Recruiting

17

Boston University (BU) School of Medicine

Boston, Massachusetts, United States, 02118

Actively Recruiting

18

Henry Ford Health System

Detroit, Michigan, United States, 48202

Actively Recruiting

19

Mayo Clinic - Rochester

Rochester, Minnesota, United States, 55905

Actively Recruiting

20

St. Luke's Hospital of Kansas City

Kansas City, Missouri, United States, 64111

Actively Recruiting

21

Washington University in St. Louis

St Louis, Missouri, United States, 63110

Actively Recruiting

22

Rutgers-Robert Wood Johnson Medical School

New Brunswick, New Jersey, United States, 08901

Actively Recruiting

23

New York University (NYU) School of Medicine - Langone Medical Center

New York, New York, United States, 10016

Actively Recruiting

24

Mount Sinai Hospital

New York, New York, United States, 10029

Actively Recruiting

25

Columbia University Medical Center

New York, New York, United States, 10032

Actively Recruiting

26

Laurelton Heart Specialists

Rosedale, New York, United States, 11422

Actively Recruiting

27

Duke University Medical Center

Durham, North Carolina, United States, 27710

Actively Recruiting

28

Cleveland Clinic

Cleveland, Ohio, United States, 44195

Actively Recruiting

29

Oregon Health & Science University

Portland, Oregon, United States, 97239

Actively Recruiting

30

Penn Presbyterian Medical Center

Philadelphia, Pennsylvania, United States, 19104

Actively Recruiting

31

University of Pittsburgh Medical Center, Presbyterian Hospital

Pittsburgh, Pennsylvania, United States, 15213

Actively Recruiting

32

Medical University of South Carolina (MUSC)

Charleston, South Carolina, United States, 29425

Actively Recruiting

33

Prisma Health Cancer Institute

Greenville, South Carolina, United States, 89605

Actively Recruiting

34

National Neuromuscular Research Institute

Austin, Texas, United States, 78759

Actively Recruiting

35

University of Texas Southwestern

Dallas, Texas, United States, 75390

Actively Recruiting

36

University of Utah

Salt Lake City, Utah, United States, 84132

Actively Recruiting

37

INOVA Fairfax Hospital

Falls Church, Virginia, United States, 22042

Actively Recruiting

38

Virginia Commonwealth University

Richmond, Virginia, United States, 23219

Actively Recruiting

39

University of Washington Medical Center

Seattle, Washington, United States, 98195

Actively Recruiting

40

Hospital Italiano de Buenos Aires

Buenos Aires, Argentina, C1199ABB

Actively Recruiting

41

Hospital Britanico de Buenos Aires

Buenos Aires, Argentina, C1280AEB

Actively Recruiting

42

St Vincent's Hospital Sydney

Darlinghurst, Australia, 2010

Actively Recruiting

43

Fiona Stanley Hospital

Murdoch, Australia, 6150

Actively Recruiting

44

Westmead Hospital

Westmead, Australia, NSW 2145

Actively Recruiting

45

Princess Alexandra Hospital

Woolloongabba, Australia, 4102

Actively Recruiting

46

UZ Leuven

Leuven, Belgium, 3000

Actively Recruiting

47

Fundacao Centro Medico de Campinas

Campinas, Brazil, 13083-190

Actively Recruiting

48

Instituto do Coracao (InCor) do Hospital das Clinicas da FMUSP

Cerqueira César, Brazil, 05403-000

Actively Recruiting

49

CAPED - Centro Avancado de Pesquisa, Estudos e Diagnostico

Ribeirão Preto, Brazil, 14026-900

Actively Recruiting

50

Cardiopulmonar da Bahia S.A. (Hospital Cardio Pulmonar)

