Actively Recruiting
DeciPHer-ILD: A Real-world Patient Registry in Group 3 Pulmonary Hypertension Associated With Interstitial Lung Disease (PH-ILD)
Led by United Therapeutics · Updated on 2026-04-29
900
Participants Needed
62
Research Sites
305 weeks
Total Duration
On this page
AI-Summary
What this Trial Is About
This is a prospective, real world, multicenter, registry of patients with pulmonary hypertension associated with interstitial lung disease (PH-ILD) and interstitial lung disease (ILD).
CONDITIONS
Official Title
DeciPHer-ILD: A Real-world Patient Registry in Group 3 Pulmonary Hypertension Associated With Interstitial Lung Disease (PH-ILD)
Who Can Participate
Eligibility Criteria
You may qualify if you...
- Adults aged 18 years or older
- Diagnosis of fibrotic interstitial lung disease confirmed by high-resolution computed tomography imaging, including idiopathic interstitial pneumonia, autoimmune ILD, chronic hypersensitivity pneumonitis, nonspecific interstitial pneumonia, occupational lung disease, or combined pulmonary fibrosis and emphysema with fibrosis greater than emphysema
- For Cohorts 1 to 3: Pulmonary hypertension confirmed by right heart catheterization with mean pulmonary artery pressure >20 mmHg, pulmonary artery wedge pressure 415 mmHg, and pulmonary vascular resistance >2 WU
- For Cohort 1: Not receiving inhaled treprostinil at baseline
- For Cohort 2: Initiated Tyvaso or Tyvaso DPI at baseline or within 90 days before baseline
- For Cohort 3: Receiving Tyvaso or Tyvaso DPI at baseline and for more than 90 days prior
- For Cohort 4: Prior right heart catheterization not meeting pulmonary hypertension criteria but with pulmonary artery wedge pressure 415 mmHg
- Co-enrollment in other observational or interventional studies allowed
- Willing and able to provide informed consent and complete questionnaires in English or Spanish
You will not qualify if you...
- Confirmed diagnosis of Group 1, 2, 4, or 5 pulmonary hypertension
- Confirmed diagnosis of Group 3 pulmonary hypertension due to lung diseases or hypoxia other than fibrotic interstitial lung disease
- Receiving inhaled treprostinil (Yutrepia) at baseline
- Patients receiving other forms of pulmonary hypertension therapy are eligible
AI-Screening
AI-Powered Screening
Complete this quick 3-step screening to check your eligibility
Trial Site Locations
Total: 62 locations
1
University of Alabama at Birmingham
Birmingham, Alabama, United States, 35294
Actively Recruiting
2
Banner Health - University Medical Center Phoenix
Phoenix, Arizona, United States, 85006
Actively Recruiting
3
University of Colorado - Anschutz Medical Campus
Aurora, Colorado, United States, 80045
Actively Recruiting
4
National Jewish Health
Denver, Colorado, United States, 80206
Actively Recruiting
5
Pasquerilla Healthcare Center - Georgetown University
Washington D.C., District of Columbia, United States, 20007
Actively Recruiting
6
University of Florida
Gainesville, Florida, United States, 32610
Actively Recruiting
7
NCH Research Institute
Naples, Florida, United States, 34102
Actively Recruiting
8
Advent Health Medical Group Advanced Lung Disease
Orlando, Florida, United States, 32804
Actively Recruiting
9
Intercoastal Medical Group
Sarasota, Florida, United States, 34239
Actively Recruiting
10
Tampa General Hospital/University of South Florida Health
Tampa, Florida, United States, 33606
Actively Recruiting
11
Weston Hospital - Cleveland Clinic Florida
Weston, Florida, United States, 33331
Actively Recruiting
12
Emory University
Atlanta, Georgia, United States, 30322
Actively Recruiting
13
Northwestern University
Chicago, Illinois, United States, 60611
Actively Recruiting
14
Loyola University Medical Center
Maywood, Illinois, United States, 60153
Actively Recruiting
15
Advocate Christ Medical Center
Oak Lawn, Illinois, United States, 60453
Actively Recruiting
16
Ascension St. Vincent
Indianapolis, Indiana, United States, 46260
Actively Recruiting
17
University of Kansas Medical Center
Kansas City, Kansas, United States, 66160
Actively Recruiting
18
Norton Pulmonary Specialists
Louisville, Kentucky, United States, 40202
Actively Recruiting
19
University Medical Center - New Orleans
New Orleans, Louisiana, United States, 70112
Actively Recruiting
20
University of Maryland Medical Center
Baltimore, Maryland, United States, 21201
Actively Recruiting
21
Washington University School of Medicine