Salvador, Brazil, 40170-130

Actively Recruiting

51

University of Calgary

Calgary, Alberta, Canada, T2N 4Z6

Actively Recruiting

52

University of British Columbia

Vancouver, British Columbia, Canada, V6Z1Y6

Actively Recruiting

53

St. Michael's Hospital

Toronto, Ontario, Canada, M5B1W8

Actively Recruiting

54

Hvitfeldt Poulsen

Aarhus, Denmark, 8200

Actively Recruiting

55

CHU Bordeaux - Hopital Pellegrin

Bordeaux, France, 33076

Actively Recruiting

56

AP-HP Hopital Henri Mondor

Créteil, France, 94000

Actively Recruiting

57

AP-HP Hopital Bicetre

Le Kremlin-Bicêtre, France, 94270

Actively Recruiting

58

CHU Rennes

Rennes, France, 35000

Actively Recruiting

59

CHU de Toulouse - Hopital Rangueil

Toulouse, France, 31400

Actively Recruiting

60

Charite Universitaetsmedizin Berlin

Berlin, Germany, 10117

Actively Recruiting

61

Universitaetsklinikum Heidelberg

Heidelberg, Germany, 69120

Actively Recruiting

62

Universitaetsmedizin der Johannes Gutenberg - Universitaet Mainz

Mainz, Germany, 55131

Actively Recruiting

63

Hippokration General Hospital of Athens

Athens, Greece, 11527

Actively Recruiting

64

General Hospital of Athens - Alexandra

Athens, Greece, 11528

Actively Recruiting

65

The Mater Misericordiae University Hospital

Dublin, Ireland, D07 R2WY

Actively Recruiting

66

Tallaght University Hospital - The Adelaide and Meath Hospital

Dublin, Ireland, D24 NR04

Actively Recruiting

67

Azienda Ospedaliero-Universitaria di Bologna IRCCS Policlinico di S.Orsola

Bologna, Italy, 40138

Actively Recruiting

68

Azienda Ospedaliero-Universitaria Careggi

Florence, Italy

Actively Recruiting

69

Fondazione IRCCS Policlinico San Matteo

Pavia, Italy, 27100

Actively Recruiting

70

Fondazione Toscana Gabriele Monasterio per la Ricerca Medica e di Sanità Pubblica - Ospedale San Cataldo

Pisa, Italy, 56124

Actively Recruiting

71

Azienda Ospedaliero Universitaria Policlinico Umberto I

Roma, Italy, 00161

Actively Recruiting

72

Fondazione Policlinico Universitario A. Gemelli IRCCS - Universita Cattolica del Sacro Cuore

Rome, Italy, 00168

Actively Recruiting

73

Azienda Ospedaliero-Universitaria Sant'Andrea

Rome, Italy, 00189

Actively Recruiting

74

Kumamoto University Hospital

Kumamoto, Japan, 860-8556

Actively Recruiting

75

Shinshu University Hospital

Nagano, Japan, 390-8621

Actively Recruiting

76

University Malaya Medical Centre (UMMC)

Kuala Lumpur, Malaysia, 59100

Actively Recruiting

77

CHU de Fort de France

Fort-de-France, Martinique, 97261

Actively Recruiting

78

National Institute of Medical Sciences and Nutrition - Salvador Zubiran(INCMNSZ)

Tlalpan, Mexico, 14080

Actively Recruiting

79

University Medical Center Groningen

Groningen, Netherlands, 9713 GZ

Actively Recruiting

80

Maastricht University Medical Center

Maastricht, Netherlands, 6229 HX

Actively Recruiting

81

Erasmus MC

Rotterdam, Netherlands, 3015 GD

Actively Recruiting

82

Universitair Medisch Centrum Utrecht

Utrecht, Netherlands, 3584 CX

Actively Recruiting

83

Unidade Local de Saude de Santa Maria EPE - Hospital de Santa Maria

Lisbon, Portugal, 1649-035

Actively Recruiting

84

Unidade Local de Saude de Santo Antonio EPE - Hospital de Santo Antonio

Porto, Portugal, 4099-001

Actively Recruiting

85

National University Hospital - National University Health System

Singapore, Singapore, 119228

Actively Recruiting

86

Singapore General Hospital

Singapore, Singapore, 169608

Actively Recruiting

87

Seoul National University Hospital

Seoul, South Korea, 03080

Actively Recruiting

88

Severance Hospital, Yonsei University Health System

Seoul, South Korea, 03722

Actively Recruiting

89

Samsung Medical Center

Seoul, South Korea, 06351

Actively Recruiting

90

Seoul St. Mary's Hospital

Seoul, South Korea, 06591

Actively Recruiting

91

Hospital Universitari de Bellvitge

Barcelona, Spain, 08907

Actively Recruiting

92

Hospital Universitario Juan Ramon Jimenez

Huelva, Spain

Actively Recruiting

93

Hospital Universitario Puerta de Hierro

Majadahonda, Spain

Actively Recruiting

94

Hospital Universitario Son Llatzer

Palma de Mallorca, Spain, 07198

Actively Recruiting

95

Hospital Clinico Universitario de Salamanca

Salamanca, Spain, 37007

Actively Recruiting

96

Norrlands universitetssjukhus (University Hospital of Umea)

Umeå, Sweden, 90185

Actively Recruiting

97

Changhua Christian Hospital - Taiwan

Changhua, Taiwan, 500

Actively Recruiting

98

National Taiwan University Hospital

Taipei, Taiwan, 10016

Actively Recruiting

99

Taipei Veterans General Hospital

Taipei, Taiwan, 11217

Actively Recruiting

100

St. Bartholomew's Hospital

London, United Kingdom, EC1A 7BE

Actively Recruiting

101

University College London Hospitals NHS Foundation Trust

London, United Kingdom, WC1N 3BG

Actively Recruiting

Loading map...

Research Team

M

Medical Information

CONTACT

How is the study designed?

Study Type

INTERVENTIONAL

Masking

QUADRUPLE

Allocation

RANDOMIZED

Model

PARALLEL

Primary Purpose

PREVENTION

Number of Arms

2

Not the Right Trial for You?

Explore thousands of other clinical trials that might be a better match.
Sign up to get personalized trial recommendations delivered to your inbox.

Already have an account? Log in here

Acoramidis Transthyretin Amyloidosis Prevention Trial in the Young (ACT-EARLY) Study in Asymptomatic Carriers of a Pathogenic TTR Variant | DecenTrialz