St Louis, Missouri, United States, 63110
Actively Recruiting
22
Dartmouth Hitchcock Medical Center
Lebanon, New Hampshire, United States, 03766
Actively Recruiting
23
Morristown Medical Center
Morristown, New Jersey, United States, 07960
Actively Recruiting
24
University of New Mexico Health Sciences Center
Albuquerque, New Mexico, United States, 87131
Actively Recruiting
25
Northwell Health
New Hyde Park, New York, United States, 11042
Actively Recruiting
26
New York University Langone Medical Center
New York, New York, United States, 10016
Actively Recruiting
27
New York Presbyterian Hospital - Weill Cornell Medicine
New York, New York, United States, 10021
Actively Recruiting
28
University of North Carolina at Chapel Hill
Chapel Hill, North Carolina, United States, 27514
Actively Recruiting
29
Duke University School of Medicine
Durham, North Carolina, United States, 27710
Actively Recruiting
30
Pulmonix, LLC
Greensboro, North Carolina, United States, 27403
Actively Recruiting
31
East Carolina University Health
Greenville, North Carolina, United States, 27834
Actively Recruiting
32
Wakemed Health and Hospital
Raleigh, North Carolina, United States, 27610-1231
Actively Recruiting
33
University of Cincinnati Medical Center
Cincinnati, Ohio, United States, 45219
Actively Recruiting
34
The Cleveland Clinic
Cleveland, Ohio, United States, 44195
Actively Recruiting
35
Ohio State Richard M. Ross Heart Hospital
Columbus, Ohio, United States, 43210
Actively Recruiting
36
The University of Oklahoma Health Sciences Center
Oklahoma City, Oklahoma, United States, 73104
Actively Recruiting
37
Oklahoma Heart Institute
Tulsa, Oklahoma, United States, 74104
Actively Recruiting
38
Summit Health
Bend, Oregon, United States, 97701
Actively Recruiting
39
Legacy Research Institute
Portland, Oregon, United States, 97210
Actively Recruiting
40
Oregon Health & Science University
Portland, Oregon, United States, 97239
Actively Recruiting
41
St. Luke's University Health Network
Bethlehem, Pennsylvania, United States, 18015
Actively Recruiting
42
University of Pennsylvania
Philadelphia, Pennsylvania, United States, 19104
Actively Recruiting
43
Thomas Jefferson University - Sidney Kimmel Medical College
Philadelphia, Pennsylvania, United States, 19107
Actively Recruiting
44
Temple Lung Center
Philadelphia, Pennsylvania, United States, 19140
Actively Recruiting
45
Temple University Hospital
Philadelphia, Pennsylvania, United States, 19140
Actively Recruiting
46
AnMed Health
Anderson, South Carolina, United States, 29621
Actively Recruiting
47
Medical University of South Carolina
Charleston, South Carolina, United States, 29425
Actively Recruiting
48
StatCare Pulmonary Consultants and Center for Biomedical Research
Knoxville, Tennessee, United States, 37909
Actively Recruiting
49
Baylor University Medical Center
Dallas, Texas, United States, 75246
Actively Recruiting
50
UT Southwest Medical Center Heart and Lung Clinic
Dallas, Texas, United States, 75390
Actively Recruiting
51
Houston Methodist
Houston, Texas, United States, 77030
Actively Recruiting
52
University of Texas Health Science Center at Houston
Houston, Texas, United States, 77030
Actively Recruiting
53
Intermountain Medical Center
Murray, Utah, United States, 84157
Actively Recruiting
54
University of Utah Health
Salt Lake City, Utah, United States, 84108
Actively Recruiting
55
Inova Medical Group
Falls Church, Virginia, United States, 22042
Actively Recruiting
56
Pulmonary Associates of Richmond, Inc.
Richmond, Virginia, United States, 23230
Actively Recruiting
57
Virginia Commonwealth University
Richmond, Virginia, United States, 23298
Actively Recruiting
58
Marshall Health
Huntington, West Virginia, United States, 25701
Actively Recruiting
59
University of Wisconsin Hospital and Clinics
Madison, Wisconsin, United States, 53792
Actively Recruiting
60
Aurora St. Luke's Medical Center
Milwaukee, Wisconsin, United States, 53215
Actively Recruiting
61
Medical College of Wisconsin
Milwaukee, Wisconsin, United States, 53226
Actively Recruiting
62
Auxilio Mutuo Hospital
Guaynabo, Puerto Rico, Puerto Rico, 00968
Actively Recruiting
Research Team
U
United Therapeutics Global Medical Information
CONTACT
How is the study designed?
Study Type
OBSERVATIONAL
Masking
N/A
Allocation
N/A
Model
N/A
Primary Purpose
N/A
Number of Arms
4
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